Protein Shmt2

URN urn:agi-llid:6472
Connectivity 0
Name Shmt2
Description serine hydroxymethyltransferase 2 (mitochondrial)
Notes This gene encodes the mitochondrial form of a pyridoxal phosphate-dependent enzyme that catalyzes the reversible reaction of serine and tetrahydrofolate to glycine and 5,10-methylene tetrahydrofolate. The encoded product is primarily responsible for glycine synthesis. The activity of the encoded protein has been suggested to be the primary source of intracellular glycine. The gene which encodes the cytosolic form of this enzyme is located on chromosome 17. Alternative splicing results in multiple transcript variants. [provided by RefSeq]

Pathway folate cycle metabolic pathway
folated mediated one carbon metabolic pathway

GO Molecular Function transferase activity
amino acid binding
pyridoxal phosphate binding
methyltransferase activity
glycine hydroxymethyltransferase activity
L-allo-threonine aldolase activity

GO Cellular Component mitochondrion
mitochondrial inner membrane
mitochondrial nucleoid
mitochondrial intermembrane space
mitochondrial matrix

GO Biological Process positive regulation of cell proliferation
one-carbon metabolic process
glycine biosynthetic process
L-serine biosynthetic process
glycine biosynthetic process from serine
glycine metabolic process
L-serine metabolic process
protein homotetramerization

Ariadne Ontology Ser-Gly metabolism

Group Ser-Gly metabolism
positive regulation of cell proliferation
one-carbon metabolic process
glycine biosynthetic process
L-serine biosynthetic process
glycine biosynthetic process from serine
glycine metabolic process
L-serine metabolic process
protein homotetramerization
transferase activity
amino acid binding
pyridoxal phosphate binding
methyltransferase activity
glycine hydroxymethyltransferase activity
L-allo-threonine aldolase activity
mitochondrion
mitochondrial inner membrane
mitochondrial nucleoid
mitochondrial intermembrane space
mitochondrial matrix

MedScan ID 6472

Hugo ID 10852

Human chromosome position 12q12-q14

LocusLink ID 6472
108037
299857

Alias GLYA
SHMT
serine hydroxymethyltransferase, mitochondrial
GLY A+
serine aldolase
serine methylase
threonine aldolase
serine hydroxymethylase
glycine hydroxymethyltransferase
glycine auxotroph A, human complement for hamster
AA408223
AA986903
2700043D08Rik
MGC105820
2700043D08
Glycine hydroxymethyltransferase 2
Glycine hydroxymethyltransferase II
mitochondrial serine hydroxymethyl transferase 2
mitochondrial serine hydroxymethyl transferase II
mitochondrial Serine hydroxymethyltransferase
serine hydroxymethyl transferase 2
serine hydroxymethyl transferase 2 (mitochondrial)
serine hydroxymethyl transferase II
serine hydroxymethyltransferase 2 (mitochondrial)
Serine methylase 2
Serine methylase II
SHMT2

Organism Homo sapiens
Mus musculus
Rattus norvegicus

GenBank ID NC_000012
NM_005412
NP_005403
NT_029419
NW_001838060
NW_925395
AC_000055
AC_000144
NM_001166356
NM_001166357
NM_001166358
NM_001166359
NR_029415
NR_029416
NR_029417
AC137834
CH471054
EAW96993
EAW96994
EAW96995
EAW96996
EAW96997
EAW96998
EAW96999
EAW97000
EAW97001
U23143
AAA64572
Y12331
CAA72999
AK055053
AK223555
BAD97275
AK295941
BAG58725
AK296183
BAG58915
AK297173
BAG59666
AK298231
BAG60500
AK301339
BAG62887
AK301443
BAG62969
AK303827
BAG64774
AK315916
BAH14287
BC008066
BC008711
BC011911
AAH11911
BC013677
AAH13677
BC025355
BC032584
AAH32584
BC044211
AAH44211
BC091501
AAH91501
BT006866
AAP35512
BX647711
CAI46021
BX648847
CN395976
CR613033
DA052422
DC339924
DC386590
L11932
AAA63258
P34897
Q53ET4
Q5BJF5
Q5HYG8
Q8N1A5
DQ891309
ABM82235
DQ894430
ABM85356
NC_000076
NM_028230
NP_082506
NT_039500
NW_001030422
AC_000032
AC167719
CH466578
EDL24510
EDL24511
AK012355
BAB28184
AK037339
BAC29790
AK051207
BAC34556
AK162421
BAE36907
AK169192
BAE40968
AK192991
AK194812
AK195953
AK200167
AK204404
AK207979
AK210079
AK211597
AK214589
AK215786
BC004825
AAH04825
BC051396
AAH51396
Q3TFD0
Q99K87
Q9CZN7
NC_005106
NM_001008322
NP_001008323
NW_001084859
NW_047777
AC_000075
CH473950
EDM16462
BC085331
AAH85331
Q5U3Z7

OMIM ID 138450

Mouse chromosome position 10

GO ID 0004372
0030170
0016740
0006563
0006544
0006730
0005759
0042645
0005739
0008732
0016597
0008168
0006564
0006545
0019264
0008284
0051289
0005743
0005758

Rat chromosome position 7q22

Swiss-Prot Accession Q5BJF5
Q8N1A5
B7Z9F1
P34897
Q5HYG8
B4DJQ3
Q53ET4
Q9CZN7
Q3TFD0
Q99K87
Q5U3Z7
O00740

PIR ID B46746

Unigene ID Hs.75069
Mm.29890
Rn.9214

KEGG ID hsa:6472
mmu:108037
rno:299857

EC Number 2.1.2.1

Swiss-Prot ID GLYM_HUMAN
Q8N1A5_HUMAN
Q5U3Z7_RAT
B4DJQ3_HUMAN
Q9CZN7_MOUSE
B7Z9F1_HUMAN
Q5HYG8_HUMAN
Q5BJF5_HUMAN

Cell Localization Mitochondrion
Cytoplasm

IPI ID IPI00002520
IPI00795816
IPI00195109
IPI00454008
IPI00789370
IPI00748411
IPI00794572
IPI00386540
IPI00794549
IPI00794060
IPI00794657
IPI00795324
IPI00797816
IPI00797074
IPI00797146

Homologene ID 38048

RGD ID 1308582

MGI ID 1277989