| 1305145 | Nars2 | asparaginyl-tRNA synthetase 2, mitochondrial | ENCODES a protein that exhibits aminoacyl-tRNA ligase activity (inferred); asparagine-tRNA ligase activity (inferred); ATP binding (inferred); INVOLVED IN asparaginyl-tRNA aminoacylation (inferred); translation (inferred); tRNA aminoacylation for protein translation (inferred); PARTICIPATES IN amino acyl-tRNA biosynthetic pathway; ASSOCIATED WITH autosomal recessive nonsyndromic deafness 94 (ortholog); combined oxidative phosphorylation deficiency 1 (ortholog); combined oxidative phosphorylation deficiency 24 (ortholog); FOUND IN mitochondrion (ortholog); INTERACTS WITH 2,3,7,8-tetrachlorodibenzodioxine; acetamide; bisphenol A | 1 | 160711680 | 160823311 | Rat | 90 | symbol , old_gene_name , PhenoGen | gene, protein-coding, VALIDATED [RefSeq] |
| 1313005 | Nars2 | asparaginyl-tRNA synthetase 2 (mitochondrial)(putative) | Predicted to enable asparagine-tRNA ligase activity. Predicted to be involved in asparaginyl-tRNA aminoacylation. Located in mitochondrion. Is expressed in embryo; extraembryonic component; and primitive endoderm. Human ortholog(s) of this gene implicated in autosomal recessive nonsyndromic deafness 94 and combined oxidative phosphorylation deficiency 24. Orthologous to human NARS2 (asparaginyl-tRNA synthetase 2, mitochondrial). [provided by Alliance of Genome Resources, Jul 2025] | 7 | 96600698 | 96725606 | Mouse | 104 | symbol , PhenoGen , description | gene, protein-coding, VALIDATED [RefSeq] |
| 1605947 | NARS2 | asparaginyl-tRNA synthetase 2, mitochondrial | This gene encodes a putative member of the class II family of aminoacyl-tRNA synthetases. These enzymes play a critical role in protein biosynthesis by charging tRNAs with their cognate amino acids. This protein is encoded by the nuclear genome but is likely to be imported to the mitochondrion where it is thought to catalyze the ligation of asparagine to tRNA molecules. Mutations in this gene have been associated with combined oxidative phosphorylation deficiency 24 (COXPD24). [provided by RefSeq, Mar 2015] | 11 | 78435968 | 78574864 | Human | 178 | symbol , COSMIC , Human Proteome Map | gene, protein-coding, REVIEWED [RefSeq] |
| 8974543 | Nars2 | asparaginyl-tRNA synthetase 2, mitochondrial | ASSOCIATED WITH autosomal recessive nonsyndromic deafness 94 (ortholog); combined oxidative phosphorylation deficiency 1 (ortholog); combined oxidative phosphorylation deficiency 24 (ortholog); FOUND IN mitochondrion (ortholog) | NW_004955414 | 13410751 | 13528014 | Chinchilla | 11 | symbol | gene, protein-coding, MODEL [RefSeq] |
| 11806115 | NARS2 | asparaginyl-tRNA synthetase 2, mitochondrial | ENCODES a protein that exhibits aminoacyl-tRNA ligase activity (inferred); asparagine-tRNA ligase activity (inferred); ATP binding (inferred); INVOLVED IN asparaginyl-tRNA aminoacylation (inferred); translation (inferred); tRNA aminoacylation for protein translation (inferred); ASSOCIATED WITH autos omal recessive nonsyndromic deafness 94 (ortholog); combined oxidative phosphorylation deficiency 1 (ortholog); combined oxidative phosphorylation deficiency 24 (ortholog); FOUND IN mitochondrial matrix (inferred); mitochondrion (inferred) | 11 | 73496423 | 73634623 | Bonobo | 28 | symbol | gene, protein-coding, MODEL [RefSeq] |
| 12400437 | NARS2 | asparaginyl-tRNA synthetase 2, mitochondrial | ENCODES a protein that exhibits phosphatidylinositol-3,4,5-trisphosphate binding (ortholog); phosphatidylinositol-3,4-bisphosphate binding (ortholog); protein domain specific binding (ortholog); INVOLVED IN cell migration (ortholog); integrin-mediated signaling pathway (ortholog); intracellular sign al transduction (ortholog); ASSOCIATED WITH autosomal recessive nonsyndromic deafness 94 (ortholog); combined oxidative phosphorylation deficiency 1 (ortholog); combined oxidative phosphorylation deficiency 24 (ortholog); FOUND IN membrane raft (ortholog); protein-containing complex (ortholog) | 21 | 20277707 | 20413624 | Dog | 46 | symbol | gene, protein-coding, MODEL [RefSeq] |
