| 1308188 | Upp2 | uridine phosphorylase 2 | ENCODES a protein that exhibits deoxyuridine phosphorylase activity (ortholog); identical protein binding (ortholog); pyrimidine-nucleoside phosphorylase activity (ortholog); INVOLVED IN CMP catabolic process (ortholog); dCMP catabolic process (ortholog); dTMP catabolic process (ortholog); PARTICIPA TES IN beta-ureidopropionase deficiency pathway; dihydropyrimidinase deficiency pathway; mitochondrial neurogastrointestinal encephalopathy syndrome pathway; ASSOCIATED WITH autism spectrum disorder (ortholog); FOUND IN cytosol (ortholog); type III intermediate filament (ortholog); INTERACTS WITH (+)-schisandrin B; 17beta-estradiol; amphetamine | 3 | 63681671 | 63726194 | Rat | 160 | symbol , PhenoGen | gene, protein-coding, PROVISIONAL [RefSeq] |
| 1317821 | UPP2 | uridine phosphorylase 2 | Enables deoxyuridine phosphorylase activity; identical protein binding activity; and uridine phosphorylase activity. Involved in dCMP catabolic process and uridine catabolic process. Located in type III intermediate filament. [provided by Alliance of Genome Resources, Jul 2025] | 2 | 157995179 | 158136154 | Human | 149 | symbol , COSMIC , Human Proteome Map | gene, protein-coding, VALIDATED [RefSeq] |
| 1317822 | Upp2 | uridine phosphorylase 2 | Enables uridine phosphorylase activity. Involved in CMP catabolic process; UMP catabolic process; and uridine catabolic process. Is active in cytosol. Is expressed in adrenal gland and gland. Orthologous to human UPP2 (uridine phosphorylase 2). [provided by Alli ance of Genome Resources, Jul 2025] | 2 | 58456329 | 58685858 | Mouse | 153 | symbol , PhenoGen , description | gene, protein-coding, VALIDATED [RefSeq] |
| 8986128 | Upp2 | uridine phosphorylase 2 | ENCODES a protein that exhibits deoxyuridine phosphorylase activity (ortholog); identical protein binding (ortholog); pyrimidine-nucleoside phosphorylase activity (ortholog); INVOLVED IN CMP catabolic process (ortholog); dCMP catabolic process (ortholog); dTMP catabolic process (ortholog); PARTICIPA TES IN beta-ureidopropionase deficiency pathway; dihydropyrimidinase deficiency pathway; mitochondrial neurogastrointestinal encephalopathy syndrome pathway; ASSOCIATED WITH autism spectrum disorder (ortholog); FOUND IN cytosol (ortholog); type III intermediate filament (ortholog) | NW_004955449 | 15355592 | 15405997 | Chinchilla | 29 | symbol | gene, protein-coding, MODEL [RefSeq] |
| 12648770 | Upp2 | uridine phosphorylase 2 | ENCODES a protein that exhibits catalytic activity (inferred); deoxyuridine phosphorylase activity (inferred); identical protein binding (inferred); INVOLVED IN dCMP catabolic process (ortholog); PARTICIPATES IN beta-ureidopropionase deficiency pathway; dihydropyrimidinase deficiency pathway; mitoch ondrial neurogastrointestinal encephalopathy syndrome pathway; ASSOCIATED WITH autism spectrum disorder (ortholog); FOUND IN cytosol (inferred); type III intermediate filament (inferred) | NW_004936469 | 20465767 | 20513084 | Squirrel | 30 | symbol | gene, protein-coding, MODEL [RefSeq] |
| 20867195 | UPP2 | uridine phosphorylase 2 | | | | | Green Monkey | | symbol | gene, protein-coding |
