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Ontology Browser

Term:
desquamative interstitial pneumonia (DOID:0050158)
Annotations: Rat: (1) Mouse: (1) Human: (1) Chinchilla: (1) Bonobo: (1) Dog: (1) Squirrel: (1) Pig: (1)
Parent Terms Term With Siblings Child Terms
acute interstitial pneumonia 
Adrenocortical Hypofunction, Chronic Primary Congenital 
adrenocorticotropic hormone deficiency  
advanced sleep phase syndrome 3  
age related macular degeneration 8  
Alpha-2-Deficient Collagen Disease 
Aquaporin 1 Deficiency 
ataxic cerebral palsy 
atrial heart septal defect 3  
atrial heart septal defect 4  
Autoimmune Interstitial Lung, Joint, and Kidney Disease  
autoimmune lymphoproliferative syndrome +   
BOCKENHEIMER SYNDROME  
brachydactyly type A1B 
brachydactyly type A1C  
brachydactyly type A1D  
brachydactyly type B1  
brachydactyly type B2  
brachydactyly type E1  
brachydactyly type E2  
bronchiolitis obliterans +   
CADASIL +   
CAKUT2  
cataract 25 
cataract 26 multiple types 
cataract 27  
cataract 28 
Cenani-Lenz syndactyly syndrome  
chromosomal disease +   
complex cortical dysplasia with other brain malformations 1  
complex cortical dysplasia with other brain malformations 2  
complex cortical dysplasia with other brain malformations 3  
complex cortical dysplasia with other brain malformations 4  
complex cortical dysplasia with other brain malformations 5  
complex cortical dysplasia with other brain malformations 6  
Congenital Hepatic Fibrosis  
Congenital Pain Insensitivity +   
cryptogenic organizing pneumonia  
desquamative interstitial pneumonia  
An idiopathic interstitial pneumonia that is characterized by the accumulation of bronchiolocentric alveolar macrophages in alveolar spaces and interstitial inflammation and involves mild bronchiolar fibrosis and chronic inflammation. (DO)
Dwarfism +   
extrinsic allergic alveolitis +   
Familial Cirrhosis +   
Familial Dysalbuminemic Hyperthyroxinemia  
Familial Hemophagocytic Lymphohistiocytoses +   
familial hypertrophic cardiomyopathy +   
Familial Lipochrome Histiocytosis 
Familial Mixed Cryoglobulinemia  
Familial Temporal Epilepsy +   
frontotemporal dementia and/or amyotrophic lateral sclerosis-3  
frontotemporal dementia and/or amyotrophic lateral sclerosis-4  
Genetic Skin Diseases +   
Goodpasture syndrome +   
granulomatosis with polyangiitis +   
Hereditary Bilateral Parotidomegaly 
Hereditary Epistaxis 
Hereditary Eye Diseases +   
hereditary lymphedema +   
Hereditary Neoplastic Syndromes +   
hypogonadotropic hypogonadism 5 with or without anosmia +   
idiopathic interstitial pneumonia +   
idiopathic pulmonary fibrosis  
inherited metabolic disorder +   
INTERSTITIAL LUNG AND LIVER DISEASE  
Interstitial Lung Disease 1  
Isolated Prolactin Deficiency 
Junctional Epidermolysis Bullosa 7, with Interstitial Lung Disease and Nephrotic Syndrome  
Kallmann syndrome +   
Laminopathies +   
Langerhans-cell histiocytosis +   
Lennox-Gastaut syndrome  
lymphoid interstitial pneumonia 
Marfan syndrome +   
monogenic disease +   
Nervous System Heredodegenerative Disorders +   
Nonimmune Chronic Idiopathic Neutropenia, Adult  
nonspecific interstitial pneumonia 
osteochondrodysplasia +   
pneumoconiosis +   
polygenic disease +   
primary hypertrophic osteoarthropathy +   
progressive familial intrahepatic cholestasis +   
pulmonary fibrosis +   
pulmonary sarcoidosis  
Pulmonary Surfactant Metabolism Dysfunction 1  
Pulmonary Surfactant Metabolism Dysfunction 2  
Pulmonary Surfactant Metabolism Dysfunction 3  
Pulmonary Surfactant Metabolism Dysfunction 5  
Radiation Pneumonitis  
Rajab Interstitial Lung Disease with Brain Calcifications +   
rheumatoid arthritis interstitial lung disease 
Sacral Agenesis with Vertebral Anomalies  
Surfactant Dysfunction  
yellow nail syndrome +  

Synonyms
Exact Synonyms: DIP ;   ILD, DESQUAMATIVE ;   Interstitial Lung Disease, Desquamative ;   RBILD ;   familial desquamative interstitial pneumonia ;   familial desquamative interstitial pneumonitis ;   respiratory bronchiolitis-associated interstitial lung disease
Primary IDs: MESH:C562470
Alternate IDs: OMIM:263000
Xrefs: ICD10CM:J84.117 ;   ICD9CM:516.37 ;   NCI:C35288
Definition Sources: http://ncit.nci.nih.gov/ncitbrowser/ConceptReport.jsp?dictionary=NCI_Thesaurus&version=14.10d&code=C35288 "DO" "DO", http://www.merck.com/mmhe/sec04/ch050/ch050b.html?qt=idiopathic%20interstitial%20pneumonia&alt=sh "DO" "DO", https://www.ncbi.nlm.nih.gov/pubmed/11790668 "DO" "DO", https://www.ncbi.nlm.nih.gov/pubmed/16142185 "DO" "DO", https://www.ncbi.nlm.nih.gov/pubmed/16456642 "DO" "DO", https://www.ncbi.nlm.nih.gov/pubmed/23001799 "DO" "DO"

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