| 620364 | Agps | alkylglycerone phosphate synthase | ENCODES a protein that exhibits alkylglycerone-phosphate synthase activity; FAD binding (ortholog); INVOLVED IN ether lipid biosynthetic process (ortholog); lipid biosynthetic process (ortholog); PARTICIPATES IN plasmalogen biosynthetic pathway; plasmalogen metabolic pathway; ether lipid metabolic p athway; ASSOCIATED WITH Experimental Liver Neoplasms; Experimental Sarcoma; Desbuquois dysplasia (ortholog); FOUND IN peroxisome; INTERACTS WITH (+)-schisandrin B; 17alpha-ethynylestradiol; 2,3,7,8-tetrachlorodibenzodioxine | 3 | 81154599 | 81253099 | Rat | 131 | symbol , PhenoGen | gene, protein-coding, VALIDATED [RefSeq] |
| 732011 | AGPS | alkylglycerone phosphate synthase | This gene is a member of the FAD-binding oxidoreductase/transferase type 4 family. It encodes a protein that catalyzes the second step of ether lipid biosynthesis in which acyl-dihydroxyacetonephosphate (DHAP) is converted to alkyl-DHAP by the addition of a long chain alcohol and the removal of a lo ng-chain acid anion. The protein is localized to the inner aspect of the peroxisomal membrane and requires FAD as a cofactor. Mutations in this gene have been associated with rhizomelic chondrodysplasia punctata, type 3 and Zellweger syndrome. [provided by RefSeq, Jul 2008] | 2 | 177392773 | 177543834 | Human | 210 | symbol , COSMIC , Human Proteome Map | gene, protein-coding, REVIEWED [RefSeq] |
| 732012 | Agps | alkylglycerone phosphate synthase | Predicted to enable FAD binding activity and alkylglycerone-phosphate synthase activity. Predicted to be involved in ether lipid biosynthetic process. Located in mitochondrion. Is expressed in several structures, including alimentary system; central nervous system; respiratory system; sensory organ; and urinary system. Used to study rhizomelic chondrodysplasia punctata type 3. Human ortholog(s) of this gene implicated in rhizomelic chondrodysplasia punctata and rhizomelic chondrodysplasia punctata type 3. Orthologous to human AGPS (alkylglycerone phosphate synthase). [provided by Alliance of Genome Resources, Jul 2025] | 2 | 75662477 | 75761694 | Mouse | 143 | symbol , PhenoGen , description | gene, protein-coding, VALIDATED [RefSeq] |
| 8799751 | Agps | alkylglycerone phosphate synthase | ENCODES a protein that exhibits alkylglycerone-phosphate synthase activity (ortholog); INVOLVED IN lipid biosynthetic process (ortholog); PARTICIPATES IN plasmalogen biosynthetic pathway; plasmalogen metabolic pathway; ASSOCIATED WITH Desbuquois dysplasia (ortholog); Experimental Liver Neoplasms (or tholog); Experimental Sarcoma (ortholog); FOUND IN peroxisome (ortholog) | NW_004955403 | 19253784 | 19381883 | Chinchilla | 17 | symbol | gene, protein-coding, MODEL [RefSeq] |
| 11942962 | AGPS | alkylglycerone phosphate synthase | ENCODES a protein that exhibits alkylglycerone-phosphate synthase activity (ortholog); INVOLVED IN lipid biosynthetic process (ortholog); PARTICIPATES IN plasmalogen biosynthetic pathway; plasmalogen metabolic pathway; ASSOCIATED WITH Desbuquois dysplasia (ortholog); Experimental Liver Neoplasms (or tholog); Experimental Sarcoma (ortholog); FOUND IN peroxisome (ortholog) | 2B | 64671136 | 64823956 | Bonobo | 30 | symbol | gene, protein-coding, MODEL [RefSeq] |
