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3-methylcrotonyl-CoA carboxylase complex, mitochondrial (GO:0002169)
Annotations: Rat: (2) Mouse: (2) Human: (2) Chinchilla: (2) Bonobo: (2) Dog: (2) Squirrel: (2) Pig: (2) Naked Mole-rat: (2) Green Monkey: (2)
Parent Terms Term With Siblings Child Terms
3-methylcrotonyl-CoA carboxylase complex, mitochondrial  
A mitochondrial protein complex which is capable of 3-methylcrotonyl-CoA carboxylase activity. In mammals, at least, consists as a dodecamer of 6 alpha and 6 beta subunits. MCCC-alpha has a covalently bound biotin essential for the ATP-dependent carboxylation. MCCC-beta possesses carboxyltransferase activity which presumably is essential for binding to 3-methylcrotonyl-CoA.
Cbp3p-Cbp6 complex 
Ecsit-NDUFAF1 complex 
gamma DNA polymerase complex  
inner mitochondrial membrane protein complex +   
mitochondrial [2Fe-2S] assembly complex  
mitochondrial [4Fe-4S] assembly complex 
mitochondrial creatine kinase complex 
mitochondrial degradosome  
mitochondrial DNA-directed RNA polymerase complex  
mitochondrial electron transfer flavoprotein complex  
mitochondrial endopeptidase Clp complex  
mitochondrial fatty acid beta-oxidation multienzyme complex  
mitochondrial glutamate synthase complex (NADH) 
mitochondrial intermembrane space protein transporter complex  
mitochondrial large ribosomal subunit  
mitochondrial mRNA editing complex 
mitochondrial permeability transition pore complex  
mitochondrial processing peptidase complex  
mitochondrial pyruvate dehydrogenase (lipoamide) phosphatase complex 
mitochondrial ribonuclease P complex  
mitochondrial small ribosomal subunit  
NAGS/NAGK complex 
outer mitochondrial membrane protein complex +   

Exact Synonyms: mitochondrial 3-methylcrotonyl-CoA carboxylase holoenzyme ;   mitochondrial MCCC complex ;   mitochondrial methylcrotonoyl-CoA carboxylase complex
Definition Sources: GOC:bf, GOC:hjd, PMID:15868465, PMID:17360195, PMID:22869039

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