RGD uses the Human Disease Ontology (DO, https://disease-ontology.org/) for disease curation across species. RGD automatically downloads each new release of the ontology on a monthly basis. Some additional terms which are required for RGD's curation purposes but are not currently covered in the official version of DO have been added. As corresponding terms are added to DO, these custom terms are retired and the DO terms substituted in existing annotations and subsequently used for curation.
A connective tissue cancer that derives_from lymphatic endothelium, and derives_from spindle cells, results_in_formation_of vascular channels that fill with blood cells, has_material_basis_in Human herpesvirus 8 (HHV8). (DO)
Synonyms:
exact_synonym:
Kaposi sarcoma; Kaposi sarcoma, susceptibility to; Kaposi's sarcoma of anus; Kaposi's sarcoma of conjunctiva; Kaposi's sarcoma of cornea; Kaposi's sarcoma of esophagus; Kaposi's sarcoma of gastrointestinal sites; Kaposi's sarcoma of lung; Kaposi's sarcoma of lymph nodes; Kaposi's sarcoma of palate; Kaposi's sarcoma of penis; Kaposi's sarcoma of skin; Kaposi's sarcoma of soft tissue; Kaposi's sarcoma of soft tissues; Kaposi's sarcoma of the CNS; Kaposi's sarcoma of the gallbladder; Kaposi's sarcoma of the prostate; Kaposi's sarcoma, lung; Kaposi's sarcoma, skin; Kaposis sarcoma; anal Kaposi's sarcoma; cardiac Kaposi's sarcoma; central nervous system Kaposi's sarcoma; conjunctival Kaposi's sarcoma; corneal Kaposi's sarcoma; cutaneous Kaposi's sarcoma; esophageal Kaposi's sarcoma; gallbladder Kaposi's sarcoma; gastric Kaposi's sarcoma; intestinal Kaposi's sarcoma; lymph node Kaposi's sarcoma; lymphadenopathic Kaposi's sarcoma; multiple idiopathic pigmented hemangiosarcoma; palate Kaposi's sarcoma; penis Kaposi's sarcoma; prostate Kaposi's sarcoma; pulmonary Kaposi's sarcoma; soft tissue Kaposi's sarcoma
narrow_synonym:
Kaposi's sarcoma of central nervous system; Kaposi's sarcoma of heart; MCD; MULTIPLE IDIOPATHIC PIGMENTED HEMANGIOSARCOMA, SUSCEPTIBILITY TO MULTICENTRIC CASTLEMAN DISEASE, SUSCEPTIBILITY TO