| URN | urn:agi-llid:2203 |
|---|---|
| Connectivity | 113 |
| Name | Fbp1 |
| Description | fructose-1,6-bisphosphatase 1 |
| Notes | Fructose-1,6-bisphosphatase 1, a gluconeogenesis regulatory enzyme, catalyzes the hydrolysis of fructose 1,6-bisphosphate to fructose 6-phosphate and inorganic phosphate. Fructose-1,6-diphosphatase deficiency is associated with hypoglycemia and metabolic acidosis. |
| Pathway | New Pathway |
|---|---|
| glycolysis/gluconeogenesis pathway | |
| gluconeogenesis pathway |
| GO Molecular Function | hydrolase activity |
|---|---|
| monosaccharide binding | |
| metal ion binding | |
| magnesium ion binding | |
| phosphoric ester hydrolase activity | |
| fructose-2,6-bisphosphate 2-phosphatase activity | |
| fructose 1,6-bisphosphate 1-phosphatase activity |
| GO Cellular Component | soluble fraction |
|---|---|
| cytosol |
| GO Biological Process | gluconeogenesis |
|---|---|
| fructose metabolic process | |
| fructose 6-phosphate metabolic process | |
| cellular response to insulin stimulus | |
| carbohydrate metabolic process | |
| carbohydrate biosynthetic process |
| Ariadne Ontology | Pentose-phosphate shunt |
|---|---|
| Glucose metabolism |
| Group | Pentose-phosphate shunt |
|---|---|
| Glucose metabolism | |
| gluconeogenesis | |
| fructose metabolic process | |
| fructose 6-phosphate metabolic process | |
| cellular response to insulin stimulus | |
| carbohydrate metabolic process | |
| carbohydrate biosynthetic process | |
| hydrolase activity | |
| monosaccharide binding | |
| metal ion binding | |
| magnesium ion binding | |
| phosphoric ester hydrolase activity | |
| fructose-2,6-bisphosphate 2-phosphatase activity | |
| fructose 1,6-bisphosphate 1-phosphatase activity | |
| soluble fraction | |
| cytosol |
| MedScan ID | 2203 |
|---|
| Hugo ID | 3606 |
|---|
| Human chromosome position | 9q22.3 |
|---|
| LocusLink ID | 2203 |
|---|---|
| 14121 | |
| 24362 |
| Alias | FBP |
|---|---|
| RP11-342C23.1 | |
| fructose-1,6-bisphosphatase 1 | |
| FBPase 1 | |
| fructose-bisphosphatase 1 | |
| growth-inhibiting protein 17 | |
| D-fructose-1,6-bisphosphate 1-phosphohydrolase 1 | |
| Fbp2 | |
| Fbp-2 | |
| FBPase liver | |
| Fdp | |
| Fructose-16- biphosphatase | |
| fructose-1,6- biphosphatase 1 | |
| FBP I | |
| FBP1 | |
| FBPase | |
| FBPase I | |
| FDPase 1 | |
| FDPase I | |
| fructose bisphosphatase 1 | |
| fructose bisphosphatase I | |
| fructose-1,6- biphosphatase I | |
| Fructose-1,6-bisphosphatase | |
| fructose-1,6-bisphosphatase I | |
| fructose-16-bisphosphatase 1 | |
| fructose-16-bisphosphatase I | |
| liver FBPase | |
| liver fructose-bisphosphatase | |
| LOC116309 | |
| OTTHUMP00000021694 | |
| D-fructose-1,6-bisphosphate 1-phosphohydrolase 1 |
| Organism | Homo sapiens |
|---|---|
| Mus musculus | |
| Rattus norvegicus |
| OMIM ID | 611570 |
|---|---|
| 229700 |
| Mouse chromosome position | 13 |
|---|---|
| 13 B3-C1 |
| GO ID | 0042132 |
|---|---|
| 0004331 | |
| 0016787 | |
| 0046872 | |
| 0048029 | |
| 0042578 | |
| 0005975 | |
| 0032869 | |
| 0006002 | |
| 0006000 | |
| 0006094 | |
| 0005829 | |
| 0005625 | |
| 0000287 | |
| 0016051 | |
| 0042802 | |
| 0005739 | |
| 0003824 | |
| 0008270 |
| Rat chromosome position | 17p14 |
|---|
| Swiss-Prot Accession | P09467 |
|---|---|
| Q2TU34 | |
| Q5VZC3 | |
| Q9QXD6 | |
| Q9JHT6 | |
| Q9JHT7 | |
| Q9JHT8 | |
| Q9QXA8 | |
| Q9QXA9 | |
| Q9QXB0 | |
| Q9QXB1 | |
| Q9QXB2 | |
| Q9QXB3 | |
| Q9QXC2 | |
| Q9QXC3 | |
| Q9QXC4 | |
| Q9QXC5 | |
| P19112 | |
| Q3UEH1 | |
| Q64594 | |
| O75571 | |
| Q53F94 | |
| Q96E46 |
| PIR ID | A31342 |
|---|---|
| A46666 |
| Unigene ID | Hs.494496 |
|---|---|
| Mm.423078 | |
| Rn.33703 |
| KEGG ID | hsa:2203 |
|---|---|
| mmu:14121 | |
| rno:24362 |
| EC Number | 3.1.3.11 |
|---|
| Swiss-Prot ID | F16P1_MOUSE |
|---|---|
| F16P1_RAT | |
| F16P1_HUMAN | |
| Q2TU34_HUMAN |
| Cell Localization | Cytoplasm |
|---|
| IPI ID | IPI00228630 |
|---|---|
| IPI00231745 | |
| IPI00073772 | |
| IPI00644994 | |
| IPI00885722 |
| Homologene ID | 55467 |
|---|
| RGD ID | 2595 |
|---|
| MGI ID | 95492 |
|---|