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Ontology Browser

Term:
desquamative interstitial pneumonia (DOID:0050158)
Annotations: Rat: (1) Mouse: (1) Human: (1) Chinchilla: (0) Bonobo: (0) Dog: (0) Squirrel: (0) Pig: (0)
Parent Terms Term With Siblings Child Terms
acute interstitial pneumonia  
Adrenocortical Hypofunction, Chronic Primary Congenital 
adrenocorticotropic hormone deficiency  
advanced sleep phase syndrome 3  
age related macular degeneration 8  
Alagille syndrome  
Alpha-2-Deficient Collagen Disease 
apparent mineralocorticoid excess syndrome  
Aquaporin 1 Deficiency 
aspartylglucosaminuria  
ataxic cerebral palsy 
atrial heart septal defect 3  
atrial heart septal defect 4  
Autoimmune Interstitial Lung, Joint, and Kidney Disease  
autoimmune lymphoproliferative syndrome +   
brachydactyly type A1B 
brachydactyly type A1C  
brachydactyly type A1D  
brachydactyly type B1  
brachydactyly type B2  
brachydactyly type E1  
brachydactyly type E2  
bronchiolitis obliterans +   
CADASIL +   
CAKUT2  
cataract 23  
cataract 25 
cataract 26 multiple types 
cataract 27  
cataract 28 
Cenani-Lenz syndactyly syndrome  
CHARGE syndrome  
chromosomal disease +   
complement factor I deficiency  
complex cortical dysplasia with other brain malformations 1  
complex cortical dysplasia with other brain malformations 2  
complex cortical dysplasia with other brain malformations 3  
complex cortical dysplasia with other brain malformations 4  
complex cortical dysplasia with other brain malformations 5  
complex cortical dysplasia with other brain malformations 6  
complex cortical dysplasia with other brain malformations 7  
congenital diarrhea +   
congenital hemolytic anemia +   
Congenital Hepatic Fibrosis  
congenital hypoplastic anemia +   
congenital muscular dystrophy +   
congenital myasthenic syndrome +   
Congenital Pain Insensitivity +   
cryptogenic organizing pneumonia  
desquamative interstitial pneumonia  
An idiopathic interstitial pneumonia that is characterized by the accumulation of bronchiolocentric alveolar macrophages in alveolar spaces and interstitial inflammation and involves mild bronchiolar fibrosis and chronic inflammation. (DO)
Dwarfism +   
extrinsic allergic alveolitis +   
Familial Cirrhosis +   
Familial Dysalbuminemic Hyperthyroxinemia  
Familial Hemophagocytic Lymphohistiocytoses +   
familial hypertrophic cardiomyopathy +   
Familial Lipochrome Histiocytosis 
Familial Mixed Cryoglobulinemia  
Familial Temporal Epilepsy +   
frontotemporal dementia and/or amyotrophic lateral sclerosis-3  
frontotemporal dementia and/or amyotrophic lateral sclerosis-4  
Genetic Skin Diseases +   
Goodpasture syndrome +   
granulomatosis with polyangiitis +   
hereditary angioedema +   
Hereditary Bilateral Parotidomegaly 
Hereditary Epistaxis 
Hereditary Eye Diseases +   
hereditary lymphedema +   
Hereditary Neoplastic Syndromes +   
hypogonadotropic hypogonadism 5 with or without anosmia +   
idiopathic interstitial pneumonia +   
idiopathic pulmonary fibrosis  
inherited metabolic disorder +   
INTERSTITIAL LUNG AND LIVER DISEASE  
Interstitial Lung Disease, Nephrotic Syndrome, and Epidermolysis Bullosa, Congenital  
Isolated Prolactin Deficiency 
Kallmann syndrome +   
Laminopathies  
Langerhans-cell histiocytosis +   
Lennox-Gastaut syndrome  
lymphoid interstitial pneumonia 
Marfan syndrome +   
monogenic disease +   
Nervous System Heredodegenerative Disorders +   
Nonimmune Chronic Idiopathic Neutropenia, Adult  
nonspecific interstitial pneumonia 
osteochondrodysplasia +   
pneumoconiosis +   
polygenic disease +   
primary hypertrophic osteoarthropathy +   
progressive familial intrahepatic cholestasis +   
pulmonary alveolar microlithiasis  
pulmonary fibrosis +   
pulmonary sarcoidosis  
Radiation Pneumonitis  
Rajab Interstitial Lung Disease with Brain Calcifications +   
rheumatoid arthritis interstitial lung disease 
Sacral Agenesis with Vertebral Anomalies  
Surfactant Dysfunction  
Surfactant Metabolism Dysfunction, Pulmonary, 1  
Surfactant Metabolism Dysfunction, Pulmonary, 2  
Surfactant Metabolism Dysfunction, Pulmonary, 3  
Surfactant Metabolism Dysfunction, Pulmonary, 5  
yellow nail syndrome +  

Synonyms
Exact Synonyms: DIP ;   ILD, DESQUAMATIVE ;   Interstitial Lung Disease, Desquamative ;   Interstitial Pneumonitis, Desquamative, Familial ;   Pneumonia, Desquamative Interstitial, Familial ;   RBILD ;   respiratory bronchiolitis-associated interstitial lung disease
Primary IDs: MESH:C562470 ;   RDO:0012185
Alternate IDs: OMIM:263000
Xrefs: ICD10CM:J84.115 ;   ICD10CM:J84.117 ;   ICD9CM:516.37 ;   NCI:C35288
Definition Sources: http://ncit.nci.nih.gov/ncitbrowser/ConceptReport.jsp?dictionary=NCI_Thesaurus&version=14.10d&code=C35288 "DO", http://www.merck.com/mmhe/sec04/ch050/ch050b.html?qt=idiopathic%20interstitial%20pneumonia&alt=sh "DO", https://www.ncbi.nlm.nih.gov/pubmed/11790668 "DO", https://www.ncbi.nlm.nih.gov/pubmed/16142185 "DO", https://www.ncbi.nlm.nih.gov/pubmed/16456642 "DO", https://www.ncbi.nlm.nih.gov/pubmed/23001799 "DO"

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RGD is funded by grant HL64541 from the National Heart, Lung, and Blood Institute on behalf of the NIH.