Protein PAFAH1B1

URN urn:agi-llid:4186
Connectivity 77
Name PAFAH1B1
Description platelet-activating factor acetylhydrolase, isoform Ib, subunit 1 (45kDa)
Notes This locus was identified as encoding a gene that when mutated or lost caused the lissencephaly associated with Miller-Dieker lissencephaly syndrome. This gene encodes the non-catalytic alpha subunit of the intracellular Ib isoform of platelet-activating factor acteylhydrolase, a heterotrimeric enzyme that specifically catalyzes the removal of the acetyl group at the SN-2 position of platelet-activating factor (identified as 1-O-alkyl-2-acetyl-sn-glyceryl-3-phosphorylcholine). Two other isoforms of intracellular platelet-activating factor acetylhydrolase exist: one composed of multiple subunits, the other, a single subunit. In addition, a single-subunit isoform of this enzyme is found in serum. [provided by RefSeq]

Pathway reelin signaling pathway
Reelin signaling pathway
Reelin signaling pathway

GO Molecular Function hydrolase activity
phosphoprotein binding
protein complex binding
dynein binding
protein homodimerization activity
dynein intermediate chain binding
dynactin binding
phospholipase binding
microtubule binding
heparin binding
platelet-activating factor acetyltransferase activity

GO Cellular Component cell leading edge
membrane
soluble fraction
insoluble fraction
neuron projection
neuronal cell body
growth cone
cytoplasm
axon part
perinuclear region of cytoplasm
cell cortex
cytosol
centrosome
astral microtubule
kinetochore
nuclear membrane
nuclear envelope
microtubule associated complex
microtubule
spindle
kinesin complex
cytoskeleton
nucleus
microtubule cytoskeleton
vesicular fraction
motile primary cilium
nonmotile primary cilium

GO Biological Process neuroblast proliferation
cell division
cell cycle
microtubule-based process
multicellular organismal development
transport
cerebral cortex development
hippocampus development
cell differentiation
acrosome assembly
layer formation in the cerebral cortex
positive regulation of axon extension
nervous system development
negative regulation of neuron projection development
corpus callosum morphogenesis
cerebral cortex neuron differentiation
brain morphogenesis
adult locomotory behavior
transmission of nerve impulse
learning or memory
neuromuscular process controlling balance
microtubule organizing center organization
microtubule cytoskeleton organization
actin cytoskeleton organization
stem cell division
establishment of mitotic spindle orientation
mitosis
vesicle transport along microtubule
retrograde axon cargo transport
positive regulation of mitotic cell cycle
synaptic transmission
regulation of Rho GTPase activity
nuclear envelope disassembly
cell migration
neuron migration
platelet activating factor metabolic process
cellular response to protein stimulus
lipid catabolic process
establishment of centrosome localization
nuclear migration

Ariadne Ontology Phospholipid biosynthesis
Microtubule cytoskeleton assembly
Kinetochore assembly
Microtubule sliding
Spindle assembly

Group Phospholipid biosynthesis
Microtubule cytoskeleton assembly
Kinetochore assembly
Microtubule sliding
Spindle assembly
neuroblast proliferation
cell division
cell cycle
microtubule-based process
multicellular organismal development
transport
cerebral cortex development
hippocampus development
cell differentiation
acrosome assembly
layer formation in the cerebral cortex
positive regulation of axon extension
nervous system development
negative regulation of neuron projection development
corpus callosum morphogenesis
cerebral cortex neuron differentiation
brain morphogenesis
adult locomotory behavior
transmission of nerve impulse
learning or memory
neuromuscular process controlling balance
microtubule organizing center organization
microtubule cytoskeleton organization
actin cytoskeleton organization
stem cell division
establishment of mitotic spindle orientation
mitosis
vesicle transport along microtubule
retrograde axon cargo transport
positive regulation of mitotic cell cycle
synaptic transmission
regulation of Rho GTPase activity
nuclear envelope disassembly
cell migration
neuron migration
platelet activating factor metabolic process
cellular response to protein stimulus
lipid catabolic process
establishment of centrosome localization
nuclear migration
hydrolase activity
phosphoprotein binding
protein complex binding
dynein binding
protein homodimerization activity
dynein intermediate chain binding
dynactin binding
phospholipase binding
microtubule binding
heparin binding
platelet-activating factor acetyltransferase activity
cell leading edge
membrane
soluble fraction
insoluble fraction
neuron projection
neuronal cell body
growth cone
cytoplasm
axon part
perinuclear region of cytoplasm
cell cortex
cytosol
centrosome
astral microtubule
kinetochore
nuclear membrane
nuclear envelope
microtubule associated complex
microtubule
spindle
kinesin complex
cytoskeleton
nucleus
microtubule cytoskeleton
vesicular fraction
motile primary cilium
nonmotile primary cilium

