PATHWAY ONTOLOGY - ANNOTATIONS
The Pathway Ontology (PW), is currently being developed at the Rat Genome Database. For more information about this vocabulary, please see Petri et al. The rat genome database pathway portal. Database (Oxford). 2011 Apr 8;2011:bar010. Print 2011 or contact us (http://rgd.mcw.edu/contact/index.shtml ).
Term: metabolic pathway of other amino acids
Accession: PW:0000132
browse the term
Definition: Those metabolic reactions involved in the synthesis, utilization and/or degradation of amino acids other than the common 20 amino acids found in protein. Some of these amino acids like carnitine or homocysteine derive from primary amino acids.
G
ABAT
4-aminobutyrate aminotransferase
ISO
SMPDB
SMP:00007
NCBI chr 6:33,385,779...33,471,348
Ensembl chr 6:33,376,996...33,471,326
G
ALDH2
aldehyde dehydrogenase 2 family member
ISO
SMPDB
SMP:00007
NCBI chr26:9,319,109...9,361,021
G
ALDH6A1
aldehyde dehydrogenase 6 family member A1
ISO
SMPDB
SMP:00007
NCBI chr 8:47,280,872...47,304,460
Ensembl chr 8:47,282,235...47,304,283
G
AOC3
amine oxidase copper containing 3
ISO
SMPDB
SMP:00007
NCBI chr 9:20,158,581...20,179,773
Ensembl chr 9:20,157,410...20,241,376
G
CNDP1
carnosine dipeptidase 1
ISO
SMPDB
SMP:00007
NCBI chr 1:4,875,790...4,912,148
Ensembl chr 1:4,876,794...4,911,976
G
DPYD
dihydropyrimidine dehydrogenase
ISO
SMPDB
SMP:00007
NCBI chr 6:51,789,786...52,564,802
Ensembl chr 6:51,814,573...52,580,923
G
DPYS
dihydropyrimidinase
ISO
SMPDB
SMP:00007
NCBI chr13:5,583,795...5,659,355
Ensembl chr13:5,583,801...5,659,463
G
GAD1
glutamate decarboxylase 1
ISO
SMPDB
SMP:00007
NCBI chr36:15,351,289...15,391,701
Ensembl chr36:15,349,683...15,391,824
G
UPB1
beta-ureidopropionase 1
ISO
SMPDB
SMP:00007
NCBI chr26:28,194,968...28,225,977
Ensembl chr26:28,195,081...28,225,567
G
ALDH9A1
aldehyde dehydrogenase 9 family member A1
ISO
SMPDB
SMP:00465
NCBI chr38:17,644,464...17,664,462
Ensembl chr38:17,644,459...17,663,886
G
BBOX1
gamma-butyrobetaine hydroxylase 1
ISO
SMPDB
SMP:00465
NCBI chr21:47,707,648...47,766,732
Ensembl chr21:47,706,717...47,766,503
G
SETD7
SET domain containing 7, histone lysine methyltransferase
ISO
SMPDB
SMP:00465
NCBI chr19:3,186,620...3,229,305
Ensembl chr19:3,186,906...3,224,113
G
SHMT1
serine hydroxymethyltransferase 1
ISO
SMPDB
SMP:00465
NCBI chr 5:41,221,531...41,248,653
Ensembl chr 5:41,221,562...41,253,166
G
TMLHE
trimethyllysine hydroxylase, epsilon
ISO
SMPDB
SMP:00465
NCBI chr X:123,322,773...123,438,999
Ensembl chr X:123,324,729...123,438,947
G
CKM
creatine kinase, M-type
ISO
RGD
PMID:12069495
RGD:1359082
NCBI chr 1:110,210,158...110,218,937
Ensembl chr 1:110,210,152...110,343,383
G
GAMT
guanidinoacetate N-methyltransferase
ISO
RGD
PMID:12069495
RGD:1359082
NCBI chr20:57,440,698...57,442,588
G
GATM
glycine amidinotransferase
ISO
RGD
PMID:8021264
RGD:70746
NCBI chr30:11,724,446...11,742,214
Ensembl chr30:11,723,519...11,742,214
