Protein Atic

URN urn:agi-llid:471
Connectivity 17
Name Atic
Description 5-aminoimidazole-4-carboxamide ribonucleotide formyltransferase/IMP cyclohydrolase
Notes This gene encodes a bifunctional protein that catalyzes the last two steps of the de novo purine biosynthetic pathway. The N-terminal domain has phosphoribosylaminoimidazolecarboxamide formyltransferase activity, and the C-terminal domain has IMP cyclohydrolase activity. A mutation in this gene results in AICA-ribosiduria. [provided by RefSeq]

Pathway de novo purine biosynthetic pathway
'Copy of 'de novo purine biosynthetic pathway'
de novo purine biosynthetic pathwaylatest
Copy of 'de novo purine biosynthetic pathwaylatest'
Copy of 'de novo purine biosynthetic pathwaylatest'
de novo purine biosynthetic pathway

GO Molecular Function catalytic activity
hydrolase activity
transferase activity
protein homodimerization activity
phosphoribosylaminoimidazolecarboxamide formyltransferase activity
IMP cyclohydrolase activity

GO Cellular Component mitochondrion

GO Biological Process organ regeneration
nucleobase, nucleoside, nucleotide and nucleic acid metabolic process
purine nucleotide biosynthetic process
purine ribonucleoside monophosphate biosynthetic process
IMP biosynthetic process
'de novo' IMP biosynthetic process

Ariadne Ontology Purine metabolism

Group Purine metabolism
catalytic activity
organ regeneration
nucleobase, nucleoside, nucleotide and nucleic acid metabolic process
purine nucleotide biosynthetic process
purine ribonucleoside monophosphate biosynthetic process
IMP biosynthetic process
'de novo' IMP biosynthetic process
hydrolase activity
transferase activity
protein homodimerization activity
phosphoribosylaminoimidazolecarboxamide formyltransferase activity
IMP cyclohydrolase activity
mitochondrion

MedScan ID 471

Hugo ID 794

Human chromosome position 2q35

LocusLink ID 471
108147
81643

Alias PURH
AICAR
AICARFT
FLJ93545
IMPCHASE
OK/SW-cl.86
bifunctional purine biosynthesis protein PURH
AICARFT/IMPCHASE
OTTHUMP00000206773
AICAR formyltransferase/IMP cyclohydrolase bifunctional enzyme
phosphoribosylaminoimidazolecarboxamide formyltransferase/IMP cyclohydrolase
5-aminoimidazole-4-carboxamide-1-beta-D-ribonucleotide transformylase/inosinicase
AA536954
AW212393
2610509C24Rik
2610509C24
5-amino-1-ribosyl-4-imidazolecarboxamide 5'-phosphate transformylase
5-amino-4-imidazolecarboxamide ribonucleotide transformylase
5-amino-4-imidazolecarboxamide ribotide transformylase
5-aminoimidazole-4-carboxamide ribonucleotide formyltransferase/IMP
5-aminoimidazole-4-carboxamide ribonucleotide formyltransferase/IMP cyclohydrolase
5'-phosphoribosyl-5-amino-4-imidazolecarboxamide formyltransferase
AICAR formyltransferase
AICAR transformylase
AICARFTs
ATIC
phosphoribosylaminoimidazolecarboxamide formyltransferase

Organism Homo sapiens
Mus musculus
Rattus norvegicus

GenBank ID NC_000002
NM_004044
NP_004035
NT_005403
NW_001838863
NW_921618
AC_000134
AC_000045
AC073284
AAY24062
CH471063
EAW70523
EAW70524
EAW70525
EAW70526
EAW70527
EAW70528
EAW70529
AA494525
AB062403
BAB93490
AK290067
BAF82756
AK298142
BAG60418
AK313066
BAG35895
BC008879
AAH08879
CR594366
CR600478
CR601137
CR604622
CR606023
CR609807
CR612551
CR617706
D82348
BAA11559
D89976
BAA21762
DA043224
DA074758
U37436
AAA97405
P31939
DQ893262
ABM84188
DQ896591
ABM87590
NC_000067
NM_026195
NP_080471
NT_039170
AC115905
CH466548
EDL00264
AK010449
BAB26949
AK010611
BAB27060
AK012074
BAB28011
AK028930
AK046353
BAC32688
AK076091
BAC36175
AK088701
AK139235
BAE23927
AK157739
AK186275
AK202783
BC039925
AAH39925
CJ178786
EF437353
ABS83519
Q9CWJ9
NC_005108
NM_031014
NP_112276
NW_047816
NW_001084883
AC_000077
CH474044
EDL75264
BC072496
AAH72496
D89514
BAA22837
O35567

OMIM ID 601731
608688

Mouse chromosome position 1

GO ID 0003937
0016787
0004643
0042803
0016740
0006188
0006139
0031100
0006164
0009168
0005739
0003824
0006189

Rat chromosome position 9q33

Swiss-Prot Accession P31939
Q9CWJ9
O35567
Q13856
Q53S28
Q6IN16

PIR ID JC4642

Unigene ID Hs.90280
Mm.38010
Rn.15114

KEGG ID hsa:471
mmu:108147
rno:81643

EC Number 3.5.4.10
2.1.2.3

Swiss-Prot ID PUR9_HUMAN
PUR9_RAT
PUR9_MOUSE

Cell Localization Cytoplasm

IPI ID IPI00289499
IPI00393333
IPI00330303
IPI00845646

Homologene ID 2983

RGD ID 70879

MGI ID 1351352