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Ontology Browser

Parent Terms Term With Siblings Child Terms
Abnormality of the pulmonary artery +   
Abnormality of the pulmonary veins +   
Agenesis of pulmonary vessels  
Arteriovenous fistula +   
Bone arteriovenous malformation 
Bronchial telangiectasia 
Cerebral arteriovenous malformation  
Gastrointestinal arteriovenous malformation +   
Hepatic arteriovenous malformation  
Muscle arteriovenous malformation 
Paraspinal arteriovenous malformation 
Pelvic arteriovenous malformation 
Peripheral lung neovascularity 
Peripheral pulmonary vessel aplasia  
Pulmonary arteriovenous malformation  
Pulmonary arteriovenous malformation, a condition most commonly associated with hereditary hemorrhagic telangiectasia, is an abnormal communication between the pulmonary artery and pulmonary vein without an intervening capillary communication. HRCT images usually show a coarse spidery appearance of the peripheral vascular markings in the lungs. More specific findings are obtained in the pulmonary angiogram where the normally invisible capillary phase is replaced by irregular vascular channels bridging the peripheral branches of pulmonary arteries and veins.
Pulmonary capillary angioectasia 
Pulmonary capillary hemangiomatosis  
Spinal arteriovenous malformation  
Uterine arteriovenous malformation 

Exact Synonyms: Pulmonary av malformation
Alternate IDs: HP:0002114 ;   HP:0006537
Xrefs: Fyler:2210 ;   UMLS:C1857690
Definition Sources: PMID:30386957, PMID:788535

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