PATHWAY ONTOLOGY - ANNOTATIONS
The Pathway Ontology (PW), is currently being developed at the Rat Genome Database. For more information about this vocabulary, please see Petri et al. The rat genome database pathway portal. Database (Oxford). 2011 Apr 8;2011:bar010. Print 2011 or contact us (http://rgd.mcw.edu/contact/index.shtml ).
Term: metabolic pathway of other amino acids
Accession: PW:0000132
browse the term
Definition: Those metabolic reactions involved in the synthesis, utilization and/or degradation of amino acids other than the common 20 amino acids found in protein. Some of these amino acids like carnitine or homocysteine derive from primary amino acids.
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ABAT
4-aminobutyrate aminotransferase
ISO
SMPDB
SMP:00007
NCBI chr16:7,609,282...7,718,049
Ensembl chr16:8,888,178...8,958,420
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ALDH2
aldehyde dehydrogenase 2 family member
ISO
SMPDB
SMP:00007
NCBI chr12:109,343,020...109,385,060
Ensembl chr12:112,734,243...112,776,471
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ALDH6A1
aldehyde dehydrogenase 6 family member A1
ISO
SMPDB
SMP:00007
NCBI chr14:54,616,531...54,643,346
Ensembl chr14:73,472,255...73,495,734
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CNDP1
carnosine dipeptidase 1
ISO
SMPDB
SMP:00007
NCBI chr18:67,920,453...67,982,843
Ensembl chr18:71,162,331...71,188,879 Ensembl chr18:71,162,331...71,188,879
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DPYD
dihydropyrimidine dehydrogenase
ISO
SMPDB
SMP:00007
NCBI chr 1:99,736,145...100,576,663
Ensembl chr 1:98,457,934...99,300,100
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DPYS
dihydropyrimidinase
ISO
SMPDB
SMP:00007
NCBI chr 8:101,008,090...101,096,234
Ensembl chr 8:103,160,922...103,248,303
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GAD1
glutamate decarboxylase 1
ISO
SMPDB
SMP:00007
NCBI chr2B:58,100,623...58,145,045
Ensembl chr2B:175,558,538...175,602,944
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UPB1
beta-ureidopropionase 1
ISO
SMPDB
SMP:00007
NCBI chr22:5,300,686...5,332,735
Ensembl chr22:22,166,370...22,197,360
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ALDH9A1
aldehyde dehydrogenase 9 family member A1
ISO
SMPDB
SMP:00465
NCBI chr 1:141,094,261...141,130,613
Ensembl chr 1:144,883,839...144,919,670
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BBOX1
gamma-butyrobetaine hydroxylase 1
ISO
SMPDB
SMP:00465
NCBI chr11:26,995,120...27,083,832
Ensembl chr11:26,898,529...26,986,705
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SETD7
SET domain containing 7, histone lysine methyltransferase
ISO
SMPDB
SMP:00465
NCBI chr 4:131,869,999...131,921,342
Ensembl chr 4:143,167,190...143,227,732
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SHMT1
serine hydroxymethyltransferase 1
ISO
SMPDB
SMP:00465
NCBI chr17:32,870,949...32,905,690
Ensembl chr17:37,849,206...37,884,220
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TMLHE
trimethyllysine hydroxylase, epsilon
ISO
SMPDB
SMP:00465
NCBI chr X:144,956,906...145,081,204
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CKM
creatine kinase, M-type
ISO
RGD
PMID:12069495
RGD:1359082
NCBI chr19:42,255,158...42,271,467
Ensembl chr19:50,854,556...50,870,366
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GAMT
guanidinoacetate N-methyltransferase
ISO
RGD
PMID:12069495
RGD:1359082
Ensembl chr19:1,371,312...1,375,461
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GATM
glycine amidinotransferase
ISO
RGD
PMID:8021264
RGD:70746
NCBI chr15:24,309,045...24,326,673
Ensembl chr15:42,639,597...42,657,209
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SLC6A8
solute carrier family 6 member 8
ISO
RGD
PMID:12069495
RGD:1359082
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ANPEP
alanyl aminopeptidase, membrane
ISO
SMPDB
