Protein Gli3

URN urn:agi-llid:2737
Total Entities 0
Connectivity 295
Name Gli3
Description GLI family zinc finger 3
Notes This gene encodes a protein which belongs to the C2H2-type zinc finger proteins subclass of the Gli family. They are characterized as DNA-binding transcription factors and are mediators of Sonic hedgehog (Shh) signaling. The protein encoded by this gene localizes in the cytoplasm and activates patched Drosophila homolog (PTCH) gene expression. It is also thought to play a role during embryogenesis. Mutations in this gene have been associated with several diseases, including Greig cephalopolysyndactyly syndrome, Pallister-Hall syndrome, preaxial polydactyly type IV, and postaxial polydactyly types A1 and B. [provided by RefSeq]

Ariadne Ontology GLI-like
Oncogenes

GO Molecular Function chromatin binding
beta-catenin binding
histone acetyltransferase binding
histone deacetylase binding
nucleic acid binding
DNA binding
sequence-specific DNA binding
metal ion binding
zinc ion binding
sequence-specific DNA binding transcription factor activity

GO Cellular Component nucleolus
mediator complex
transcriptional repressor complex
cell projection
intracellular
cytoplasm
cytosol
intracellular membrane-bounded organelle
nucleus
cilium

GO Biological Process negative regulation of smoothened signaling pathway
negative regulation of canonical Wnt receptor signaling pathway
regulation of cell differentiation
regulation of cell proliferation
smoothened signaling pathway
smoothened signaling pathway involved in dorsal-ventral neural tube patterning
smoothened signaling pathway involved in spinal cord motor neuron cell fate specification
smoothened signaling pathway involved in ventral spinal cord interneuron specification
positive regulation of transcription, DNA-dependent
positive regulation of transcription from RNA polymerase II promoter
negative regulation of transcription, DNA-dependent
negative regulation of transcription from RNA polymerase II promoter
regulation of transcription, DNA-dependent
negative regulation of cell differentiation
negative regulation of cell proliferation
negative regulation of neuron differentiation
negative regulation of alpha-beta T cell differentiation
negative regulation of apoptotic process
positive regulation of neuroblast proliferation
positive regulation of alpha-beta T cell differentiation
positive regulation of osteoblast differentiation
positive regulation of chondrocyte differentiation
positive regulation of protein import into nucleus
regulation of apoptotic process
cell differentiation involved in kidney development
T cell differentiation in thymus
oligodendrocyte differentiation
forebrain radial glial cell differentiation
melanocyte differentiation
neuron fate commitment
transcription, DNA-dependent
cerebral cortex radial glia guided migration
thymocyte apoptotic process
negative thymic T cell selection
lateral ganglionic eminence cell proliferation
response to estrogen stimulus
axon guidance
wound healing
regulation of gene expression
multicellular organismal development
anatomical structure development
pattern specification process
anatomical structure formation involved in morphogenesis
developmental growth
embryonic digit morphogenesis
embryonic digestive tract morphogenesis
branching morphogenesis of a tube
hindgut morphogenesis
branching involved in ureteric bud morphogenesis
mammary gland specification
frontal suture morphogenesis
lambdoid suture morphogenesis
sagittal suture morphogenesis
forebrain development
pallium development
subpallium development
telencephalon development
palate development
tube development
inner ear development
neural tube development
central nervous system development
artery development
brain development
lung development
kidney development
heart development
tongue development
camera-type eye development
metanephros development
embryonic digestive tract development
mammary gland development
in utero embryonic development
limb development
anterior semicircular canal development
lateral semicircular canal development
dorsal-ventral pattern formation
anterior-posterior pattern specification
proximal-distal pattern formation
forebrain dorsal-ventral pattern formation
spinal cord dorsal-ventral patterning
embryonic morphogenesis
embryonic limb morphogenesis
embryonic skeletal system morphogenesis
nose morphogenesis
camera-type eye morphogenesis
odontogenesis of dentin-containing tooth
optic nerve morphogenesis
limb morphogenesis
protein processing