| 12301624 | AGPS | alkylglycerone phosphate synthase | ENCODES a protein that exhibits alkylglycerone-phosphate synthase activity (ortholog); INVOLVED IN lipid biosynthetic process (ortholog); PARTICIPATES IN plasmalogen biosynthetic pathway; plasmalogen metabolic pathway; ASSOCIATED WITH Desbuquois dysplasia (ortholog); Experimental Liver Neoplasms (or tholog); Experimental Sarcoma (ortholog); FOUND IN peroxisome (ortholog) | 36 | 21131616 | 21264615 | Dog | 30 | symbol | gene, protein-coding, MODEL [RefSeq] |
| 12719527 | Agps | alkylglycerone phosphate synthase | ENCODES a protein that exhibits alkylglycerone-phosphate synthase activity (ortholog); INVOLVED IN lipid biosynthetic process (ortholog); PARTICIPATES IN plasmalogen biosynthetic pathway; plasmalogen metabolic pathway; ASSOCIATED WITH Desbuquois dysplasia (ortholog); Experimental Liver Neoplasms (or tholog); Experimental Sarcoma (ortholog); FOUND IN peroxisome (ortholog) | NW_004936509 | 6742800 | 6872045 | Squirrel | 31 | symbol | gene, protein-coding, MODEL [RefSeq] |
| 155248273 | agps | | | | | | Tropical Clawed Frog | | symbol | gene, null |
| 13951300 | AGPS | alkylglycerone phosphate synthase | ENCODES a protein that exhibits alkylglycerone-phosphate synthase activity (ortholog); INVOLVED IN lipid biosynthetic process (ortholog); PARTICIPATES IN plasmalogen biosynthetic pathway; plasmalogen metabolic pathway; ASSOCIATED WITH Desbuquois dysplasia (ortholog); Experimental Liver Neoplasms (or tholog); Experimental Sarcoma (ortholog); FOUND IN peroxisome (ortholog); INTERACTS WITH ethanol | | | | Pig | 32 | symbol | gene, protein-coding, MODEL [RefSeq] |
| 626096506 | Agps | alkylglycerone phosphate synthase | ENCODES a protein that exhibits alkylglycerone-phosphate synthase activity (ortholog); INVOLVED IN lipid biosynthetic process (ortholog); PARTICIPATES IN plasmalogen biosynthetic pathway; plasmalogen metabolic pathway; ASSOCIATED WITH Desbuquois dysplasia (ortholog); Experimental Liver Neoplasms (or tholog); Experimental Sarcoma (ortholog); FOUND IN peroxisome (ortholog) | | | | Black Rat | 17 | symbol | gene, protein-coding, MODEL [RefSeq] |
| 18567949 | AGPS | alkylglycerone phosphate synthase | ENCODES a protein that exhibits alkylglycerone-phosphate synthase activity (ortholog); INVOLVED IN lipid biosynthetic process (ortholog); PARTICIPATES IN plasmalogen biosynthetic pathway; plasmalogen metabolic pathway; ASSOCIATED WITH Desbuquois dysplasia (ortholog); Experimental Liver Neoplasms (or tholog); Experimental Sarcoma (ortholog); FOUND IN peroxisome (ortholog) | | | | Green Monkey | 30 | symbol | gene, protein-coding, MODEL [RefSeq] |
| 18900723 | Agps | alkylglycerone phosphate synthase | ENCODES a protein that exhibits alkylglycerone-phosphate synthase activity (ortholog); INVOLVED IN lipid biosynthetic process (ortholog); PARTICIPATES IN plasmalogen biosynthetic pathway; plasmalogen metabolic pathway; ASSOCIATED WITH Desbuquois dysplasia (ortholog); Experimental Liver Neoplasms (or tholog); Experimental Sarcoma (ortholog); FOUND IN peroxisome (ortholog) | | | | Naked Mole-Rat | 28 | symbol | gene, protein-coding, MODEL [RefSeq] |
| 155233622 | agps.L | | | | | | African Clawed Frog | | symbol | gene, null |
| 155254189 | agps.S | | | | | | African Clawed Frog | | symbol | gene, null |
| 597538573 | IFT70A-AS1 | IFT70A antisense RNA 1 | | 2 | 177603060 | 177619238 | Human | | old_gene_symbol | gene, ncrna, VALIDATED [RefSeq] |