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Ontology Browser

Term:
Parent Terms Term With Siblings Child Terms
Castleman disease +     
Angiofollicular Ganglionic Hyperplasia 
multicentric Castleman disease  
A Castleman disease characterized by systemic inflammatory symptoms, polyclonal lymphoproliferation, cytopenias, and multiple organ system dysfunction caused by a cytokine storm often including interleukin-6. (DO)

Synonyms
Exact Synonyms: HHV-8-associated multicentric Castleman disease ;   HHV8 Multicentric Castleman Disease ;   Idiopathic multicentric Castleman's disease ;   KSHV Muticentric Castleman Disease ;   KSHV-Associated Multicentric Castleman Disease ;   MCD ;   Multi-centric Castleman's Disease ;   Multicentric Castleman's disease ;   Multicentric plasma cell variant of Castleman's disease ;   PMCD ;   Tafro syndrome ;   multicentric giant lymph node hyperplasia ;   plasmablastic multicentric Castleman disease
Primary IDs: MESH:C537372
Xrefs: GARD:9644 ;   NCI:C27855 ;   ORDO:93686
Definition Sources: http://www.bloodjournal.org/content/129/12/1646 "DO" "DO", https://rarediseases.info.nih.gov/diseases/9644/multicentric-castleman-disease "DO" "DO"

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