| 1311268 | Rpusd4 | RNA pseudouridine synthase D4 | ENCODES a protein that exhibits mitochondrial ribosomal large subunit rRNA binding (ortholog); pseudouridine synthase activity (ortholog); tRNA binding (ortholog); INVOLVED IN mitochondrial RNA modification (ortholog); mitochondrial tRNA pseudouridine synthesis (ortholog); mRNA pseudouridine synthes is (ortholog); FOUND IN mitochondrial matrix (ortholog); mitochondrion (ortholog); ribonucleoprotein granule (ortholog); INTERACTS WITH 2,3,7,8-tetrachlorodibenzodioxine; 2,4-dinitrotoluene; C60 fullerene | 8 | 41875217 | 41884702 | Rat | 77 | symbol , old_gene_name , PhenoGen | gene, protein-coding, PROVISIONAL [RefSeq] |
| 1345355 | RPUSD4 | RNA pseudouridine synthase D4 | Enables mitochondrial ribosomal large subunit rRNA binding activity; pseudouridine synthase activity; and tRNA binding activity. Involved in positive regulation of mitochondrial translation and pseudouridine synthesis. Located in mitochondrial matrix; nucleoplasm; and ribonucleoprotein granule. [pro vided by Alliance of Genome Resources, Jul 2025] | 11 | 126202096 | 126211650 | Human | 72 | symbol , old_gene_name , COSMIC , Human Proteome Map | gene, protein-coding, VALIDATED [RefSeq] |
| 1550291 | Rpusd4 | RNA pseudouridylate synthase domain containing 4 | Predicted to enable mitochondrial ribosomal large subunit rRNA binding activity; pseudouridine synthase activity; and tRNA binding activity. Predicted to be involved in mRNA pseudouridine synthesis; mitochondrial tRNA pseudouridine synthesis; and positive regulation of mitochondrial translation. Loc ated in mitochondrion. Is expressed in genitourinary system. Orthologous to human RPUSD4 (RNA pseudouridine synthase D4). [provided by Alliance of Genome Resources, Apr 2025] | 9 | 35179177 | 35187253 | Mouse | 80 | symbol , old_gene_name , PhenoGen , description | gene, protein-coding, PROVISIONAL [RefSeq] |
| 8897615 | Rpusd4 | RNA pseudouridine synthase D4 | ENCODES a protein that exhibits mitochondrial ribosomal large subunit rRNA binding (ortholog); pseudouridine synthase activity (ortholog); tRNA binding (ortholog); INVOLVED IN mitochondrial RNA modification (ortholog); mitochondrial tRNA pseudouridine synthesis (ortholog); mRNA pseudouridine synthes is (ortholog); FOUND IN mitochondrial matrix (ortholog); mitochondrion (ortholog); ribonucleoprotein granule (ortholog) | NW_004955412 | 27231371 | 27239366 | Chinchilla | 16 | symbol | gene, protein-coding, MODEL [RefSeq] |
| 11960143 | RPUSD4 | RNA pseudouridine synthase D4 | ENCODES a protein that exhibits isomerase activity (inferred); mitochondrial ribosomal large subunit rRNA binding (inferred); pseudouridine synthase activity (inferred); INVOLVED IN mitochondrial RNA modification (inferred); mitochondrial tRNA pseudouridine synthesis (inferred); mRNA pseudouridine s ynthesis (inferred); FOUND IN mitochondrial matrix (inferred); mitochondrion (inferred); ribonucleoprotein granule (inferred) | 11 | 120997815 | 121025558 | Bonobo | 21 | symbol , old_gene_name | gene, protein-coding, MODEL [RefSeq] |
| 12349871 | RPUSD4 | RNA pseudouridine synthase D4 | ENCODES a protein that exhibits isomerase activity (inferred); mitochondrial ribosomal large subunit rRNA binding (inferred); pseudouridine synthase activity (inferred); INVOLVED IN mitochondrial RNA modification (inferred); mitochondrial tRNA pseudouridine synthesis (inferred); mRNA pseudouridine s ynthesis (inferred); FOUND IN mitochondrial matrix (inferred); mitochondrion (inferred); ribonucleoprotein granule (inferred) | 5 | 8300421 | 8311193 | Dog | 23 | symbol , old_gene_name | gene, protein-coding, MODEL [RefSeq] |
