Protein Mthfr

URN urn:agi-llid:4524
Total Entities 0
Connectivity 1061
Name Mthfr
Description methylenetetrahydrofolate reductase (NAD(P)H)
Notes The protein encoded by this gene catalyzes the conversion of 5,10-methylenetetrahydrofolate to 5-methyltetrahydrofolate, a co-substrate for homocysteine remethylation to methionine. Genetic variation in this gene influences susceptibility to occlusive vascular disease, neural tube defects, colon cancer and acute leukemia, and mutations in this gene are associated with methylenetetrahydrofolate reductase deficiency.

GO Molecular Function oxidoreductase activity
methylenetetrahydrofolate reductase (NAD(P)H) activity
catalytic activity
flavin adenine dinucleotide binding
NADP binding
modified amino acid binding

GO Cellular Component cytosol
neuron projection

GO Biological Process metabolic process
small molecule metabolic process
oxidation-reduction process
methionine biosynthetic process
vitamin metabolic process
cellular amino acid metabolic process
homocysteine metabolic process
S-adenosylmethionine metabolic process
tetrahydrofolate metabolic process
folic acid metabolic process
tetrahydrofolate interconversion
methionine metabolic process
water-soluble vitamin metabolic process
blood circulation
response to drug
response to amino acid
response to folic acid
response to vitamin B2
response to interleukin-1
response to hypoxia

Pathway Proteins Involved in Pathogenesis of Amyotrophic Lateral Sclerosis
Proteins Involved in Pathogenesis of Myocardial Ischemia
homocysteine metabolic pathway

Group Folate and pterins biosynthesis
metabolic process
small molecule metabolic process
oxidation-reduction process
methionine biosynthetic process
oxidoreductase activity
methylenetetrahydrofolate reductase (NAD(P)H) activity
vitamin metabolic process
cellular amino acid metabolic process
homocysteine metabolic process
S-adenosylmethionine metabolic process
tetrahydrofolate metabolic process
folic acid metabolic process
tetrahydrofolate interconversion
methionine metabolic process
water-soluble vitamin metabolic process
blood circulation
response to drug
response to amino acid
response to folic acid
response to vitamin B2
response to interleukin-1
response to hypoxia
catalytic activity
flavin adenine dinucleotide binding
NADP binding
modified amino acid binding
cytosol
neuron projection
Proteins Involved in Pathogenesis of Mental Retardation Caused by Hypothyroidism
Genes Associated with Systemic Lupus Erythematosus
Proteins Involved in Pathogenesis of Li-Fraumeni Syndrome
Genes with Mutations Associated with Atherosclerosis
Biofluids assayable substances

LocusLink ID 4524
17769
362657

Cell Localization Mitochondria

GO ID 0004489
0072341
0008015
0006520
0046655
0050667
0009086
0044281
0035999
0006766
0006767
0005829
0050661
0003824
0050660
0016491
0008152
0006555
0055114
0046653
0043005
0046500
0043200
0042493
0051593
0001666
0070555
0033274
0005625

Alias RP11-56N19.4
methylenetetrahydrofolate reductase
5,10-methylenetetrahydrofolate reductase (NADPH)
AI323986
RP23-139J21.2
methylenetetrahydrofolate dehydrogenase (NADPH2)
methylenetetrahydrofolate reductase intermediate form
MTHFR
OTTHUMP00000002367
OTTHUMP00000002368
OTTHUMP00000002373
OTTMUSP00000035697
methylenetetrahydrofolate reductase (NAD(P)H)
5,10-methylenetetrahydrofolate reductase (NAD(P)H)
methylenetetrahydrofolate dehydrogenase (NADP(H)2)
OTTMUSP00000010830
5,10-methylenetetrahydrofolate reductase (FADH)
methylenetetrahydrofolate dehydrogenase (NAD(P)H2)
5,10-methylenetetrahydrofolate reductase
5,10-methylenetetrahydrofolate reductase (FADH) activity
5,10-methylenetetrahydrofolate reductase (FADH)s
5,10-methylenetetrahydrofolate reductase (FADH2)
5,10-methylenetetrahydrofolate reductase (NADP(H))
5,10-CH2-H4folate reductase
5,10-methylenetetrahydrofolic acid reductase
5,10-methylenetetrahydrofolic acid reductases
Methylene tetrahydrofolate reductase
5,10-CH2-H4folate reductases

Mouse chromosome position 4 78.67 cM
4 76.4 cM

OMIM ID 607093
236250
601634
181500
188050
119530

Rat chromosome position 5q36

Hugo ID 7436

Human chromosome position 1p36.3

Swiss-Prot Accession P42898
Q59GJ6
Q8IU67
Q5SNW6
A2A7F7
Q3UDB2
Q497H7
Q9WU20
D4A7E8
B2R7A6
Q5SNW9
Q7Z6M6
Q8IU73
Q9UQR2
Q8CDE4
Q5SNW5
Q5SNW7
Q9NY62
Q9NY63
Q3V399
Q8BHN2
Q8CJA5
Q8CJA6
Q8CJA7
Q8CJA8
Q8CJA9
Q62984