| 18505711 | UPP2 | uridine phosphorylase 2 | ENCODES a protein that exhibits catalytic activity (inferred); deoxyuridine phosphorylase activity (inferred); identical protein binding (inferred); INVOLVED IN dCMP catabolic process (ortholog); PARTICIPATES IN beta-ureidopropionase deficiency pathway; dihydropyrimidinase deficiency pathway; mitoch ondrial neurogastrointestinal encephalopathy syndrome pathway; ASSOCIATED WITH autism spectrum disorder (ortholog); FOUND IN cytoplasm (inferred); cytosol (inferred); type III intermediate filament (inferred) | | | | Green Monkey | 33 | symbol | gene, protein-coding, MODEL [RefSeq] |
| 625847359 | Upp2 | uridine phosphorylase 2 | ENCODES a protein that exhibits deoxyuridine phosphorylase activity (ortholog); identical protein binding (ortholog); pyrimidine-nucleoside phosphorylase activity (ortholog); INVOLVED IN CMP catabolic process (ortholog); dCMP catabolic process (ortholog); dTMP catabolic process (ortholog); PARTICIPA TES IN beta-ureidopropionase deficiency pathway; dihydropyrimidinase deficiency pathway; mitochondrial neurogastrointestinal encephalopathy syndrome pathway; ASSOCIATED WITH autism spectrum disorder (ortholog); FOUND IN cytosol (ortholog); type III intermediate filament (ortholog) | | | | Black Rat | 29 | symbol | gene, protein-coding, MODEL [RefSeq] |
| 14238873 | UPP2 | uridine phosphorylase 2 | ENCODES a protein that exhibits catalytic activity (inferred); deoxyuridine phosphorylase activity (inferred); glycosyltransferase activity (inferred); INVOLVED IN dCMP catabolic process (ortholog); PARTICIPATES IN beta-ureidopropionase deficiency pathway; dihydropyrimidinase deficiency pathway; mit ochondrial neurogastrointestinal encephalopathy syndrome pathway; ASSOCIATED WITH autism spectrum disorder (ortholog); FOUND IN cytoplasm (inferred); cytosol (inferred); type III intermediate filament (inferred) | | | | Pig | 40 | symbol | gene, protein-coding, MODEL [RefSeq] |
| 18900798 | Upp2 | uridine phosphorylase 2 | ENCODES a protein that exhibits identical protein binding (ortholog); pyrimidine-nucleoside phosphorylase activity (ortholog); thymidine phosphorylase activity (ortholog); INVOLVED IN dCMP catabolic process (ortholog); dTMP catabolic process (ortholog); dUMP catabolic process (ortholog); PARTICIPATE S IN beta-ureidopropionase deficiency pathway; dihydropyrimidinase deficiency pathway; mitochondrial neurogastrointestinal encephalopathy syndrome pathway; ASSOCIATED WITH autism spectrum disorder (ortholog); FOUND IN cytosol (ortholog); type III intermediate filament (ortholog) | | | | Naked Mole-Rat | 42 | symbol | gene, protein-coding, MODEL [RefSeq] |
| 155234723 | upp2 | | | | | | Tropical Clawed Frog | | symbol | gene, null |
| 155260083 | upp2.L | | | | | | African Clawed Frog | | symbol | gene, null |
| 155234045 | upp2.S | | | | | | African Clawed Frog | | symbol | gene, null |
| 11822892 | LOC100995749 | uridine phosphorylase 2 | ENCODES a protein that exhibits catalytic activity (inferred); deoxyuridine phosphorylase activity (inferred); glycosyltransferase activity (inferred); INVOLVED IN dCMP catabolic process (ortholog); PARTICIPATES IN beta-ureidopropionase deficiency pathway; dihydropyrimidinase deficiency pathway; mit ochondrial neurogastrointestinal encephalopathy syndrome pathway; ASSOCIATED WITH autism spectrum disorder (ortholog); FOUND IN cytoplasm (inferred); cytosol (inferred); type III intermediate filament (inferred) | 2B | 45363103 | 45400281 | Bonobo | 44 | old_gene_symbol | gene, protein-coding, MODEL [RefSeq] |
| 12112158 | LOC106558297 | uncharacterized LOC106558297 | | 36 | 4061587 | 4073397 | Dog | | old_gene_symbol | gene, protein-coding, MODEL [RefSeq] |