Protein Umps

URN urn:agi-llid:7372
Connectivity 20
Name Umps
Description uridine monophosphate synthetase
Notes This gene encodes a uridine 5'-monophosphate synthase. The encoded protein is a bifunctional enzyme that catalyzes the final two steps of the de novo pyrimidine biosynthetic pathway. The first reaction is carried out by the N-terminal enzyme orotate phosphoribosyltransferase which converts orotic acid to orotidine-5'-monophosphate. The terminal reaction is carried out by the C-terminal enzyme OMP decarboxylase which converts orotidine-5'-monophosphate to uridine monophosphate. Defects in this gene are the cause of hereditary orotic aciduria. Alternate splicing results in multiple transcript variants. [provided by RefSeq]

Pathway de novo pyrimidine biosynthetic pathway
Copy of 'de novo pyrimidine biosynthetic pathway'
Copy of 'de novo pyrimidine biosynthetic pathway'
Copy of 'de novo pyrimidine biosynthetic pathway'hl
Copy of 'de novo pyrimidine biosynthetic pathway'hl
de novo pyrimidine biosynthetic pathwayl
de novo pyrimidine biosynthetic pathwayl2
de novo pyrimidine biosynthetic pathways
de novo pyrimidine biosynthetic pathway

GO Molecular Function catalytic activity
lyase activity
transferase activity
transferase activity, transferring glycosyl groups
orotate phosphoribosyltransferase activity
carboxy-lyase activity
orotidine-5'-phosphate decarboxylase activity

GO Cellular Component cytoplasm
nucleus

GO Biological Process metabolic process
pyrimidine nucleotide biosynthetic process
'de novo' pyrimidine base biosynthetic process
UMP biosynthetic process
nucleoside metabolic process

Ariadne Ontology Pyrimidine metabolism

Group Pyrimidine metabolism
catalytic activity
metabolic process
pyrimidine nucleotide biosynthetic process
'de novo' pyrimidine base biosynthetic process
UMP biosynthetic process
nucleoside metabolic process
lyase activity
transferase activity
transferase activity, transferring glycosyl groups
orotate phosphoribosyltransferase activity
carboxy-lyase activity
orotidine-5'-phosphate decarboxylase activity
cytoplasm
nucleus

MedScan ID 7372

Hugo ID 12563

Human chromosome position 3q13

LocusLink ID 7372
22247
288051

Alias OPRT
OK/SW-cl.21
uridine 5'-monophosphate synthase
OPRTase
OMPdecase
UMP synthase
OTTHUMP00000215266
orotate phosphoribosyltransferase
orotidine 5'-phosphate decarboxylase
AA408257
AL033308
BB164745
1700095D23Rik
uridine monophosphate synthase
1700095D23
LOC131725
orotate phosphoribosyl pyrophosphate transferase
orotate phosphoribosyl transferase
orotate phosphoribosyl transferase and orotidine-5'-decarboxylase
orotate phosphoribosyltransferase phosphoribosyltransferase
orotic acid phosphoribosyltransferase
orotidine 5'-monophosphate pyrophosphorylase
orotidine monophosphate pyrophosphorylase
orotidine phosphoribosyltransferase
orotidine-5'-decarboxylase
orotidine-5'-phosphate pyrophosphorylase
orotidylate phosphoribosyltransferase
orotidylate pyrophosphorylase
orotidylic acid phosphorylase
orotidylic acid pyrophosphorylase
orotidylic phosphorylase
UMP synthetase
Umps
Uridine 5'-monophosphate synthetase
uridine monophosphate synthase (orotate phosphoribosyl transferase and or
uridine monophosphate synthetase
uridine monophosphate synthetase (orotate phosphoribosyl transferase and or

Organism Homo sapiens
Mus musculus
Rattus norvegicus

GenBank ID NC_000003
NM_000373
NP_000364
NT_005612
NW_001838882
NW_921807
AC_000135
AC_000046
NR_033434
NR_033437
AB041359
BAB20663
AC022336
AY691629
AAT85801
CH471052
EAW79407
EAW79408
AB062285
BAB93468
AK291306
BAF83995
AL080099
CAB45710
BC000364
AAH00364
BC007511
AAH07511
CR456787
CAG33068
CR590318
CR592156
CR593249
CR597849
CR599292
CR601942
CR604719
CR608134
CR614357
CR618739
CR623728
CR624319
CR625054
D86227
BAA19920
D86228
BAA19921
D86230
BAA19923
EU921886
ACH48224
EU921887
ACH48225
EU921888
ACH48226
EU921889
ACH48227
EU921890
ACH48228
EU921891
ACH48229
EU921892
ACH48230
EU921893
ACH48231
EU921894
ACH48232
EU921895
ACH48233
J03626
AAA61255
M36661
AAA61256
P11172
EU832341
ACE87598
EU832426
ACE86911
NC_000082
NM_009471
NP_033497
NT_039624
NW_001030584
AC_000038
AC165079
CH466521
EDK97857
EDK97858
AK007077
AK035821
BAC29199
AK035997
AK090102
AK135187
AK159808
BAE35388
AK159955
BAE35511
AK164487
BC003887
AAH03887
BC095981
AAH95981
M29395
AAA39859
P13439
Q3TVV7
Q544K9
NC_005110
NM_001025402
NP_001020573
NW_001084662
NW_047356
AC_000079
CH473967
EDM11351
EDM11352
BC098033
AAH98033
Q4QQS7

OMIM ID 258900

Mouse chromosome position 16

GO ID 0016829
0004588
0004590
0016757
0006207
0006222
0008152
0009116
0006221
0005737
0005634
0016831
0003824
0016740

Rat chromosome position 11q22

Swiss-Prot Accession A8K5J1
P11172
P13439
Q544K9
Q3TVV7
Q4QQS7
O00758
O00759
O00760
Q16862
Q9H3Q2
Q9UG49
Q99L26

PIR ID A30148
A25323

Unigene ID Hs.2057
Mm.13145
Mm.466951
Rn.102010

KEGG ID hsa:7372
mmu:22247
rno:288051

EC Number 4.1.1.23
2.4.2.10

Swiss-Prot ID PYR5_HUMAN
PYR5_MOUSE
Q4QQS7_RAT
A8K5J1_HUMAN
Q544K9_MOUSE

Cell Localization Cytoplasm

IPI ID IPI00003923
IPI00398067
IPI00121552
IPI00370714
IPI00880704

Homologene ID 319

RGD ID 1311908

MGI ID 1298388