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Primary Progressive Aphasia (DOID:9008293)
Annotations: Rat: (3) Mouse: (3) Human: (3) Chinchilla: (3) Bonobo: (3) Dog: (3) Squirrel: (3) Pig: (3)
Parent Terms Term With Siblings Child Terms
aphasia +     
dementia +     
AIDS Dementia Complex  
Alzheimer's disease +   
amyotrophic lateral sclerosis-parkinsonism/dementia complex 1  
Aphasia, Broca 
Aphasia, Conduction 
Ataxia with Myoclonic Epilepsy and Presenile Dementia 
Cerebral Amyloidosis with Spongiform Encephalopathy +   
Creutzfeldt-Jakob disease +   
deafness-dystonia-optic neuronopathy syndrome  
Dementia/Parkinsonism with Non-Alzheimer Amyloid Plaques 
Diffuse Neurofibrillary Tangles with Calcification 
Familial Developmental Dysphasia 
Frontotemporal Lobar Degeneration +   
Huntington's disease +   
Huntington's disease-like 2  
ITM2B-related cerebral amyloid angiopathy 2  
juvenile amyotrophic lateral sclerosis with dementia 
Kluver-Bucy syndrome +  
Kohlschutter-Tonz syndrome  
Lewy body dementia +   
MAST syndrome  
Motor Neuron Disease with Dementia and Ophthalmoplegia 
nominal aphasia 
Presenile Dementia, Kraepelin Type 
Primary Progressive Aphasia +   
A progressive form of dementia characterized by the global loss of language abilities and initial preservation of other cognitive functions. Fluent and nonfluent subtypes have been described. Eventually a pattern of global cognitive dysfunction, similar to ALZHEIMER DISEASE, emerges. Pathologically, there are no Alzheimer or PICK DISEASE like changes, however, spongiform changes of cortical layers II and III are present in the TEMPORAL LOBE and FRONTAL LOBE. (From Brain 1998 Jan;121(Pt 1):115-26)
Spastic Paraplegia, Optic Atrophy, and Dementia 
vascular dementia +   
Wernicke Aphasia 
Wright Dyck Syndrome 

Exact Synonyms: Aphasia, Primary Progressive, Susceptibility To ;   Mesulam Syndrome ;   Mesulam's Syndrome ;   Primary Progressive Aphasias
Primary IDs: MESH:D018888 ;   RDO:0007243
Definition Sources: MESH:D018888

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