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Pathways

Ontology Browser

Term:
Parent Terms Term With Siblings Child Terms
Aganglionic megacolon +   
An abnormality resulting from a lack of intestinal ganglion cells (i.e., an aganglionic section of bowel) that results in bowel obstruction with enlargement of the colon.
Aganglionosis of the small intestine +  
Ganglioneuromatosis 
Hypoganglionosis 
Total intestinal aganglionosis  

Synonyms
Exact Synonyms: Enlarged colon lacking nerve cells;  Hirschsprung megacolon
Related Synonyms: Hirschsprung disease
Alternate IDs: HP:0002029;  HP:0002030;  HP:0002606;  HP:0004391
Definition Sources: https://orcid.org/0000-0002-0736-9199, PMID:17965226

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