Protein Lrat

URN urn:agi-llid:9227
Connectivity 26
Name Lrat
Description lecithin retinol acyltransferase (phosphatidylcholine--retinol O-acyltransferase)
Notes The protein encoded by this gene is a microsomal enzyme that catalyzes the esterification of all-trans-retinol into all-trans-retinyl ester, an essential reaction for the retinoid cycle in visual system and vitamin A status in liver. Mutations in this gene have been associated with early-onset severe retinal dystrophy. [provided by RefSeq]

Pathway retinoic acid metabolic pathway
retinoid cycle metabolic pathway

GO Molecular Function transferase activity
retinol binding
retinoic acid binding
acyltransferase activity
O-acyltransferase activity
phosphatidylcholine-retinol O-acyltransferase activity

GO Cellular Component membrane
endoplasmic reticulum membrane
endoplasmic reticulum
microsome
integral to membrane

GO Biological Process response to stimulus
embryonic development
visual perception
retinol metabolic process
lecithin metabolic process
vitamin A metabolic process

Group response to stimulus
embryonic development
visual perception
retinol metabolic process
lecithin metabolic process
vitamin A metabolic process
transferase activity
retinol binding
retinoic acid binding
acyltransferase activity
O-acyltransferase activity
phosphatidylcholine-retinol O-acyltransferase activity
membrane
endoplasmic reticulum membrane
endoplasmic reticulum
microsome
integral to membrane

MedScan ID 9227

Hugo ID 6685

Human chromosome position 4q32.1

LocusLink ID 9227
79235
64047

Alias LCA14
MGC33103
lecithin retinol acyltransferase
AI449251
1300010A18Rik
phosphatidylcholine-retinol-O-acyltransferase
phosphatidylcholine--retinol O-acyltransferase
lecithin retinol acyltransferase (phosphatidylcholine--retinol O-acyltransferase)
1300010A18
lecithin-retinol acyltransferase (phosphatidylcholine-retinol-O-acyltransferase)
LOC299882
LOC497758
Lrat
phosphatidylcholine-retinol O-acyltransferase

Organism Homo sapiens
Mus musculus
Rattus norvegicus

GenBank ID NC_000004
NM_004744
NP_004735
NT_016354
NW_001838921
NW_922217
NG_009110
AC_000136
AC_000047
AC009567
CH471056
EAX04904
AF071510
AAD13529
AK125823
AK292598
BAF85287
AY546085
AAS49412
AY546086
AAS49413
BC031053
AAH31053
O95237
GQ129396
ACT64530
GQ129397
ACT64531
NC_000069
NM_023624
NP_076113
NT_039240
NW_001030721
AC_000025
AC158935
CH466547
EDL15427
AF255061
AAF97787
AK004953
BAB23696
AK085922
BC037373
BC141375
AAI41376
BC141378
AAI41379
Q9JI60
NC_005101
NM_022280
NP_071616
NW_001084805
NW_047626
AC_000070
CH473976
EDM00844
EDM00845
AF255060
AAF97786
Q9JI61

OMIM ID 604863
613341

Mouse chromosome position 3

GO ID 0008415
0047173
0016740
0050896
0007601
0005783
0005789
0016021
0016020
0008374
0001972
0019841
0009790
0006653
0042572
0006776
0005792

Rat chromosome position 2q34

Swiss-Prot Accession O95237
B2RUR5
Q9JI60
Q9JI61
A8K983
Q8N716

Unigene ID Hs.658427
Mm.33921
Rn.137431

KEGG ID hsa:9227
mmu:79235
rno:64047

EC Number 2.3.1.135

Swiss-Prot ID LRAT_MOUSE
LRAT_HUMAN
LRAT_RAT
B2RUR5_MOUSE
A8K983_HUMAN

Cell Localization Endoplasmic reticulum membrane

IPI ID IPI00119943
IPI00006231
IPI00199982
IPI00735216

Homologene ID 3483

RGD ID 68362

MGI ID 1891259