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Ontology Browser

Term:
Anti-Neutrophil Cytoplasmic Antibody-Associated Vasculitis (DOID:9003819)
Annotations: Rat: (32) Mouse: (31) Human: (34) Chinchilla: (28) Bonobo: (32) Dog: (31) Squirrel: (28) Pig: (32) Naked Mole-rat: (28) Green Monkey: (31)
Parent Terms Term With Siblings Child Terms
autoimmune disease +     
Acquired Pulmonary Alveolar Proteinosis  
Addison's disease +   
Alpha/Beta T-Cell Lymphopenia with Gamma/Delta T-Cell Expansion, Severe Cytomegalovirus Infection, and Autoimmunity  
Anti-Neutrophil Cytoplasmic Antibody-Associated Vasculitis +   
Group of systemic vasculitis with a strong association with ANCA. The disorders are characterized by necrotizing inflammation of small and medium size vessels, with little or no immune-complex deposits in vessel walls.
antisynthetase syndrome  
autoimmune disease of blood +   
autoimmune disease of cardiovascular system +   
autoimmune disease of endocrine system +   
autoimmune disease of exocrine system +   
autoimmune disease of gastrointestinal tract +   
autoimmune disease of musculoskeletal system +   
autoimmune disease of the nervous system +   
autoimmune disease of urogenital tract +   
Autoimmune Hypophysitis 
autoimmune interstitial lung, joint, and kidney disease  
autoimmune lymphoproliferative syndrome +   
Autoimmune Progesterone Dermatitis 
CINCA syndrome  
Combined Immunodeficiency with Autoimmunity and Spondylometaphyseal Dysplasia  
common variable immunodeficiency +   
Diabetes Mellitus, Congenital Autoimmune  
Experimental Autoimmune Uveitis +   
familial mediterranean fever +   
Gardner-Diamond Syndrome 
IgA glomerulonephritis +   
IgG4-related disease  
IMMUNE DYSREGULATION, AUTOIMMUNITY, AND AUTOINFLAMMATION  
immune dysregulation-polyendocrinopathy-enteropathy-X-linked syndrome  
Immunodeficiency 113  
Immunodeficiency 78 with Autoimmunity and Developmental Delay  
Immunodeficiency 85  
Immunodeficiency 87 and Autoimmunity  
Immunodeficiency 89 and Autoimmunity  
Jaccoud's syndrome 
Linear IgA Bullous Dermatosis 
membranous glomerulonephritis  
Multisystem Autoimmune Disease with Facial Dysmorphism  
Multisystem Autoimmune Disease, Infantile-Onset +   
Pediatric Autoimmune Neuropsychiatric Disorders Associated with Streptococcal infections 
polyarteritis nodosa +   
Rheumatoid Vasculitis 
Spondyloenchondrodysplasia  
VEXAS syndrome  
X-linked immunodeficiency with magnesium defect, Epstein-Barr virus infection, and neoplasia  

Synonyms
Exact Synonyms: ANCA Associated Vasculitides ;   ANCA Associated Vasculitis ;   ANCA-Associated Vasculitide ;   Pauci Immune Vasculitis ;   Pauci-Immune Vasculitides ;   anti-neutrophil antibody associated vasculitis
Primary IDs: MESH:D056648
Xrefs: EFO:0004826 ;   MONDO:0015492
Definition Sources: MESH:D056648

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