SMP:00015
NCBI chr15:68,479,349...68,509,238
Ensembl chr15:87,681,826...87,703,713
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CASP7
caspase 7
ISO
SMPDB
SMP:00015
NCBI chr10:110,273,318...110,324,800
Ensembl chr10:113,707,780...113,758,626
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GCLC
glutamate-cysteine ligase catalytic subunit
ISO
SMPDB RGD
PMID:16137247 PMID:16183645
RGD:1582661 RGD:1582663 SMP:00015
NCBI chr 6:53,052,145...53,102,794
Ensembl chr 6:54,687,315...54,734,994
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GCLM
glutamate-cysteine ligase modifier subunit
ISO
RGD SMPDB
PMID:16137247 PMID:16183645
RGD:1582661 RGD:1582663 SMP:00015
NCBI chr 1:96,548,850...96,573,273
Ensembl chr 1:95,278,665...95,297,893
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GGCT
gamma-glutamylcyclotransferase
ISO
SMPDB
SMP:00015
NCBI chr 7:31,125,964...31,134,330
Ensembl chr 7:31,247,760...31,255,903
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GGT6
gamma-glutamyltransferase 6
ISO
SMPDB
SMP:00015
NCBI chr17:4,611,707...4,615,336
Ensembl chr17:4,604,393...4,608,037
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GPX1
glutathione peroxidase 1
ISO
SMPDB
SMP:00015
NCBI chr 3:49,280,038...49,281,455
Ensembl chr 3:50,360,947...50,361,826
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GSR
glutathione-disulfide reductase
ISO
SMPDB
SMP:00015
NCBI chr 8:29,990,543...30,040,157
Ensembl chr 8:27,180,300...27,229,557
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GSS
glutathione synthetase
ISO
SMPDB
SMP:00015
NCBI chr20:31,256,734...31,284,356
Ensembl chr20:32,381,745...32,409,297
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GSTO2
glutathione S-transferase omega 2
ISO
SMPDB
SMP:00015
NCBI chr10:100,868,109...100,901,013
Ensembl chr10:104,326,175...104,357,604
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OPLAH
5-oxoprolinase, ATP-hydrolysing
ISO
SMPDB
SMP:00015
Ensembl chr 8:143,809,440...143,818,219
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AHCY
adenosylhomocysteinase
ISO
RGD
PMID:11741948 PMID:20814827
RGD:7242426 RGD:730275
NCBI chr20:30,603,701...30,626,835
Ensembl chr20:31,738,007...31,760,803
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AS3MT
arsenite methyltransferase
ISO
RGD
PMID:11790780
RGD:625365
NCBI chr10:99,470,026...99,502,829
Ensembl chr10:102,933,671...102,964,692
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CARM1
coactivator associated arginine methyltransferase 1
ISO
RGD
PMID:15866169
RGD:1359044
NCBI chr19:10,424,993...10,476,702
Ensembl chr19:11,144,733...11,195,948
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COMT
catechol-O-methyltransferase
ISO
RGD
PMID:12584150
RGD:1359089
NCBI chr22:2,704,015...2,731,326
Ensembl chr22:18,375,434...18,402,387
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DNMT1
DNA methyltransferase 1
ISO
RGD
PMID:12473678
RGD:1359078
NCBI chr19:9,681,847...9,745,334
Ensembl chr19:10,342,478...10,406,972
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GAMT
guanidinoacetate N-methyltransferase
ISO
RGD
PMID:15533043
RGD:1359081
Ensembl chr19:1,371,312...1,375,461
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GNMT
glycine N-methyltransferase
ISO
RGD
PMID:15347642
RGD:1359070
NCBI chr 6:42,550,631...42,554,385
Ensembl chr 6:43,846,560...43,849,679
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HNMT
histamine N-methyltransferase
ISO
RGD
PMID:11566133
RGD:1359041
NCBI chr2B:21,840,342...21,892,744
Ensembl chr2B:142,036,321...142,088,315
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MTHFR
methylenetetrahydrofolate reductase
ISO
RGD
PMID:20814827
RGD:7242426
NCBI chr 1:10,548,196...10,568,174
Ensembl chr 1:11,766,334...11,785,419
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NNMT
nicotinamide N-methyltransferase
ISO
RGD
PMID:15922112
RGD:1359084
NCBI chr11:109,174,490...109,186,758