| 12546856 | Rpusd4 | RNA pseudouridine synthase D4 | ENCODES a protein that exhibits isomerase activity (inferred); mitochondrial ribosomal large subunit rRNA binding (inferred); pseudouridine synthase activity (inferred); INVOLVED IN mitochondrial RNA modification (inferred); mitochondrial tRNA pseudouridine synthesis (inferred); mRNA pseudouridine s ynthesis (inferred); FOUND IN mitochondrial matrix (inferred); mitochondrion (inferred); ribonucleoprotein granule (inferred) | NW_004936572 | 6013920 | 6027023 | Squirrel | 23 | symbol , old_gene_name | gene, protein-coding, MODEL [RefSeq] |
| 18930522 | Rpusd4 | RNA pseudouridine synthase D4 | ENCODES a protein that exhibits mitochondrial ribosomal large subunit rRNA binding (ortholog); tRNA binding (ortholog); INVOLVED IN mitochondrial RNA modification (ortholog); mitochondrial tRNA pseudouridine synthesis (ortholog); mRNA pseudouridine synthesis (ortholog); FOUND IN mitochondrial matrix (ortholog); ribonucleoprotein granule (ortholog) | | | | Naked Mole-Rat | 21 | symbol | gene, protein-coding, MODEL [RefSeq] |
| 155249434 | rpusd4 | | | | | | Tropical Clawed Frog | | symbol | gene, null |
| 18614054 | RPUSD4 | RNA pseudouridine synthase D4 | ENCODES a protein that exhibits isomerase activity (inferred); mitochondrial ribosomal large subunit rRNA binding (inferred); pseudouridine synthase activity (inferred); INVOLVED IN mitochondrial RNA modification (inferred); mitochondrial tRNA pseudouridine synthesis (inferred); mRNA pseudouridine s ynthesis (inferred); FOUND IN mitochondrial matrix (inferred); mitochondrion (inferred); ribonucleoprotein granule (inferred) | | | | Green Monkey | 21 | symbol , old_gene_name | gene, protein-coding, MODEL [RefSeq] |
| 14263674 | RPUSD4 | RNA pseudouridine synthase D4 | ENCODES a protein that exhibits isomerase activity (inferred); mitochondrial ribosomal large subunit rRNA binding (inferred); pseudouridine synthase activity (inferred); INVOLVED IN mitochondrial RNA modification (inferred); mitochondrial tRNA pseudouridine synthesis (inferred); mRNA pseudouridine s ynthesis (inferred); FOUND IN mitochondrial matrix (inferred); mitochondrion (inferred); ribonucleoprotein granule (inferred) | | | | Pig | 23 | symbol , old_gene_name | gene, protein-coding, VALIDATED [RefSeq] |
| 626149199 | Rpusd4 | RNA pseudouridine synthase D4 | ENCODES a protein that exhibits mitochondrial ribosomal large subunit rRNA binding (ortholog); pseudouridine synthase activity (ortholog); tRNA binding (ortholog); INVOLVED IN mitochondrial RNA modification (ortholog); mitochondrial tRNA pseudouridine synthesis (ortholog); mRNA pseudouridine synthes is (ortholog); FOUND IN mitochondrial matrix (ortholog); mitochondrion (ortholog); ribonucleoprotein granule (ortholog) | | | | Black Rat | 16 | symbol , old_gene_name | gene, protein-coding, MODEL [RefSeq] |
| 155246574 | rpusd4.L | | | | | | African Clawed Frog | | symbol | gene, null |
| 9083598 | Rpusd4-ps1 | RNA pseudouridine synthase D4, pseudogene 1 | | 6 | 32186441 | 32190110 | Rat | | symbol , PhenoGen | gene, pseudo, MODEL [RefSeq] |
| 12529508 | LOC101960470 | mitochondrial RNA pseudouridine synthase RPUSD4-like | | NW_004936499 | 13426430 | 13432669 | Squirrel | | name | gene, pseudo, MODEL [RefSeq] |
| 625964733 | LOC116905555 | mitochondrial RNA pseudouridine synthase Rpusd4-like | | | | | Black Rat | | name | gene, pseudo, MODEL [RefSeq] |