Pathway pancreatic cancer pathway
pancreatic cancer pathway

Group GLI-like
Oncogenes
negative regulation of smoothened signaling pathway
negative regulation of canonical Wnt receptor signaling pathway
regulation of cell differentiation
regulation of cell proliferation
smoothened signaling pathway
smoothened signaling pathway involved in dorsal-ventral neural tube patterning
smoothened signaling pathway involved in spinal cord motor neuron cell fate specification
smoothened signaling pathway involved in ventral spinal cord interneuron specification
positive regulation of transcription, DNA-dependent
positive regulation of transcription from RNA polymerase II promoter
negative regulation of transcription, DNA-dependent
negative regulation of transcription from RNA polymerase II promoter
regulation of transcription, DNA-dependent
negative regulation of cell differentiation
negative regulation of cell proliferation
negative regulation of neuron differentiation
negative regulation of alpha-beta T cell differentiation
negative regulation of apoptotic process
positive regulation of neuroblast proliferation
positive regulation of alpha-beta T cell differentiation
positive regulation of osteoblast differentiation
positive regulation of chondrocyte differentiation
positive regulation of protein import into nucleus
regulation of apoptotic process
cell differentiation involved in kidney development
T cell differentiation in thymus
oligodendrocyte differentiation
forebrain radial glial cell differentiation
melanocyte differentiation
neuron fate commitment
transcription, DNA-dependent
cerebral cortex radial glia guided migration
thymocyte apoptotic process
negative thymic T cell selection
lateral ganglionic eminence cell proliferation
response to estrogen stimulus
axon guidance
wound healing
regulation of gene expression
multicellular organismal development
anatomical structure development
pattern specification process
anatomical structure formation involved in morphogenesis
developmental growth
embryonic digit morphogenesis
embryonic digestive tract morphogenesis
branching morphogenesis of a tube
hindgut morphogenesis
branching involved in ureteric bud morphogenesis
mammary gland specification
frontal suture morphogenesis
lambdoid suture morphogenesis
sagittal suture morphogenesis
forebrain development
pallium development
subpallium development
telencephalon development
palate development
tube development
inner ear development
neural tube development
central nervous system development
artery development
brain development
lung development
kidney development
heart development
tongue development
camera-type eye development
metanephros development
embryonic digestive tract development
mammary gland development
in utero embryonic development
limb development
anterior semicircular canal development
lateral semicircular canal development
dorsal-ventral pattern formation
anterior-posterior pattern specification
proximal-distal pattern formation
forebrain dorsal-ventral pattern formation
spinal cord dorsal-ventral patterning
embryonic morphogenesis
embryonic limb morphogenesis
embryonic skeletal system morphogenesis
nose morphogenesis
camera-type eye morphogenesis
odontogenesis of dentin-containing tooth
optic nerve morphogenesis
limb morphogenesis
protein processing
chromatin binding
beta-catenin binding
histone acetyltransferase binding
histone deacetylase binding
nucleic acid binding
DNA binding
sequence-specific DNA binding
metal ion binding
zinc ion binding
sequence-specific DNA binding transcription factor activity
nucleolus
mediator complex
transcriptional repressor complex
cell projection
intracellular
cytoplasm
cytosol
intracellular membrane-bounded organelle
nucleus
cilium