G
SLC6A8
solute carrier family 6 member 8
ISO
RGD
PMID:12069495
RGD:1359082
NCBI chr X:121,505,117...121,511,674
Ensembl chr X:121,505,141...121,510,347
G
ANPEP
alanyl aminopeptidase, membrane
ISO
SMPDB
SMP:00015
NCBI chr 3:52,764,418...52,779,516
Ensembl chr 3:52,764,418...52,779,746
G
CASP7
caspase 7
ISO
SMPDB
SMP:00015
NCBI chr28:24,599,866...24,630,018
Ensembl chr28:24,599,493...24,628,668
G
GCLC
glutamate-cysteine ligase catalytic subunit
ISO
SMPDB RGD
PMID:16137247 PMID:16183645
RGD:1582661 RGD:1582663 SMP:00015
NCBI chr12:20,999,815...21,047,779
Ensembl chr12:21,000,792...21,047,779
G
GCLM
glutamate-cysteine ligase modifier subunit
ISO
SMPDB RGD
PMID:16137247 PMID:16183645
RGD:1582661 RGD:1582663 SMP:00015
NCBI chr 6:55,204,602...55,244,217
G
GGCT
gamma-glutamylcyclotransferase
ISO
SMPDB
SMP:00015
NCBI chr14:43,244,220...43,252,930
Ensembl chr14:43,245,102...43,252,923
G
GGT6
gamma-glutamyltransferase 6
ISO
SMPDB
SMP:00015
NCBI chr 5:30,540,461...30,543,878
Ensembl chr 5:30,540,450...30,543,773
G
GPX1
glutathione peroxidase 1
ISO
SMPDB
SMP:00015
NCBI chr20:39,889,165...39,890,253
Ensembl chr20:39,889,174...39,890,260
G
GSR
glutathione-disulfide reductase
ISO
SMPDB
SMP:00015
NCBI chr16:33,633,949...33,680,411
Ensembl chr16:33,633,968...33,679,752
G
GSS
glutathione synthetase
ISO
SMPDB
SMP:00015
NCBI chr24:23,973,807...24,000,281
Ensembl chr24:23,901,045...23,997,286
G
GSTO2
glutathione S-transferase omega 2
ISO
SMPDB
SMP:00015
NCBI chr28:16,580,250...16,604,977
Ensembl chr28:16,586,777...16,604,976
G
OPLAH
5-oxoprolinase, ATP-hydrolysing
ISO
SMPDB
SMP:00015
NCBI chr13:37,555,035...37,564,241
Ensembl chr13:37,555,045...37,564,810
G
AHCY
adenosylhomocysteinase
ISO
RGD
PMID:11741948 PMID:20814827
RGD:7242426 RGD:730275
NCBI chr24:23,410,553...23,423,494
Ensembl chr24:23,411,140...23,419,767
G
AS3MT
arsenite methyltransferase
ISO
RGD
PMID:11790780
RGD:625365
NCBI chr28:15,334,141...15,350,749
G
CARM1
coactivator associated arginine methyltransferase 1
ISO
RGD
PMID:15866169
RGD:1359044
NCBI chr20:50,328,466...50,371,845
Ensembl chr20:50,331,030...50,348,195
G
COMT
catechol-O-methyltransferase
ISO
RGD
PMID:12584150
RGD:1359089
NCBI chr26:29,359,930...29,381,854
Ensembl chr26:29,360,356...29,366,008
G
DNMT1
DNA methyltransferase 1
ISO
RGD
PMID:12473678
RGD:1359078
NCBI chr20:50,872,213...50,928,352
Ensembl chr20:50,879,527...50,928,029
G
GAMT
guanidinoacetate N-methyltransferase
ISO
RGD
PMID:15533043
RGD:1359081
NCBI chr20:57,440,698...57,442,588
G
GNMT
glycine N-methyltransferase
ISO
RGD
PMID:15347642
RGD:1359070
NCBI chr12:11,500,363...11,503,075
Ensembl chr12:11,500,392...11,503,481
G
HNMT
histamine N-methyltransferase
ISO
RGD
PMID:11566133
RGD:1359041
NCBI chr19:40,656,266...40,702,498
Ensembl chr19:40,655,161...40,702,218
G
MTHFR
methylenetetrahydrofolate reductase
ISO
RGD
PMID:20814827
RGD:7242426
NCBI chr 2:84,445,526...84,457,435