MedScan ID 4186

Hugo ID 8574

Human chromosome position 17p13.3

LocusLink ID 4186
5048
18472
83572

Alias MDS
LIS1
LIS2
MDCR
PAFAH
platelet-activating factor acetylhydrolase IB subunit alpha
LIS-1
PAFAH alpha
PAF-AH alpha
PAF-AH 45 kDa subunit
lissencephaly 1 protein
lissencephaly-1 protein
PAF acetylhydrolase 45 kDa subunit
platelet-activating factor acetylhydrolase, isoform Ib, subunit 1 (45kDa)
platelet-activating factor acetylhydrolase, isoform Ib, alpha subunit (45kD)
Mdsh
Ms10u
Pafaha
MMS10-U
MGC25297
RP23-194P5.2
OTTMUSP00000006469
OTTMUSP00000006470
platelet-activating factor acetylhydrolase IB alpha subunit
platelet-activating factor acetylhydrolase 1b, regulatory subunit 1
platelet-activating factor acetylhydrolase, isoform 1b, beta1 subunit
PAF-AH beta
platelet-activating factor acetylhydrolase beta subunit (PAF-AH beta)
platelet-activating factor acetylhydrolase, isoform Ib, alpha subunit 45kDa
CYTOSOLIC PAF-AH IB
LIS I
Lissencephaly 1 gene
Lissencephaly-1 gene
LOC100046589
MDS protein
Miller-Dieker syndrome chromosome region
minisatellite 10u detected by probe MMS10
PAF acetylhydrolase 1B
PAF-AH 1B
PAF-AH 45
PAF-AH IB
Pafah1b I
Pafah1b1
platelet-activating factor acetylhydrolase 1b, regulatory subunit 1 (45kDa)
platelet-activating factor acetylhydrolase beta subunit
platelet-activating factor acetylhydrolase Ib
Platelet-activating factor acetylhydrolase, isoform 1B, alpha subunit
platelet-activating factor acetylhydrolase, isoform 1b, subunit 1
platelet-activating factor acetylhydrolase, isoform Ib, alpha subunit (45kD
platelet-activating factor acetylhydrolase, isoform Ib, alpha subunit
PAF-AH 45 kDa subunit

Organism Homo sapiens
Mus musculus
Rattus norvegicus

GenBank ID NC_000017
NM_000430
NP_000421
NT_010718
NW_926584
NW_001838403
NG_009799
AC_000060
AC_000149
AC005696
AC015799
CH471108
EAW90536
U72342
AAC51111
AF208835
AF208836
AF208837
AAL34972
AF208838
AAL34973
AF400434
AAK92483
AK293918
BAG57299
AK303015
BAG64145
AK313078
BAG35904
BC064638
AAH64638
BX538346
CAD98141
CR594061
CR599910
CR608859
CR622803
CR624292
L13385
AAA02880
L13386
AAA02881
L13387
AAA02882
L13388
L25107
S81396
P43034
NC_000077
NM_013625
NP_038653
NT_096135
NW_001030480
XM_001476465
XP_001476515
AC_000033
AJ243741
AJ243742
AJ243743
AJ243744
AJ243745
AJ243746
AJ243747
AJ243748
AJ243749
AJ243750
AJ243752
AJ243753
AJ248244
AL607024
CAI24375
CAI24377
CH466596
EDL12776
U95117
U95118
U95119
AAC63099
U95120
AAC63098
AK144908
BAE26129
AK147207
BAE27764
AK147229
AK147237
BAE27787
AK147309
BAE27837
AK147507
BAE27961
AK147515
BAE27965
AK147533
BAE27977
AK147793
BAE28141
AK152284
AK160764
BAE35996
AK161751
AK164008
BAE37586
AK164276
AK167448
BAE39534
AK167824
BAE39846
AK168929
BAE40742
AK168960
BAE40766
AY189217
AAO41716
AY189218
AAO41717
BC014831
AAH14831
BC026141
AAH26141
BC046989
BC099462
BQ895724
L25108
L25109
AAD23059
U95116
AAC04610
P63005
Q3TIK0
Q3TJG1
Q3TUH5
Q3UGR6
Q3UH92
Q3UHM0
Q5SW16
Q5SW18
NC_005109
NM_031763
NP_113951
NW_047336
NW_001084656
AC_000078
CH473948
EDM05186
EDM05187
AF016049
AAC27975
BC072510
AAH72510
P63004

OMIM ID 601545
607432
247200

Mouse chromosome position 11 44.0 cM

GO ID 0034452
0045502
0045505
0008201
0008017
0043274
0051219
0042803
0001675
0030036
0008344
0048854
0007049
0030154
0021987
0021540
0000132
0021766
0021819
0007611
0016042
0000226
0031023
0007017
0007067
0007275
0007399
0007405
0050885
0001764
0051081
0046469
0032319
0008090
0017145
0007268
0019226
0006810
0047496
0000235
0005938
0031252
0005813
0005737
0005829
0030426
0005626
0000776
0016020
0005874
0005875
0031512
0043025
0031513
0005635
0031965
0005634
0048471
0005625
0005819
0042598
0016787
0051301
0016477
0005856
0015630
0047179
0032403
0071445
0021895
0051660
0010977
0007097
0045773
0045931
0033267
0005871
0043005
0005515

Rat chromosome position 10q24

Swiss-Prot Accession P43034
P63005
Q3UH92
Q5SW18
Q3TIK0
Q3TJG1
Q3TUH5
Q3UGR6
Q3UHM0
Q5SW16
P63004
O35592
P43035
P81692
Q9R2A6
B2R7Q7
Q8WZ88
Q8WZ89

PIR ID S36113

Unigene ID Hs.77318
Mm.397111
Rn.5827

KEGG ID hsa:5048
mmu:18472
rno:83572

EC Number 3.1.1.47

Swiss-Prot ID LIS1_RAT
LIS1_HUMAN
LIS1_MOUSE
Q3UH92_MOUSE
Q5SW18_MOUSE
B2R7Q7_HUMAN

Cell Localization Cytoplasm
cytoskeleton
centrosome
spindle
Nucleus membrane
Nucleus

IPI ID IPI00231298
IPI00218728
IPI00760905
IPI00227864
IPI00309207
IPI00873228
IPI00755990
IPI00648594

Homologene ID 371

RGD ID 620331

MGI ID 109520