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Ontology Browser

Term:
desmoplastic small round cell tumor (DOID:6785)
Annotations: Rat: (1) Mouse: (1) Human: (2) Chinchilla: (1) Bonobo: (1) Dog: (1) Squirrel: (1) Pig: (1)
Parent Terms Term With Siblings Child Terms
sarcoma +     
adenosarcoma +  
alveolar soft part sarcoma  
angiosarcoma +   
anus sarcoma +  
bile duct sarcoma +  
bladder sarcoma 
bone sarcoma +   
breast sarcoma +   
carcinosarcoma +   
central nervous system sarcoma +   
clear cell sarcoma +   
colon sarcoma +  
dendritic cell sarcoma +  
desmoplastic small round cell tumor  
A sarcoma that is characterized by a recurrent chromosomal translocation t(11;22)(p13;q12) and the presence of small round cells in a desmoplastic stroma. It usually affects children and young adults. The most common site of involvement is the abdomen. Patients usually present with abdominal distention, pain, ascites, and a palpable abdominal mass. (DO)
endometrial stromal tumor +   
epithelioid sarcoma +   
esophagus sarcoma +  
Ewing sarcoma +   
Experimental Sarcoma +   
fibrosarcoma +   
gallbladder sarcoma +  
germ cell and embryonal cancer +   
heart sarcoma +  
Kaposi's sarcoma +   
kidney sarcoma +  
larynx sarcoma +  
leiomyosarcoma +   
liposarcoma +   
liver sarcoma +   
lung sarcoma +  
lymphangiosarcoma +   
malignant fibrous histiocytoma +   
malignant hemangioma +   
mast-cell sarcoma 
mediastinum sarcoma +   
Mesodermal Mixed Tumor 
muscle cancer +   
myeloid sarcoma +   
myxofibrosarcoma  
myxosarcoma 
orbit sarcoma +  
ovary sarcoma +   
pancreas sarcoma 
paranasal sinus sarcoma 
penis sarcoma 
Phyllodes Tumor +   
Plexosarcoma 
prostate sarcoma +  
rectum sarcoma +  
sarcomatosis +  
skin sarcoma +   
small cell sarcoma +   
small intestinal sarcoma +  
spindle cell sarcoma +   
synovial sarcoma +   
testis sarcoma +  
thyroid sarcoma +   
trachea sarcoma 
uterine corpus sarcoma +   
vagina sarcoma +  
vulvar sarcoma +   

Synonyms
Exact Synonyms: desmoplastic small cell tumor ;   desmoplastic small round-cell neoplasm ;   desmoplastic small-cell tumors
Primary IDs: MESH:D058405
Xrefs: GARD:6265 ;   NCI:C8300
Definition Sources: https://en.wikipedia.org/wiki/Desmoplastic_small-round-cell_tumor "DO" "DO", https://www.cancer.gov/pediatric-adult-rare-tumor/rare-tumors/rare-soft-tissue-tumors/desmoplastic-small-round-cell-tumors "DO" "DO"

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