Protein G6pd

Name G6pd
Description glucose-6-phosphate dehydrogenase
Notes This gene encodes glucose-6-phosphate dehydrogenase. This protein is a cytosolic enzyme encoded by a housekeeping X-linked gene whose main function is to produce NADPH, a key electron donor in the defense against oxidizing agents and in reductive biosynthetic reactions. G6PD is remarkable for its genetic diversity. Many variants of G6PD, mostly produced from missense mutations, have been described with wide ranging levels of enzyme activity and associated clinical symptoms. G6PD deficiency may cause neonatal jaundice, acute hemolysis, or severe chronic non-spherocytic hemolytic anemia. Two transcript variants encoding different isoforms have been found for this gene.
Owner Public
URN urn:agi-llid:2539
Connectivity 629

LocusLink ID 2539
14381
24377

OMIM ID 305900

GO ID 0005488
0004345
0016491
0005975
0006010
0006006
0008152
0006098
0005575
0005737
0003824
0042803
0006741
0001998
0001816
0048821
0006749
0032613
0032615
0019322
0040014
0006979
0002033
0050661
0005536
0005529
0051156
0009051
0045767
0005829
0005792
0005634
0005625

Hugo ID 4057

Human chromosome position Xq28

GenBank ID NC_000023
NM_001042351
NP_001035810
NM_000402
NP_000393
NT_011726
NW_001842419
NW_927732
AC_000155
AC_000066
AF277315
AAL27011
AY158096
AAN76367
AY158097
AAN76368
AY158098
AAN76369
AY158099
AAN76370
AY158100
AAN76371
AY158101
AAN76372
AY158102
AAN76373
AY158103
AAN76374
AY158104
AAN76375
AY158105
AAN76376
AY158106
AAN76377
AY158107
AAN76378
AY158108
AAN76379
AY158109
AAN76380
AY158110
AAN76381
AY158111
AAN76382
AY158112
AAN76383
AY158113
AAN76384
AY158114
AAN76385
AY158115
AAN76386
AY158116
AAN76387
AY158117
AAN76388
AY158118
AAN76389
AY158119
AAN76390
AY158120
AAN76391
AY158121
AAN76392
AY158122
AAN76393
AY158123
AAN76394
AY158124
AAN76395
AY158125
AAN76396
AY158126
AAN76397
AY158127
AAN76398
AY158128
AAN76399
AY158129
AAN76400
AY158130
AAN76401
AY158131
AAN76402
AY158132
AAN76403
AY158133
AAN76404
AY158134
AAN76405
AY158135
AAN76406
AY158136
AAN76407
AY158137
AAN76408
AY158138
AAN76409
AY158139
AAN76410
AY158140
AAN76411
AY158141
AAN76412
AY158142
AAN76413
CH471172
EAW72682
EAW72683
EAW72684
EAW72685
EAW72686
EAW72687
DQ173568
ABB90566
DQ173592
ABC25732
DQ173593
ABC25737
DQ173594
ABC25742
DQ173595
ABC25747
DQ173596
ABC25752
DQ173597
ABC25757
DQ173598
ABC25761
DQ173599
ABC25766
DQ173600
ABC25771
DQ173601
ABC25776
DQ173602
ABC25781
DQ173603
ABC25786
DQ173604
ABC25791
DQ173605
ABC25796
DQ173606
ABC25801
DQ173607
ABC25806
DQ173608
ABC25811
DQ173609
ABC25816
DQ173610
ABC25821
DQ173611
ABC25826
DQ173612
ABC25831
DQ173613
ABC25836
DQ173614
ABC25841
DQ173615
ABC25846
DQ173616
ABC25851
DQ173617
ABC25856
DQ173618
ABC25861
DQ173619
ABC25866
DQ173620
ABC25871
DQ173621
ABC25876
DQ173622
ABC25881
DQ173623
ABC25886
DQ173624
ABC25891
DQ173625
ABC25896
DQ173626
ABC25901
DQ173627
ABC25906
DQ173628
ABC25911
DQ173629
ABC25916
DQ173630
ABC25921
DQ173631
ABC25926
DQ173632
ABC25931
DQ173633
ABC25936
DQ173634
ABC25941
DQ173635
ABC25946
DQ173636
ABC25951
DQ173637
ABC25956
DQ173638
ABC25961
DQ173639
ABC25966
DQ173640
ABC25971
DQ173641
ABC25976
DQ173642
ABC25981
DQ832766
ABH03569
L44140
AAA92653
M23423
AAB59390
M65234
AAA63175
S64462
AAB20299
X53815
CAA37811
X55448
CAA39089
AK292304
BAF84993
AL560686
BC000337
AAH00337
CR606589
CR624380
M19866
AAA52501
M21248
AAA52500
M27940
AAA52504
S58359
AAB26169
X03674
CAA27309
P11413
Q0PHS1
Q2Q9B7
Q2Q9H2
Q2VF42
DQ892219
ABM83145
DQ895415
ABM86341
NC_000086
NM_008062
NP_032088
NT_039740
NT_111917
NT_039706
NW_001035173
AC_000042
AC091474
AF326207
AAK69185
AL669976
CAM45964
CAM45965
AL807376
AL954863
CH466650
EDL29811
U88533
AAB52998
U88534
AAB52999
X53617
CAA37679
AK088135
BAC40166
AK148031
AK165207
BAE38077
AK183482
AK201217
BC075663
AAH75663
Z11911
CAA77967
Q00612
Q3TNL1
Q790Y8
NC_005120
NM_017006
NP_058702
NW_001084770
NW_048052
AC_000069
CH474099
EDL84965
BC081820
AAH81820
CB729647
X07467
CAA30355
P05370

