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HUMAN PHENOTYPE - ANNOTATIONS

The Human Phenotype Ontology (HPO) is downloaded weekly from http://compbio.charite.de/hudson/job/hpo/lastStableBuild/artifact/ontology/release/hp.obo. The file downloaded is considered the "last stable build" available for the ontology. For more about the HPO, view their website at http://www.human-phenotype-ontology.org/.

Term:Extrapulmonary lobar sequestration
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Accession:HP:0006544 term browser browse the term
Definition:A type of pulmonary sequestration that is completely enclosed in its own pleural sac, occurring above, within, or below the diaphragm, and without communication with the tracheobronchial tree.
Comment:Extralobar sequestration (ELS) may be asymptomatic. Infants with symptomatic lesions may present with respiratory distress, pneumonia, feeding difficulties, hemorrhage, or even congestive heart failure. The sequestered lobe may cause substantial arteriovenous shunting, leading to high-output cardiac failure. Extrapulmonary sequestra nearly all appear on the left side.
Synonyms:exact_synonym: Extralobar sequestration;   Extrapulmonary sequestrum
 related_synonym: Diaphragmatic sequestrum
 xref: UMLS:C4020814;   UMLS:C4025023



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  Human phenotype 82305
    Phenotypic abnormality 81987
      Abnormality of the respiratory system 5361
        Abnormal respiratory system physiology 4926
          Abnormal respiratory system morphology 2685
            Abnormal lung morphology 2402
              Abnormal lung development 247
                Pulmonary sequestration 4
                  Extrapulmonary lobar sequestration 0
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