Protein Drosha

URN urn:agi-llid:29102
Total Entities 0
Connectivity 451
Name Drosha
Description ribonuclease type III, nuclear
Notes Members of the ribonuclease III superfamily of double-stranded (ds) RNA-specific endoribonucleases participate in diverse RNA maturation and decay pathways in eukaryotic and prokaryotic cells (Fortin et al., 2002 [PubMed 12191433]). The RNase III Drosha is the core nuclease that executes the initiation step of microRNA (miRNA) processing in the nucleus (Lee et al., 2003 [PubMed 14508493]).[supplied by OMIM]

GO Molecular Function hydrolase activity
nuclease activity
endonuclease activity
endoribonuclease activity
ribonuclease III activity
RNA binding
metal ion binding

GO Cellular Component nucleoplasm
nucleolus
nucleus

GO Biological Process pre-miRNA processing
regulation of gene expression
rRNA catabolic process
RNA processing
RNA phosphodiester bond hydrolysis, endonucleolytic
miRNA metabolic process
gene expression
ribosome biogenesis

Pathway RNA Gene Silencing
Dysregulation of RNA and DNA Metabolism in Amyotrophic Lateral Sclerosis
microRNA pathway
microRNA pathway

Group RNA gene silencing
pre-miRNA processing
regulation of gene expression
hydrolase activity
nuclease activity
endonuclease activity
endoribonuclease activity
ribonuclease III activity
rRNA catabolic process
RNA processing
RNA phosphodiester bond hydrolysis, endonucleolytic
miRNA metabolic process
gene expression
ribosome biogenesis
RNA binding
metal ion binding
nucleoplasm
nucleolus
nucleus
Genes with Mutations Associated with Ovarian Cancer

LocusLink ID 29102
14000
310159

Cell Localization Cytoplasm
Nucleus
Nucleolus

GO ID 0003723
0046872
0004525
0010467
0010586
0031054
0016075
0042254
0005730
0005654
0004519
0004521
0016787
0004518
0090502
0006396
0010468
0005634
0003725
0005515
0031047
0005622
0003674
0008150
0005575

Alias RN3
ETOHI2
RNASEN
RANSE3L
RNASE3L
HSA242976
ribonuclease 3
p241
RNase III
protein Drosha
nuclear RNase III Drosha
putative ribonuclease III
ribonuclease III, nuclear
ribonuclease type III, nuclear
drosha, double-stranded RNA-specific endoribonuclease
putative protein p241 which interacts with transcription factor Sp1
AI874853
1110013A17Rik
ethanol induced 2
MGC115770
RIKEN cDNA 1110013A17 gene
ribonuclease III
OTTMUSP00000027894
1110013A17
DROSHA
drosha, ribonuclease type III
ethanol induced II
RGD1307626
Etohi2s

Mouse chromosome position 15
15 A1

OMIM ID 608828

Rat chromosome position 2q16

Hugo ID 17904

Human chromosome position 5p13.3

Swiss-Prot Accession Q9NRR4
Q5HZJ0
E7EMP9
Q7Z5V2
Q86YH0
Q9NW73
Q9Y2V9
Q9Y4Y0
Q59FF9
Q6PAJ6
Q6PF88
Q7TMI8
Q80UU5
Q80Z69
Q8CJ74
Q9CTG2
Q67B98

GenBank ID NC_000005
NM_013235
NP_037367
NM_001100412
NP_001093882
XM_005248294
XP_005248351
XM_005248293
XP_005248350
XM_005248292
XP_005248349
XM_005248291
XP_005248348
NC_018916
AC_000137
ABBA01066716
ABBA01066717
AC008768
AC022417
AC106802
AMYH02011111
AMYH02011112
AMYH02011113
CH471118
EAX10767
EAX10768
EAX10769
EAX10770
HC879388
CBM42910
HD033097
CBV35643
AA917625
AB209501
BAD92738
AF116910
AAD29637
AF189011
AAF80558
AJ242976
CAB45133
AK001121
BAA91511
AK026563
AK308093
BC024261
BC041162
AAH41162
BC054003
AAH54003
BX647724
DB065470
Q9NRR4
NC_000081
XR_383823
XM_006520021
XP_006520084
NM_001130149
NP_001123621
NM_026799
NP_081075
AC_000037
NW_001032926
AAHY01119554
AAHY01119555
AAHY01119556
AAHY01119557
AAHY01119558
AAHY01119559
AAHY01119560
AAHY01119561
AAHY01119562
AAHY01119563
AAHY01197685
AC133189
AF440766
AAN63637
AF533013
AAO65849
AK003651
BAB22917
AK077549
AK144147
BAE25729
AK148640
BAE28629
AK217593
BB726746
BC040801
BC050057
AAH50057
BC055696
AAH55696
BC057687
AAH57687
BC060265
AAH60265
BC088999
AAH88999
BU701939
BY673703
CA328055
U94841
Q5HZJ0
NT_006576
NW_922562
NW_001838929
AC_000048
CR607257
CR613595
Q59FF9
NT_039618
Q6PAJ6
Q6PF88
Q7TMI8
Q80UU5
Q80Z69
Q8CJ74
Q9CTG2
NC_005101
XM_226843
XP_226843
NW_001084797
XM_001058381
XP_001058381
NW_047622
AC_000070
NM_001107655
CH474058
EDL82945
AY373464
AAR85911
Q67B98

Unigene ID Hs.97997
Mm.293142
Rn.41113

KEGG ID hsa:29102
mmu:14000
rno:310159

Swiss-Prot ID RNC_MOUSE
RNC_HUMAN
Q5HZJ0_MOUSE

EC Number 3.1.26.3

Ensembl ID ENSG00000113360
ENSP00000424161
ENST00000513349
ENSP00000425979
ENST00000511367
ENSMUSG00000022191
ENSMUSP00000129279
ENSMUST00000169061
ENSMUSP00000087762
ENSMUST00000090292

Homologene ID 8293

Organism Homo sapiens
Mus musculus
Rattus norvegicus

MGI ID 1261425

RGD ID 1307626

MedScan ID 29102

IPI ID IPI00300956
IPI00219990
IPI00515032
IPI00626208
IPI00336345
IPI00559397
IPI00870720