Protein PCK2

URN urn:agi-llid:5106
Total Entities 0
Connectivity 68
Name PCK2
Description phosphoenolpyruvate carboxykinase 2 (mitochondrial)
Notes This gene encodes a member of the phosphoenolpyruvate carboxykinase (GTP) family. The protein is a mitochondrial enzyme that catalyzes the conversion of oxaloacetate to phosphoenolpyruvate in the presence of GTP. A cytosolic form encoded by a different gene has also been characterized and is the key enzyme of gluconeogenesis in the liver. The encoded protein may serve a similar function, although it is constitutively expressed and not modulated by hormones such as glucagon and insulin that regulate the cytosolic form. Alternatively spliced transcript variants have been described.

GO Molecular Function lyase activity
carboxy-lyase activity
phosphoenolpyruvate carboxykinase activity
phosphoenolpyruvate carboxykinase (GTP) activity
nucleotide binding
purine nucleotide binding
GTP binding
metal ion binding

GO Cellular Component mitochondrial matrix
mitochondrion

GO Biological Process small molecule metabolic process
gluconeogenesis
glucose metabolic process
NADH oxidation
pyruvate metabolic process
oxaloacetate metabolic process
positive regulation of insulin secretion
cellular response to glucose stimulus
response to glucocorticoid
carbohydrate metabolic process

Pathway Insulin Resistance in Hepatocytes
Role of Adiponectin in Insulin Resistance Prevention
Proteins Involved in Pathogenesis of Diabetes Mellitus Type 2
TGFB1-TGFBR2 Expression Targets
GH1-GHR/NF-kB/ELK-SRF/MYC Expression Targets
GH1-GHR/STAT Expression Targets
PRL-GHR/NF-kB/ELK-SRF/MYC Expression Targets
PRL-GHR/STAT Expression Targets
PRL-PRLR Expression Targets
Leptin/ELK-SRF Expression Targets
Leptin/STAT Expression Targets
CCL2 Expression Targets
Epinephrine/Gq Expression Targets
Epinephrine/Gs Expression Targets
GCG Expression Targets
POMC Expression Targets
IGF1/CEBPA/FOXO1A Expression Targets
Insulin/ELK-SRF/HIF1A/MYC/SREBF Expression Targets
Insulin/STAT Expression Targets
TNF/NF-kB Expression Targets
AGT/CREB Expression Targets
Insulin/CEBPA/CTNNB/FOXA/FOXO Expression Targets
gluconeogenesis pathway

Group Tricarboxylic acid cycle
small molecule metabolic process
gluconeogenesis
glucose metabolic process
NADH oxidation
pyruvate metabolic process
oxaloacetate metabolic process
positive regulation of insulin secretion
cellular response to glucose stimulus
response to glucocorticoid
lyase activity
carboxy-lyase activity
phosphoenolpyruvate carboxykinase activity
phosphoenolpyruvate carboxykinase (GTP) activity
carbohydrate metabolic process
nucleotide binding
purine nucleotide binding
GTP binding
metal ion binding
mitochondrial matrix
mitochondrion
Secreted proteins

LocusLink ID 5106
74551
361042

Cell Localization Mitochondria
Mitochondrion

GO ID 0005525
0046872
0004613
0004611
0005975
0006094
0006006
0044281
0005759
0005739
0016831
0016829
0000166
0017076
0006116
0006107
0032024
0006090
0071333
0051384
0030145
0016301
0003674
0005575

Alias PEPCK
PEPCK2
PEPCK-M
phosphoenolpyruvate carboxykinase [GTP], mitochondrial
PEP carboxykinase
phosphopyruvate carboxylase
phosphoenolpyruvate carboxylase
1810010O14Rik
9130022B02Rik
phosphoenolpyruvate carboxykinase 2 (mitochondrial)
PEPCK-Ms
phosphoenolpyruvate carboxykinase (GTP), mitochondrial
phosphoenolpyruvate carboxykinase 2
Phosphoenolpyruvate carboxykinase, mitochondrial precursor (GTP)
Phosphoenolpyruvate carboxylase 2
RATPEPCK
Phosphoenolpyruvate carboxylase II
RIKEN cDNA 1810010O14 gene
1810010O14
9130022B02
gAF1/PCK2
mitochondrial phosphoenolpyruvate carboxykinase 2
mitochondrial phosphoenolpyruvate carboxykinase II
mitochondrial Phosphoenolpyruvate carboxykinase precursor (GTP)
OTTHUMP00000164700
PCK2
RIKEN cDNA 9130022B02 gene
PEPCK2s

Mouse chromosome position 14 28.19 cM
14 21.0 cM

OMIM ID 614095
261650

Rat chromosome position 15p13

Hugo ID 8725

Human chromosome position 14q11.2
14q12

Swiss-Prot Accession Q16822
B4DW73
Q8BH04
B2RYG2
Q8BMM9
Q91Z10
O43253
Q86U01
Q9BV62

PIR ID S69546

GenBank ID NC_000014
XM_005267726
XP_005267783
XM_005267727
XP_005267784
NM_004563
NP_004554
NM_001018073
NP_001018083
XM_005267729
XP_005267786
XM_005267728
XP_005267785
NG_008162
NC_018925
AC_000146
ABBA01061330
ABBA01061331
AL136295
AMYH02028878
AMYH02028879
CH471078
EAW66115
Y11484
CAA72272
AK129934
AK301400
BAG62935
AK307913
AK311710
AK316206
BAH14577
BC001454
AAH01454
BU623248
BX248272
CAD62600
CR456913
CAG33194
X92720
CAA63380
Q16822
NC_000080
XM_006519632
XP_006519695
NM_028994
NP_083270
XM_006519633
XP_006519696
AC_000036
AAHY01114079
AC159002
CH466535
EDL36289
EDL36290
EDL36291
AK007429
AK030501
BAC26991
AK031612
BAC27477
AK034927
BAC28883
AK142561
BAE25104
AK147972
BAE28259
AK161944
AK165094
AK170242
BAE41656
AK181899
AK189946
AK199613
AK200018
AK200451
AK210790
AK214165
AK218043
AK218547
AK219654
BC010318
AAH10318
BC011126
BC023437
AAH23437
BC028326
AAH28326
Q8BH04
NC_005114
NM_001108377
NP_001101847
AC_000083
AABR06083265
AAHX01083058
CH474049
EDM14236
EDM14237
BC166766
AAI66766
CB787746
FQ226789
NT_026437
NW_001838110
NW_925539
AC_000057
CR602594
CR608041
CR609997
CR611857
CR613166
CR616177
CR618266
Q6IB91
Q86U01
NT_039606
NW_001030560
Q3TDE6
Q3UGF0
Q3UQD8
Q8R3X7
XM_341319
XP_341320
NW_001084707
XM_001055522
XP_001055522
NW_047454

Unigene ID Hs.75812
Mm.29856
Mm.491140
Rn.35508

KEGG ID hsa:5106
mmu:74551
rno:361042

Swiss-Prot ID PCKGM_MOUSE
PCKGM_HUMAN

EC Number 4.1.1.32

Ensembl ID ENSG00000100889
ENSP00000380171
ENST00000396973
ENSP00000216780
ENST00000216780
ENSP00000454011
ENST00000561286
ENSP00000441826
ENST00000545054
ENSMUSG00000040618
ENSMUSP00000038555
ENSMUST00000048781

Homologene ID 3356

Organism Homo sapiens
Mus musculus
Rattus norvegicus

MGI ID 1860456

RGD ID 1311112

MedScan ID 5106