Unigene ID Hs.461047
Hs.684904
Mm.27210
Rn.11040

KEGG ID hsa:2539
mmu:14381
rno:24377

Alias G6PD1
glucose-6-phosphate dehydrogenase
glucose-6-phosphate 1-dehydrogenase
glucose-6-phosphate dehydrogenase, G6PD
G28A
G6pd
Gpdx
RP23-436K3.17
glucose-6-phosphate dehydrogenase X-linked
G6pdx
G6pdx-ps1
glucose-6-phosphate dehydrogenase 2
Glucose-6-phosphate dehydrogenase, autosomal
6-phosphoglucose dehydrogenase
Entner-Doudoroff enzyme
NADP-dependent glucose 6-phosphate dehydrogenase
Zwischenferment
glucose-6-phosphate dehydrogenase X-linked, pseudogene
NADP-glucose-6-phosphate dehydrogenase
glucose-6-phosphate dehydrogenase II
G6pd2
G6PD I
NADP-glucose-6-phosphate dehydrogenases
6-phosphoglucose dehydrogenases
D-glucose 6-phosphate dehydrogenases
NADP-dependent glucose 6-phosphate dehydrogenases
G-6-PDHs
glucose-6-phosphate dehydrogenase X-linked, pseudogene I
G-6-PDH
glucose-6-phosphate dehydrogenase X-linked, pseudogene 1
G6pdx-ps I
D-glucose 6-phosphate dehydrogenase
G(28)A
G28-a
G 28A
G-28a

Organism Homo sapiens
Mus musculus
Rattus norvegicus

Mouse chromosome position X 30.02 cM

Rat chromosome position Xq37

Cell Localization Cytoplasm

Homologene ID 37906

Pathway pentose phosphate pathway

MGI ID 105979

Ariadne Ontology Pentose-phosphate shunt

RGD ID 2645

GO Molecular Function catalytic activity
binding
sugar binding
glucose binding
NADP binding
protein homodimerization activity
oxidoreductase activity
glucose-6-phosphate dehydrogenase activity

GO Cellular Component cellular_component
soluble fraction
microsome
cytoplasm
cytosol
nucleus

GO Biological Process metabolic process
regulation of anti-apoptosis
regulation of multicellular organism growth
erythrocyte development
vasodilation by angiotensin involved in regulation of systemic arterial blood pressure
angiotensin mediated vasoconstriction involved in regulation of systemic arterial blood pressure
pentose biosynthetic process
pentose-phosphate shunt
pentose-phosphate shunt, oxidative branch
glucose metabolic process
glucose 6-phosphate metabolic process
glucose 6-phosphate utilization
NADP biosynthetic process
glutathione metabolic process
carbohydrate metabolic process
cytokine production
interleukin-12 production
interleukin-10 production
response to oxidative stress

Group cellular_component
soluble fraction
microsome
cytoplasm
cytosol
nucleus
catalytic activity
binding
sugar binding
glucose binding
NADP binding
protein homodimerization activity
oxidoreductase activity
glucose-6-phosphate dehydrogenase activity
metabolic process
regulation of anti-apoptosis
regulation of multicellular organism growth
erythrocyte development
vasodilation by angiotensin involved in regulation of systemic arterial blood pressure
angiotensin mediated vasoconstriction involved in regulation of systemic arterial blood pressure
pentose biosynthetic process
pentose-phosphate shunt
pentose-phosphate shunt, oxidative branch
glucose metabolic process
glucose 6-phosphate metabolic process
glucose 6-phosphate utilization
NADP biosynthetic process
glutathione metabolic process
carbohydrate metabolic process
cytokine production
interleukin-12 production
interleukin-10 production
response to oxidative stress
Pentose-phosphate shunt