Ensembl chr11:113,016,613...113,029,581
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PCMT1
protein-L-isoaspartate (D-aspartate) O-methyltransferase
ISO
RGD
PMID:8263531
RGD:729481
NCBI chr 6:147,564,783...147,623,402
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PEMT
phosphatidylethanolamine N-methyltransferase
ISO
RGD
PMID:8344945
RGD:729486
NCBI chr17:33,703,800...33,790,470
Ensembl chr17:38,651,024...38,737,202
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PNMT
phenylethanolamine N-methyltransferase
ISO
RGD
PMID:12438084
RGD:1359087
NCBI chr17:17,618,399...17,620,691
Ensembl chr17:17,835,277...17,837,180
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PRMT1
protein arginine methyltransferase 1
ISO
RGD
PMID:15866169
RGD:1359044
NCBI chr19:46,691,795...46,705,179
Ensembl chr19:55,610,938...55,623,135
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PRMT5
protein arginine methyltransferase 5
ISO
RGD
PMID:15866169
RGD:1359044
NCBI chr14:3,737,741...3,746,646
Ensembl chr14:21,836,984...21,846,018
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PRMT6
protein arginine methyltransferase 6
ISO
RGD
PMID:15866169
RGD:1359044
NCBI chr 1:109,582,715...109,586,744
Ensembl chr 1:108,699,098...108,700,225
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RNMT
RNA guanine-7 methyltransferase
ISO
RGD
PMID:11472630
RGD:1359071
NCBI chr18:560,744...598,216
Ensembl chr18:2,729,921...2,767,279
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SETDB1
SET domain bifurcated histone lysine methyltransferase 1
ISO
RGD
PMID:11959841
RGD:1359072
NCBI chr 1:126,275,719...126,314,043
Ensembl chr 1:129,925,009...129,962,442
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MTHFR
methylenetetrahydrofolate reductase
ISO
RGD
PMID:20814827
RGD:7242426
NCBI chr 1:10,548,196...10,568,174
Ensembl chr 1:11,766,334...11,785,419
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MTR
5-methyltetrahydrofolate-homocysteine methyltransferase
ISO
RGD
PMID:15845641 PMID:20814827
RGD:1359026 RGD:7242426
NCBI chr 1:212,353,195...212,463,304
Ensembl chr 1:217,358,050...217,460,946
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MTRR
5-methyltetrahydrofolate-homocysteine methyltransferase reductase
ISO
RGD
PMID:15979034 PMID:20814827
RGD:1359037 RGD:7242426
NCBI chr 5:8,195,868...8,228,071
Ensembl chr 5:8,017,403...8,049,322
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AHCY
adenosylhomocysteinase
ISO
SMPDB
SMP:00123
NCBI chr20:30,603,701...30,626,835
Ensembl chr20:31,738,007...31,760,803
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ALDH7A1
aldehyde dehydrogenase 7 family member A1
ISO
SMPDB
SMP:00123
NCBI chr 5:121,946,527...122,000,273
Ensembl chr 5:127,718,978...127,771,047
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BHMT
betaine--homocysteine S-methyltransferase
ISO
SMPDB RGD
PMID:15845641 PMID:20346934 PMID:20814827
RGD:1359026 RGD:7242426 RGD:7242428 SMP:00123
NCBI chr 5:36,181,183...36,201,833
Ensembl chr 5:36,670,854...36,728,993
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CHDH
choline dehydrogenase
ISO
SMPDB
SMP:00123
NCBI chr 3:53,751,179...53,784,437
Ensembl chr 3:54,976,780...54,982,991
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MAT2A
methionine adenosyltransferase 2A
ISO
SMPDB
SMP:00123
NCBI chr2A:85,589,301...85,595,437
Ensembl chr2A:87,141,857...87,148,322
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MAT2B
methionine adenosyltransferase 2 non-catalytic beta subunit
ISO
SMPDB
SMP:00123
NCBI chr 5:158,879,425...158,895,690
Ensembl chr 5:165,656,086...165,672,176
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MTR
5-methyltetrahydrofolate-homocysteine methyltransferase
ISO
SMPDB
SMP:00123
NCBI chr 1:212,353,195...212,463,304
Ensembl chr 1:217,358,050...217,460,946
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PEMT