Ensembl chr 2:84,380,919...84,536,818
G
NNMT
nicotinamide N-methyltransferase
ISO
RGD
PMID:15922112
RGD:1359084
NCBI chr 5:19,026,514...19,044,154
Ensembl chr 5:19,026,556...19,044,016
G
PCMT1
protein-L-isoaspartate (D-aspartate) O-methyltransferase
ISO
RGD
PMID:8263531
RGD:729481
NCBI chr 1:40,494,441...40,539,453
Ensembl chr 1:40,494,461...40,538,937
G
PEMT
phosphatidylethanolamine N-methyltransferase
ISO
RGD
PMID:8344945
RGD:729486
NCBI chr 5:41,871,685...41,960,831
Ensembl chr 5:41,872,108...41,960,828
G
PNMT
phenylethanolamine N-methyltransferase
ISO
RGD
PMID:12438084
RGD:1359087
NCBI chr 9:22,808,505...22,810,587
Ensembl chr 9:22,808,601...22,810,551
G
PRMT1
protein arginine methyltransferase 1
ISO
RGD
PMID:15866169
RGD:1359044
NCBI chr 1:106,849,864...106,859,896
Ensembl chr 1:106,849,864...106,874,075
G
PRMT5
protein arginine methyltransferase 5
ISO
RGD
PMID:15866169
RGD:1359044
NCBI chr 8:3,248,349...3,257,567
Ensembl chr 8:3,248,404...3,257,456
G
PRMT6
protein arginine methyltransferase 6
ISO
RGD
PMID:15866169
RGD:1359044
NCBI chr 6:44,475,829...44,478,215
Ensembl chr 6:44,477,030...44,478,160
G
RNMT
RNA guanine-7 methyltransferase
ISO
RGD
PMID:11472630
RGD:1359071
NCBI chr 1:24,465,634...24,499,526
Ensembl chr 1:24,430,063...24,497,206
G
SETDB1
SET domain bifurcated histone lysine methyltransferase 1
ISO
RGD
PMID:11959841
RGD:1359072
NCBI chr17:60,035,819...60,069,721
Ensembl chr17:60,037,379...60,069,551
G
MTHFR
methylenetetrahydrofolate reductase
ISO
RGD
PMID:20814827
RGD:7242426
NCBI chr 2:84,445,526...84,457,435
Ensembl chr 2:84,380,919...84,536,818
G
MTR
5-methyltetrahydrofolate-homocysteine methyltransferase
ISO
RGD
PMID:15845641 PMID:20814827
RGD:1359026 RGD:7242426
NCBI chr 4:3,219,851...3,328,000
Ensembl chr 4:3,215,090...3,328,115
G
MTRR
5-methyltetrahydrofolate-homocysteine methyltransferase reductase
ISO
RGD
PMID:15979034 PMID:20814827
RGD:1359037 RGD:7242426
NCBI chr34:6,068,572...6,119,580
Ensembl chr34:6,070,046...6,098,312
G
AHCY
adenosylhomocysteinase
ISO
SMPDB
SMP:00123
NCBI chr24:23,410,553...23,423,494
Ensembl chr24:23,411,140...23,419,767
G
ALDH7A1
aldehyde dehydrogenase 7 family member A1
ISO
SMPDB
SMP:00123
NCBI chr11:15,828,581...15,878,556
Ensembl chr11:15,815,936...15,878,516
G
BHMT
betaine--homocysteine S-methyltransferase
ISO
SMPDB RGD
PMID:15845641 PMID:20346934 PMID:20814827
RGD:1359026 RGD:7242426 RGD:7242428 SMP:00123
NCBI chr 3:27,732,381...27,752,168
Ensembl chr 3:27,734,108...27,752,046
G
CHDH
choline dehydrogenase
ISO
SMPDB
SMP:00123
NCBI chr20:36,150,214...36,188,976
Ensembl chr20:36,150,229...36,187,068
G
MAT2A
methionine adenosyltransferase 2A
ISO
SMPDB
SMP:00123
NCBI chr17:39,525,635...39,532,512
Ensembl chr17:39,525,626...39,532,512
G
MAT2B
methionine adenosyltransferase 2B
ISO
SMPDB
SMP:00123
NCBI chr 4:47,703,991...47,726,363
Ensembl chr 4:47,709,576...47,726,360
G
MTR