MedScan ID 2737
140588

Hugo ID 4319

Human chromosome position 7p13

GenBank ID NC_000007
NM_000168
NP_000159
NG_008434
NC_018918
AC_000068
AC_000139
AC005026
AAP21869
AC005028
AAS01998
AC005158
AAS02015
AC073852
AJ250408
CAB59315
CH236951
EAL24002
CH471073
EAW94144
EAW94145
M20674
AA330409
AI863961
AK299299
BAG61313
AK308429
BC113616
AAI13617
BC117168
AAI17169
BF194991
BI497308
DA713549
M57609
AAA52564
P10071
NC_000079
NM_008130
NP_032156
AC_000035
AC163610
AC173115
AC173210
AF418601
CH466561
EDL32734
AK037232
AK045960
AK048009
AK053922
AK144851
BAE26100
AK158261
BAE34433
BC141135
AAI41136
BC145445
AAI45446
CA752350
X95255
CAA64543
Q61602
NC_005116
NM_080405
NP_536330
AC_000085
CH474030
EDL87409
AB073718
BAB71724
NT_007819
NT_079592
NW_001839004
NW_923240
AC_000050
NT_039578
NW_001030513
Q3TYX7
Q3UMJ8

LocusLink ID 2737
14634
140588

Alias PHS
ACLS
GCPS
PAPA
PAPB
PAP-A
PAPA1
PPDIV
GLI3FL
GLI3-190
transcriptional activator GLI3
oncogene GLI3
zinc finger protein GLI3
GLI-Kruppel family member GLI3
glioma-associated oncogene family zinc finger 3
Xt
Bph
Pdn
add
AI854843
AU023367
extra toes
brachyphalangy
polydactyly Nagoya
GLI3 form of 190 kDa
GLI3 full length protein
anterior digit pattern deformity
GLI-Kruppel family member GLI3 (Greig cephalopolysyndactyly syndrome)
PPD IV
OTTHUMP00000025248
OTTHUMP00000159085
OTTMUSP00000029127
OTTMUSP00000029128
anterior digit pattern deformity mutant
DNA-binding GLI3
extra toes mutant
GLI family zinc finger 3
GLI3
DNA-binding protein

Organism Homo sapiens
Mus musculus
Rattus norvegicus

OMIM ID 165240
200990
175700
241800
146510
174200
174700

Unigene ID Hs.21509
Mm.5098
Rn.199034

KEGG ID hsa:2737
mmu:14634
rno:140588

Swiss-Prot Accession P10071
B2RUG4
Q3TYX7
Q61602
A4D1W1
O75219
Q17RW4
Q75MT0
Q75MU9
Q9UDT5
Q9UJ39
Q3UMJ8

GO ID 0008013
0003682
0035035
0042826
0043565
0003700
0008270
0033077
0060873
0009952
0060840
0007411
0001658
0048593
0061005
0021801
0048589
0048566
0048557
0042733
0048704
0021798
0021861
0060364
0007507
0007442
0001701
0060366
0022018
0060875
0035108
0030324
0060594
0030318
0001656
0046639
0043066
0090090
0008285
0045665
0045879
0000122
0045892
0045060
0043585
0042475
0048709
0021631
0060021
0046638
0032332
0002052
0045669
0042307
0045944
0045893
0016485
0009954
0060367
0007224
0060831
0021776
0021775
0070242
0043586
0006351
0005929
0005737
0005829
0043231
0016592
0005730
0005634
0017053
0003677
0046872
0003676
0048856
0048646
0007420
0048754
0043010
0007417
0009953
0030326
0048598
0030900
0048839
0001822
0060173
0030879
0045596
0021915
0048663
0021543
0007389
0042981
0045595
0042127
0010468
0006355
0021513
0021544
0021537
0035295
0042995
0005622
0007275
0043627
0042060
0016564
0010552
0045941
0016481
0032583
0045449
0006350
0048558
0070491

PIR ID A35927

Swiss-Prot ID GLI3_MOUSE
GLI3_HUMAN
B2RUG4_MOUSE
Q3TYX7_MOUSE

Cell Localization Nucleus
Cytoplasm
Cell projection
cilium

IPI ID IPI00123429
IPI00018889
IPI00651982
IPI00857095

Mouse chromosome position 13 14.0 cM

Rat chromosome position 17q12.1

Homologene ID 139

MGI ID 95729

RGD ID 620272

Primary Cell Localization Nucleus