Protein FBP1

URN urn:agi-llid:2203
Total Entities 0
Connectivity 431
Name FBP1
Description fructose-1,6-bisphosphatase 1
Notes Fructose-1,6-bisphosphatase 1, a gluconeogenesis regulatory enzyme, catalyzes the hydrolysis of fructose 1,6-bisphosphate to fructose 6-phosphate and inorganic phosphate. Fructose-1,6-diphosphatase deficiency is associated with hypoglycemia and metabolic acidosis.

GO Molecular Function catalytic activity
hydrolase activity
phosphoric ester hydrolase activity
fructose 1,6-bisphosphate 1-phosphatase activity
AMP binding
monosaccharide binding
metal ion binding

GO Cellular Component cytoplasm
cytosol

GO Biological Process metabolic process
small molecule metabolic process
regulation of gluconeogenesis
gluconeogenesis
negative regulation of glycolytic process
glucose metabolic process
fructose metabolic process
negative regulation of Ras protein signal transduction
negative regulation of cell growth
cellular response to insulin stimulus
cellular response to magnesium ion
cellular response to drug
fructose 6-phosphate metabolic process
dephosphorylation
carbohydrate metabolic process
protein homotetramerization

Pathway New Pathway
glycolysis/gluconeogenesis pathway
gluconeogenesis pathway

Group Glucose metabolism
Pentose-phosphate shunt
metabolic process
small molecule metabolic process
regulation of gluconeogenesis
gluconeogenesis
negative regulation of glycolytic process
glucose metabolic process
fructose metabolic process
negative regulation of Ras protein signal transduction
negative regulation of cell growth
cellular response to insulin stimulus
cellular response to magnesium ion
cellular response to drug
catalytic activity
hydrolase activity
phosphoric ester hydrolase activity
fructose 1,6-bisphosphate 1-phosphatase activity
fructose 6-phosphate metabolic process
dephosphorylation
carbohydrate metabolic process
protein homotetramerization
AMP binding
monosaccharide binding
metal ion binding
cytoplasm
cytosol
Secreted proteins
Biofluids assayable substances

LocusLink ID 2203
14121
24362

Cell Localization Cytoplasm

GO ID 0016208
0042132
0046872
0048029
0005975
0035690
0071286
0016311
0006002
0006000
0006094
0006006
0046580
0030308
0045820
0051289
0006111
0044281
0005737
0005829
0003824
0016787
0042578
0008152
0032869
0004331
0042802
0008270
0005625

Alias FBP
RP11-342C23.1
fructose-1,6-bisphosphatase 1
FBPase 1
fructose-bisphosphatase 1
growth-inhibiting protein 17
D-fructose-1,6-bisphosphate 1-phosphohydrolase 1
Fbp2
Fbp3
Fbp-2
FBPase liver
FBPase brain isoform
fructose-1,6-bisphosphatase isozyme 3
D-fructose-1,6-bisphosphate 1-phosphohydrolase 3
Fdp
Fructose-16- biphosphatase
fructose-1,6- biphosphatase 1
fructose-1,6- biphosphatase I
Fructose-1,6-bisphosphatase
fructose-1,6-bisphosphatase I
fructose-16-bisphosphatase 1
fructose-16-bisphosphatase I
liver FBPase
liver fructose-bisphosphatase
OTTHUMP00000021694
fructose bisphosphatase I
LOC116309
fructose bisphosphatase III
FBP I
FBP1
FBPase
FBPase I
FDPase 1
FDPase I
fructose bisphosphatase 1
fructose bisphosphatase 3
FBPase 3
D-fructose-1,6-bisphosphate 1-phosphohydrolase 1

Mouse chromosome position 13
13 B3-C1

OMIM ID 611570
229700

Rat chromosome position 17p14

Hugo ID 3606

Human chromosome position 9q22.3

Swiss-Prot Accession P09467
Q2TU34
Q9QXD6
P97323
P19112
Q64594
Q3UEH1
O75571
Q53F94
Q96E46

PIR ID A31342
A46666

GenBank ID NC_000009
NM_001127628
NP_001121100
NM_000507
NP_000498
NG_008174
NC_018920
AC_000141
ABBA01043635
ABBA01043636
ABBA01043637
ABBA01043638
ABBA01043639
ABBA01043640
AL161728
AMYH02021259
AMYH02021260
AY866483
AAW34363
CH471174
EAW92617
HB907234
CBF86692
HB964552
CBG16870
HC964643
CBV02277
HD021962
CBV30316
U21925
AAC50207
U21931
AF073475
AAC25774
AK223395
BAD97115
AK292199
BAF84888
AK316583
BAG38171
AY544122
AAT11153
BC012927
AAH12927
D26054
BAA05051
D26055
BAA05052
D26056
BAA05053
DA962803
L10320
AAA35817
M19922
AAA35517
U47918
AAA89097
U47919
AAA89098
P09467
NC_000079
NM_019395
NP_062268
AC_000035
AAHY01107011
AAHY01107012
AAHY01107013
AAHY01107014
AC156572
AC171004
AJ242919
CAB65255
AJ242920
CAB65599
AJ242921
CAB65256
AJ242922
CAB65257
AJ243030
CAB97174
AJ243031
CAB97175
AJ243032
CAB97176
AJ245385
CAB65264
AJ245386
CAB65265
AJ245387
CAB65266
AJ245388
CAB65267
AJ245389
CAB65268
AJ245390
CAB65269
AJ245391
CAB65551
CH466631
EDL16210
AJ132693
CAB65244
AK002216
BAB21941
AK149527
BAE28940
BC011480
AAH11480
BC051392
AAH51392
Y11067
CAA71946
P97323
Q9QXD6
NC_005116
NM_012558
NP_036690
AC_000085
AABR06089860
AABR06089861
AABR06089862
AAHX01089510
AAHX01089511
AAHX01089512
CH474087
EDL84407
M57274
AAA41131
M57278
M57279
M57281
M57282
M57283
M57284
BC078894
AAH78894
BC078895
AAH78895
J04112
AAA60739
M86240
AAA86425
P19112
NT_008470
NW_924506
NW_001839235
AC_000052
CAH72692
CAH72693
Q2TU34
Q5VZC3
NT_039589
NW_001030520
Q9JHT6
Q9JHT7
Q9JHT8
Q9QXA8
Q9QXA9
Q9QXB0
Q9QXB1
Q9QXB2
Q9QXB3
Q9QXC2
Q9QXC3
Q9QXC4
Q9QXC5
NW_047487
NW_001084720

Unigene ID Hs.494496
Mm.423078
Rn.33703

KEGG ID hsa:2203
mmu:14121
rno:24362

Swiss-Prot ID F16P1_RAT
F16P1_MOUSE
F16P1_HUMAN

EC Number 3.1.3.11

Ensembl ID ENSG00000165140
ENSP00000364475
ENST00000375326
ENSP00000408025
ENST00000415431
ENSMUSG00000069805
ENSMUSP00000090564
ENSMUST00000092888

Homologene ID 55467

Organism Homo sapiens
Mus musculus
Rattus norvegicus

MGI ID 95492

RGD ID 2595

MedScan ID 2203