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Ontology Browser

Term:
Parent Terms Term With Siblings Child Terms
Contracture +     
fibroma +     
Aase Smith Syndrome 
Abdominal Fibromatosis  
Aggressive Fibromatosis +   
Alopecia Contractures Dwarfism Mental Retardation 
Alpha-2-Deficient Collagen Disease 
Anetoderma +   
arterial tortuosity syndrome  
autoimmune disease of skin and connective tissue +   
Axial Mesodermal Dysplasia Spectrum 
Bethlem myopathy +   
bone disease +   
Bone Fragility with Contractures, Arterial Rupture, and Deafness  
Bowen Syndrome 
bullous skin disease +   
Camptodactyly Joint Contractures and Facial Skeletal Dysplasia 
cartilage disease +   
cellulitis +   
chondromyxoid fibroma 
chronic interstitial cystitis 
collagen disease +   
congenital contractural arachnodactyly  
Congenital Contractures, Torticollis, and Malignant Hyperthermia 
Congenital Ectodermal Dysplasia with Hearing Loss 
Congenital Fascial Dystrophy 
congenital limbs-face contractures-hypotonia-developmental delay syndrome  
congenital myopathy 6  
congenital vertical talus  
Connective Tissue Neoplasms +   
contractures, pterygia, and spondylocarpotarsal fusion syndrome +   
cutaneous lupus erythematosus +   
cutis laxa +   
Davenport Donlan Syndrome 
dental pulp disease +   
dermatomyositis +   
Desmoplastic Fibroma 
Dupuytren Contracture +  
A fibromatosis of the palmar fascia characterized by thickening and contracture of the fibrous bands on the palmar surfaces of the hand and fingers. It arises most commonly in men between the ages of 30 and 50.
Dystonia with Ringbinden 
enthesopathy +  
Erosive Arthropathy 
Familial Multiple Trichodiscomas 
Familial Plantar Fibromatosis 
fasciitis +   
fibrodysplasia ossificans progressiva  
funisitis 
Ganglion Cysts 
Growth Failure, Microcephaly, Mental Retardation, Cataracts, Large Joint Contractures, Osteoporosis, Cortical Dysplasia, and Cerebellar Atrophy 
Hereditary Fibrosing Poikiloderma with Tendon Contractures, Myopathy, and Pulmonary Fibrosis  
hereditary spastic paraplegia 18  
Hip Contracture  
histiocytosis-lymphadenopathy plus syndrome  
homocystinuria +   
hyaline fibromatosis syndrome  
Hyperparathyroidism 2  
Iida Kannari Syndrome 
interstitial keratitis +  
interstitial lung disease +   
JOINT CONTRACTURES, OSTEOCHONDROMAS, AND B-CELL LYMPHOMA  
lethal congenital contracture syndrome 3  
Lipedema 
lipodystrophy +   
liver fibroma 
Macleod Fraser syndrome 
Marden-Walker Syndrome  
mediastinitis +  
Mental Retardation Mietens Weber Type 
Mental Retardation, Microcephaly, Growth Retardation, Joint Contractures, and Facial Dysmorphism 
Miles-Carpenter syndrome +   
mucinoses +   
Multiple Polyps and Recurrent Inflammatory Fibroid, Gastrointestinal  
Noonan syndrome +   
ochronosis +   
ossifying fibroma  
Osteopoikilosis +   
Ovarian Fibromata 
Pachydermodactyly, Familial 
Peyronie's disease  
plantar fascial fibromatosis 
pseudoxanthoma elasticum +   
restrictive dermopathy +   
rheumatic disease +   
Rozin Hertz Goodman Syndrome 
Solitary Fibrous Tumors +   
Spondylospinal Thoracic Dysostosis 
Stickler syndrome +   
stiff skin syndrome  
synovitis +   
systemic lupus erythematosus +   
uterine fibroid +   
Van den Ende-Gupta syndrome  
VISS syndrome  
Volkmann contracture 
Warburg-Cinotti Syndrome  
Wiedemann-Steiner syndrome  
Winchester syndrome  
Winter Harding Hyde Syndrome 
X-linked Emery-Dreifuss muscular dystrophy 1  

Synonyms
Exact Synonyms: Dupuytren Disease ;   Dupuytren's Contracture ;   Dupuytren's Disease ;   Dupuytrens Contracture ;   Dupuytrens Disease ;   Palmar Fibromatosis
Narrow Synonyms: PLANTAR FIBROMAS ;   PLANTAR FIBROMATOSIS, FAMILIAL
Primary IDs: MESH:D004387
Alternate IDs: OMIM:126900
Xrefs: EFO:0004229 ;   EFO:1000438
Definition Sources: MESH:D004387

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