Protein Proc

URN urn:agi-llid:5624
Total Entities 0
Connectivity 1708
Name Proc
Description protein C (inactivator of coagulation factors Va and VIIIa)
Notes This gene encodes a vitamin K-dependent plasma glycoprotein. The encoded protein is cleaved to its activated form by the thrombin-thrombomodulin complex. This activated form contains a serine protease domain and functions in degradation of the activated forms of coagulation factors V and VIII. Mutations in this gene have been associated with thrombophilia due to protein C deficiency, neonatal purpura fulminans, and recurrent venous thrombosis.[provided by RefSeq, Dec 2009]

GO Molecular Function catalytic activity
hydrolase activity
peptidase activity
serine-type peptidase activity
serine-type endopeptidase activity
calcium ion binding

GO Cellular Component extracellular region
Golgi lumen
endoplasmic reticulum lumen
plasma membrane
extracellular space

GO Biological Process leukocyte migration
negative regulation of coagulation
negative regulation of blood coagulation
hemostasis
blood coagulation
negative regulation of apoptotic process
negative regulation of inflammatory response
cellular protein metabolic process
post-translational protein modification
peptidyl-glutamic acid carboxylation
proteolysis

Pathway Coagulation Cascade
Proteins Involved in Pathogenesis of Vasospasm
Proteins Involved in Pathogenesis of Amyotrophic Lateral Sclerosis
Proteins Involved in Pathogenesis of Myocardial Ischemia
Vitamin K metabolism
protein C anticoagulant pathway

Group leukocyte migration
negative regulation of coagulation
negative regulation of blood coagulation
hemostasis
blood coagulation
negative regulation of apoptotic process
negative regulation of inflammatory response
catalytic activity
hydrolase activity
peptidase activity
serine-type peptidase activity
serine-type endopeptidase activity
cellular protein metabolic process
post-translational protein modification
peptidyl-glutamic acid carboxylation
proteolysis
calcium ion binding
extracellular region
Golgi lumen
endoplasmic reticulum lumen
plasma membrane
extracellular space
Genes Associated with Systemic Lupus Erythematosus
Secreted proteins
Biofluids assayable substances

LocusLink ID 5624
19123
25268

GO ID 0005509
0004252
0007596
0044267
0050900
0043066
0030195
0017187
0043687
0006508
0005796
0005788
0005576
0005886
0003824
0016787
0008233
0008236
0007599
0005615
0050819
0050728

Alias PC
APC
PROC1
THPH3
THPH4
vitamin K-dependent protein C
autoprothrombin IIA
anticoagulant protein C
blood coagulation factor XIV
inactivator of coagulation factors Va, VIII
ceprotin
OTTHUMP00000203827
PROC
protein C
protein C (inactivator of coagulating factors Va and VIIIa)
protein C (inactivator of coagulation factors Va and VIIIa)
Vitamin-K dependent protein C
autoprothrombin iiia
glycoprotein c
human protein C
Activated protein C
inactivator of coagulating factors Va, 8
OTTHUMP00000203820
autoprothrombin 3a
Autoprothrombin IIAs
inactivator of coagulation factors Va and VIIIa
activated blood coagulating factor XIV
Activated blood coagulation factor XIV
Blood coagulating factor XIV
blood-coagulating factor XIVa
inactivator of coagulation factors Va, 5
GSAPC
inactivator of coagulating factors Va and VIIIa
inactivator of coagulating factors Va, VIII
Blood-coagulation factor XIVa
inactivator of coagulation factors Va, V

Mouse chromosome position 18

OMIM ID 612283
176860
612304

Rat chromosome position 18p12

Hugo ID 9451

Human chromosome position 2q13-q14

Swiss-Prot Accession P04070
B4DPQ7
P33587
P31394
Q15189
Q15190
Q16001
Q53S74
Q9UC55
O35498
Q91WN8
Q99PC6

PIR ID S18994
A22331
JX0210

GenBank ID NC_000002
NM_000312
NP_000303
XM_005263717
XP_005263774
XM_005263716
XP_005263773
XM_005263715
XP_005263772
NG_016323
NC_018913
AC_000134
AB083690
BAC21165
AB083693
BAC21166
AB083695
BAC21167
AB083696
BAC21168
AB083697
BAC21169
AB083698
BAC21170
AB083699
BAC21171
AB083700
BAC21172
AB086849
BAC53629
AB086850
BAC53630
AB086851
BAC53631
AB086852
BAC54280
ABBA01040207
AC068282
AAY15044
AF378903
AAK56377
AMYH02004732
AY348553
AAQ24849
AY348554
AAQ24850
AY454079
AAR23427
CH471103
EAW95320
CQ757487
CAF32600
CQ821348
CAG34344
CS355172
CAL24228
GM997828
CAX30697
GM997830
CAX30698
M11228
AAA60166
M12712
AAA60165
S55227
AAB25410
S58668
AAB26335
AK298280
BAG60540
AK298449
BAG60665
AK298454
BAG60669
AK303773
BAG64736
BC034377
AAH34377
BM975043
CB113383
DA642156
K02059
AAA60164
S50739
AAB24150
X02750
CAA26528
P04070
DQ890791
ABM81717
DQ893947
ABM84873
NC_000084
NM_001042767
NP_001036232
XM_006525722
XP_006525785
NM_008934
NP_032960
NR_045173
NM_001042768
NP_001036233
XM_006525721
XP_006525784
AC_000040
AAHY01137527
AAHY01137528
AC126686
AC127347
AF034569
AAC33795
CH466557
EDK97054
EDK97055
D43755
BAA07812
GM997836
CAX30700
AF318182
AAK07918
AI118438
AI286922
BC013896
AAH13896
BY082597
BY086829
BY788141
CA456834
CA468822
CB599669
CF550816
D10445
BAA01235
DV662175
P33587
NC_005117
XM_006254527
XP_006254589
XM_006254526
XP_006254588
NM_012803
NP_036935
AC_000086
AABR06094502
AAHX01094383
CH473974
EDL76183
EDL76184
GM997838
CAX30701
BC078879
AAH78879
X64336
CAA45617
P31394

Unigene ID Hs.224698
Mm.2786
Mm.489734
Rn.91064

KEGG ID hsa:5624
mmu:19123
rno:25268

Swiss-Prot ID PROC_RAT
PROC_HUMAN
PROC_MOUSE

EC Number 3.4.21.69

Ensembl ID ENSG00000115718
ENSP00000234071
ENST00000234071
ENSP00000404030
ENST00000453608
ENSMUSG00000024386
ENSMUSP00000132226
ENSMUST00000171765
ENSRNOG00000014376
ENSRNOP00000019596
ENSRNOT00000019596

Homologene ID 37288

Organism Homo sapiens
Mus musculus
Rattus norvegicus

MGI ID 97771

RGD ID 3411

MedScan ID 5624