5-methyltetrahydrofolate-homocysteine methyltransferase
ISO
SMPDB
SMP:00123
NCBI chr 4:3,219,851...3,328,000
Ensembl chr 4:3,215,090...3,328,115
G
PEMT
phosphatidylethanolamine N-methyltransferase
ISO
SMPDB
SMP:00123
NCBI chr 5:41,871,685...41,960,831
Ensembl chr 5:41,872,108...41,960,828
G
AHCY
adenosylhomocysteinase
ISO
SMPDB
SMP:00029
NCBI chr24:23,410,553...23,423,494
Ensembl chr24:23,411,140...23,419,767
G
CBS
cystathionine beta-synthase
ISO
SMPDB
SMP:00029
NCBI chr31:37,230,900...37,247,170
G
CTH
cystathionine gamma-lyase
ISO
SMPDB
SMP:00029
NCBI chr 6:75,324,328...75,348,476
Ensembl chr 6:75,324,787...75,349,451
G
GGT1
gamma-glutamyltransferase 1
ISO
SMPDB
SMP:00029
NCBI chr26:28,301,455...28,315,029
G
MARS1
methionyl-tRNA synthetase 1
ISO
SMPDB
SMP:00029
NCBI chr10:1,588,503...1,606,752
Ensembl chr10:1,588,875...1,606,750
G
MAT2A
methionine adenosyltransferase 2A
ISO
SMPDB
SMP:00029
NCBI chr17:39,525,635...39,532,512
Ensembl chr17:39,525,626...39,532,512
G
MAT2B
methionine adenosyltransferase 2B
ISO
SMPDB
SMP:00029
NCBI chr 4:47,703,991...47,726,363
Ensembl chr 4:47,709,576...47,726,360
G
PAPSS1
3'-phosphoadenosine 5'-phosphosulfate synthase 1
ISO
SMPDB
SMP:00029
NCBI chr32:28,136,741...28,235,529
Ensembl chr32:28,136,909...28,235,484
G
SCLY
selenocysteine lyase
ISO
SMPDB
SMP:00029
NCBI chr25:48,574,648...48,608,367
Ensembl chr25:48,574,130...48,632,035
G
SEPHS2
selenophosphate synthetase 2
ISO
SMPDB
SMP:00029
NCBI chr 6:17,667,766...17,670,007
G
SH3BP5
SH3 domain binding protein 5
ISO
SMPDB
SMP:00029
NCBI chr23:27,202,880...27,217,753
Ensembl chr23:27,202,875...27,334,010
G
ADO
2-aminoethanethiol dioxygenase
ISO
SMPDB
SMP:00021
NCBI chr 4:14,698,582...14,702,635
Ensembl chr 4:14,698,616...14,699,428
G
CDO1
cysteine dioxygenase type 1
ISO
SMPDB
SMP:00021
NCBI chr11:5,512,996...5,524,556
Ensembl chr11:5,371,378...5,524,562
G
CSAD
cysteine sulfinic acid decarboxylase
ISO
SMPDB
SMP:00021
NCBI chr27:2,005,482...2,036,703
Ensembl chr27:2,005,355...2,036,228
G
GAD1
glutamate decarboxylase 1
ISO
SMPDB
SMP:00021
NCBI chr36:15,351,289...15,391,701
Ensembl chr36:15,349,683...15,391,824
G
GGT6
gamma-glutamyltransferase 6
ISO
SMPDB
SMP:00021
NCBI chr 5:30,540,461...30,543,878
Ensembl chr 5:30,540,450...30,543,773
G
CBS
cystathionine beta-synthase
ISO
SMPDB RGD
PMID:20162368
RGD:7242427 SMP:00455
NCBI chr31:37,230,900...37,247,170
G
CDO1
cysteine dioxygenase type 1
ISO
RGD
PMID:20162368
RGD:7242427
NCBI chr11:5,512,996...5,524,556
Ensembl chr11:5,371,378...5,524,562
G
CSAD
cysteine sulfinic acid decarboxylase
ISO
RGD
PMID:20162368
RGD:7242427
NCBI chr27:2,005,482...2,036,703
Ensembl chr27:2,005,355...2,036,228
G
CTH
cystathionine gamma-lyase
ISO
SMPDB RGD
PMID:20162368
RGD:7242427 SMP:00455
NCBI chr 6:75,324,328...75,348,476
Ensembl chr 6:75,324,787...75,349,451
Term paths to the root one shortest all shortest one longest all longest one shortest and longest all