phosphatidylethanolamine N-methyltransferase
ISO
SMPDB
SMP:00123
NCBI chr17:33,703,800...33,790,470
Ensembl chr17:38,651,024...38,737,202
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AHCY
adenosylhomocysteinase
ISO
SMPDB
SMP:00029
NCBI chr20:30,603,701...30,626,835
Ensembl chr20:31,738,007...31,760,803
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CBS
cystathionine beta-synthase
ISO
SMPDB
SMP:00029
NCBI chr21:29,361,519...29,385,610
Ensembl chr21:42,670,530...42,690,932
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CTH
cystathionine gamma-lyase
ISO
SMPDB
SMP:00029
NCBI chr 1:69,646,608...69,674,301
Ensembl chr 1:71,629,333...71,677,666
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GGT1
gamma-glutamyltransferase 1
ISO
SMPDB
SMP:00029
NCBI chr22:5,424,334...5,469,705
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MARS1
methionyl-tRNA synthetase 1
ISO
SMPDB
SMP:00029
NCBI chr12:31,410,231...31,438,015
Ensembl chr12:31,668,708...31,693,839
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MAT2A
methionine adenosyltransferase 2A
ISO
SMPDB
SMP:00029
NCBI chr2A:85,589,301...85,595,437
Ensembl chr2A:87,141,857...87,148,322
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MAT2B
methionine adenosyltransferase 2 non-catalytic beta subunit
ISO
SMPDB
SMP:00029
NCBI chr 5:158,879,425...158,895,690
Ensembl chr 5:165,656,086...165,672,176
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METTL6
methyltransferase 6, tRNA N3-cytidine
ISO
SMPDB
SMP:00029
NCBI chr 3:15,306,890...15,353,505
Ensembl chr 3:15,643,545...15,690,238
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PAPSS1
3'-phosphoadenosine 5'-phosphosulfate synthase 1
ISO
SMPDB
SMP:00029
NCBI chr 4:100,119,540...100,225,575
Ensembl chr 4:110,692,601...110,798,619
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SCLY
selenocysteine lyase
ISO
SMPDB
SMP:00029
NCBI chr2B:125,276,540...125,331,057
Ensembl chr2B:244,144,105...244,181,767
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SEPHS2
selenophosphate synthetase 2
ISO
SMPDB
SMP:00029
NCBI chr16:24,523,111...24,525,390
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ADO
2-aminoethanethiol dioxygenase
ISO
SMPDB
SMP:00021
NCBI chr10:59,312,788...59,316,554
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CDO1
cysteine dioxygenase type 1
ISO
SMPDB
SMP:00021
NCBI chr 5:111,159,041...111,170,965
Ensembl chr 5:116,955,295...116,967,506
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CSAD
cysteine sulfinic acid decarboxylase
ISO
SMPDB
SMP:00021
NCBI chr12:35,572,064...35,598,077
Ensembl chr12:36,354,437...36,379,738
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GAD1
glutamate decarboxylase 1
ISO
SMPDB
SMP:00021
NCBI chr2B:58,100,623...58,145,045
Ensembl chr2B:175,558,538...175,602,944
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GGT6
gamma-glutamyltransferase 6
ISO
SMPDB
SMP:00021
NCBI chr17:4,611,707...4,615,336
Ensembl chr17:4,604,393...4,608,037
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CBS
cystathionine beta-synthase
ISO
SMPDB RGD
PMID:9359866 PMID:20162368
RGD:1359024 RGD:7242427 SMP:00455
NCBI chr21:29,361,519...29,385,610
Ensembl chr21:42,670,530...42,690,932
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CDO1
cysteine dioxygenase type 1
ISO
RGD
PMID:20162368
RGD:7242427
NCBI chr 5:111,159,041...111,170,965
Ensembl chr 5:116,955,295...116,967,506
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CSAD
cysteine sulfinic acid decarboxylase
ISO
RGD
PMID:20162368
RGD:7242427
NCBI chr12:35,572,064...35,598,077
Ensembl chr12:36,354,437...36,379,738
G
CTH
cystathionine gamma-lyase
ISO
RGD SMPDB
PMID:9359866 PMID:20162368
RGD:1359024 RGD:7242427 SMP:00455
NCBI chr 1:69,646,608...69,674,301
Ensembl chr 1:71,629,333...71,677,666
Term paths to the root one shortest all shortest one longest all longest one shortest and longest all