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Ontology Browser
Term:
Parent Terms Term With Siblings Child Terms
B cell deficiency +  
B-cell neoplasm +  
B-cell non-Hodgkins lymphoma +  
basophil adenoma 
bubonic plague 
Chylothorax 
defective phagocytic cell engulfment +  
dendritic cell sarcoma +  
EBV-Positive T-Cell Lymphoproliferative Disorder of Childhood 
eosinophil disorder +  
eosinophil peroxidase deficiency 
functional neutrophil defect +  
Giant Lymph Node Hyperplasia 
hemophagocytic syndrome +  
hereditary neutrophilia 
human granulocytic anaplasmosis 
Langerhans Cell Histiocytosis 
Langerhans cell histiocytosis (LCH) is a systemic disease associated with the proliferation and accumulation (usually in granulomas) of Langerhans cells in various tissues.
leukostasis 
lymph node disorder +  
lymphangiectasis +  
lymphangitis 
lymphatic system cancer +  
lymphatic vessel neoplasm +  
lymphedema +  
lymphogranuloma venereum 
lymphopenia +  
malignant lymphatic vessel tumor 
Mastocytosis +  
neutropenia +  
non-Langerhans cell histiocytosis +  
phagocyte bactericidal dysfunction +  
POEMS syndrome 
pseudolymphoma 
reticulum cell sarcoma 
Small Intestinal Enteropathy-Associated T-Cell Lymphoma 
splenic disease +  
Subcutaneous Panniculitis-Like T-Cell Lymphoma 
T-cell leukemia +  
thymoma type B +  

Synonyms
Exact Synonyms: Langerhan's cell histiocytosis ;   Langerhans cell granulomatosis ;   Langerhans cell histiocytosis, NOS ;   Langerhans cell histiocytosis, Not otherwise specified ;   histiocytosis X ;   letterer-Siwe disease involving intra-abdominal lymph nodes ;   letterer-Siwe disease involving intrapelvic lymph nodes ;   letterer-Siwe disease involving intrathoracic lymph nodes ;   letterer-Siwe disease involving lymph nodes of axilla and upper limb ;   letterer-Siwe disease involving lymph nodes of head, face and neck ;   letterer-Siwe disease involving lymph nodes of inguinal region and lower limb ;   letterer-Siwe disease involving lymph nodes of multiple sites ;   letterer-Siwe disease involving spleen ;   letterer-Siwe disease of intra-abdominal lymph nodes ;   letterer-Siwe disease of intrapelvic lymph nodes ;   letterer-Siwe disease of intrathoracic lymph nodes ;   letterer-Siwe disease of lymph nodes of axilla and upper limb ;   letterer-Siwe disease of lymph nodes of axilla and/or upper limb ;   letterer-Siwe disease of lymph nodes of head, face and neck ;   letterer-Siwe disease of lymph nodes of head, face and/or neck ;   letterer-Siwe disease of lymph nodes of inguinal region amd/or lower limb ;   letterer-Siwe disease of lymph nodes of inguinal region and lower limb ;   letterer-Siwe disease of lymph nodes of inguinal region and/or lower limb ;   letterer-Siwe disease of lymph nodes of multiple sites ;   letterer-Siwe disease of spleen
Related Synonyms: Lch
Xrefs: COHD:4278365 ;   DOID:2571 ;   GARD:6858 ;   ICD10:C96.0 ;   ICD10:C96.5 ;   ICD10:C96.6 ;   ICD9:202.5 ;   ICD9:277.89 ;   ICDO:9751/1 ;   ICDO:9751/3 ;   ICDO:9752/1 ;   ICDO:9753/1 ;   ICDO:9754/3 ;   MONDO:0018310 ;   MedDRA:10069698 ;   NANDO:2200031 ;   NCI:C3107 ;   NORD:1348 ;   OMIM:604856 ;   ONCOTREE:LCH ;   ORDO:389 ;   SCTID:65399007 ;   UMLS:C0019621 ;   UMLS:C0432547 ;   UMLS:C0432548 ;   UMLS:C0432549 ;   UMLS:C0432550 ;   UMLS:C0432551 ;   UMLS:C0432552 ;   UMLS:C0432553 ;   UMLS:C0432554 ;   icd11.foundation:216625985
External Ontologys: disease_causes_dysfunction_of EFO:CL:0000453 ;   disease_has_location EFO:CL:0000453 ;   has_disease_location EFO:CL:0000453
Definition Sources: Orphanet:389

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