| 12717825 | Nars2 | asparaginyl-tRNA synthetase 2, mitochondrial | ENCODES a protein that exhibits aminoacyl-tRNA ligase activity (inferred); asparagine-tRNA ligase activity (inferred); ATP binding (inferred); INVOLVED IN asparaginyl-tRNA aminoacylation (inferred); translation (inferred); tRNA aminoacylation for protein translation (inferred); ASSOCIATED WITH autos omal recessive nonsyndromic deafness 94 (ortholog); combined oxidative phosphorylation deficiency 1 (ortholog); combined oxidative phosphorylation deficiency 24 (ortholog); FOUND IN mitochondrial matrix (inferred); mitochondrion (inferred) | NW_004936498 | 6967277 | 7108130 | Squirrel | 28 | symbol | gene, protein-coding, MODEL [RefSeq] |
| 14289909 | NARS2 | asparaginyl-tRNA synthetase 2, mitochondrial | ENCODES a protein that exhibits aminoacyl-tRNA ligase activity (inferred); asparagine-tRNA ligase activity (inferred); ATP binding (inferred); INVOLVED IN asparaginyl-tRNA aminoacylation (inferred); translation (inferred); tRNA aminoacylation for protein translation (inferred); ASSOCIATED WITH autos omal recessive nonsyndromic deafness 94 (ortholog); combined oxidative phosphorylation deficiency 1 (ortholog); combined oxidative phosphorylation deficiency 24 (ortholog); FOUND IN mitochondrial matrix (inferred); mitochondrion (inferred); INTERACTS WITH deoxynivalenol | | | | Pig | 30 | symbol | gene, protein-coding, MODEL [RefSeq] |
| 626024441 | Nars2 | asparaginyl-tRNA synthetase 2, mitochondrial | ASSOCIATED WITH autosomal recessive nonsyndromic deafness 94 (ortholog); combined oxidative phosphorylation deficiency 1 (ortholog); combined oxidative phosphorylation deficiency 24 (ortholog); FOUND IN mitochondrion (ortholog) | | | | Black Rat | 10 | symbol | gene, protein-coding, MODEL [RefSeq] |
| 18900708 | Nars2 | asparaginyl-tRNA synthetase 2, mitochondrial | ENCODES a protein that exhibits aminoacyl-tRNA ligase activity (inferred); asparagine-tRNA ligase activity (inferred); ATP binding (inferred); INVOLVED IN asparaginyl-tRNA aminoacylation (inferred); translation (inferred); tRNA aminoacylation for protein translation (inferred); ASSOCIATED WITH autos omal recessive nonsyndromic deafness 94 (ortholog); combined oxidative phosphorylation deficiency 1 (ortholog); combined oxidative phosphorylation deficiency 24 (ortholog); FOUND IN mitochondrial matrix (inferred); mitochondrion (inferred) | | | | Naked Mole-Rat | 28 | symbol | gene, protein-coding, MODEL [RefSeq] |
| 18355434 | NARS2 | asparaginyl-tRNA synthetase 2, mitochondrial | ENCODES a protein that exhibits aminoacyl-tRNA ligase activity (inferred); asparagine-tRNA ligase activity (inferred); ATP binding (inferred); INVOLVED IN asparaginyl-tRNA aminoacylation (inferred); translation (inferred); tRNA aminoacylation for protein translation (inferred); ASSOCIATED WITH autos omal recessive nonsyndromic deafness 94 (ortholog); combined oxidative phosphorylation deficiency 1 (ortholog); combined oxidative phosphorylation deficiency 24 (ortholog); FOUND IN mitochondrion (inferred) | | | | Green Monkey | 28 | symbol | gene, protein-coding, MODEL [RefSeq] |
| 155241632 | nars2 | | | | | | Tropical Clawed Frog | | symbol | gene, null |
| 626179890 | nars2.L | | | | | | African Clawed Frog | | symbol | gene, null |
| 155234755 | nars2.S | | | | | | African Clawed Frog | | symbol | gene, null |
| 16560570 | NARS2-AS1 | NARS2 antisense RNA 1 | | 11 | 78533176 | 78558565 | Human | | symbol , COSMIC , name , Human Proteome Map | gene, ncrna, VALIDATED [RefSeq] |