PIR ID S46454

GenBank ID NC_000001
NM_005957
NP_005948
XM_005263463
XP_005263520
XM_005263460
XP_005263517
XM_005263462
XP_005263519
XM_005263461
XP_005263518
XM_005263458
XP_005263515
XM_005263459
XP_005263516
NG_013351
NC_018912
AC_000133
ABBA01003060
AF105977
AAD17965
AF105978
AF105979
AF105980
AF105981
AF105982
AF105983
AF105984
AF105985
AF105986
AF105987
AF398930
AAN40863
AAN40864
AAN40865
AJ249275
CAB81551
CAB81552
AL021155
AL953897
AMYH02000300
AY338232
AAP88033
CH471130
EAW71708
EAW71709
AB209113
BAD92350
AJ237672
CAB41971
AK312907
BAG35753
AY046560
AAL17646
AY046561
AAL17647
AY046562
AAL17648
AY046563
AAL17649
AY046564
AAL17650
AY046565
AAL17651
BC011614
BC018766
BC053509
AAH53509
CN355286
JQ429447
AFQ62002
P42898
U09806
AAA74440
NC_000070
XM_006538618
XP_006538681
XM_006538620
XP_006538683
XM_006538622
XP_006538685
NM_010840
NP_034970
XM_006538619
XP_006538682
XM_006538621
XP_006538684
XM_006538617
XP_006538680
XR_390732
XR_390731
XR_390733
NM_001161798
NP_001155270
NR_027809
NT_166299
XM_006535928
XP_006535991
XR_389856
XR_389857
XM_006535929
XP_006535992
XM_006535932
XP_006535995
XM_006535930
XP_006535993
XM_006535931
XP_006535994
XM_006535933
XP_006535996
AC_000026
AAHY01041896
AF105988
AAD20313
AF105989
AF105990
AF105991
AF105992
AF105993
AF105994
AF105995
AF105996
AF105997
AF105998
AF260234
AF398931
AAN40867
AAN40868
AL606929
AY046557
AAL17641
AAL17642
CH466594
EDL14794
EDL14795
EDL14796
EDL14797
EDL14798
CU207376
AF404270
AAN40872
AF404271
AAN40873
AF404272
AAN40874
AF404273
AAN40875
AF404274
AAN40876
AK030192
BAC26832
AK043144
BAE43318
AK149795
AK150159
BAE29349
AK191706
AK199913
AK219632
BB726553
BC019719
BC051017
AAH51017
BC052466
AAH52466
BC100550
AAI00551
Q9WU20
NC_005104
XM_006239414
XP_006239476
XM_006239415
XP_006239477
XM_006239416
XP_006239478
XM_006239417
XP_006239479
XM_342975
XP_342976
XM_006239413
XP_006239475
XM_006239418
XP_006239480
AC_000073
XM_006225612
XP_006225674
XM_006225613
XP_006225675
XM_006225614
XP_006225676
XM_006225615
XP_006225677
XM_001074061
XP_001074061
XM_006225611
XP_006225673
XM_006225616
XP_006225678
AABR06040922
AAHX01040795
CH473968
EDL81091
EDL81092
EDL81093
EDL81094
EDL81095
EDL81096
U57049
AAB01988
NT_021937
NW_923572
NW_001838534
AC_000044
CAI15885
CAI15886
CAI15887
CAI15888
CAI15889
Q59GJ6
Q5SNW5
Q5SNW6
Q5SNW7
Q8IU67
Q8IU73
Q9NY62
Q9NY63
NT_039268
NW_001030773
CAM14893
CAM14895
CAM14896
Q3UDB2
Q3V399
Q497H7
Q8BHN2
Q8CDE4
Q8CJA5
Q8CJA6
Q8CJA7
Q8CJA8
Q8CJA9
NW_001084844
NW_047727
Q62984

Unigene ID Hs.214142
Hs.737916
Mm.89959
Rn.10494

KEGG ID hsa:4524
mmu:17769
rno:362657

Swiss-Prot ID MTHR_HUMAN
MTHR_MOUSE
A2A7F7_MOUSE
Q3UDB2_MOUSE
Q8CDE4_MOUSE
Q59GJ6_HUMAN
Q497H7_MOUSE
Q8IU67_HUMAN
Q5SNW9_HUMAN

EC Number 1.5.1.20

Ensembl ID ENSG00000177000
ENSP00000365775
ENST00000376590
ENSMUSG00000029009
ENSMUSP00000069774
ENSMUST00000069604

Homologene ID 4349

Organism Homo sapiens
Mus musculus
Rattus norvegicus

MGI ID 106639

RGD ID 1309952

MedScan ID 4524

IPI ID IPI00002487
IPI00284146
IPI00648736
IPI00646036
IPI00880754
IPI00646654
IPI00643819
IPI00642645
IPI00880907
IPI00880862
IPI00318090
IPI00894661
IPI00895457
IPI00894887
IPI00210370
IPI00388156