Protein Dclre1c

URN urn:agi-llid:6321
Total Entities 0
Connectivity 130
Name Dclre1c
Description DNA cross-link repair 1C
Notes This gene encodes a nuclear protein that is involved in V(D)J recombination and DNA repair. The protein has single-strand-specific 5'-3' exonuclease activity; it also exhibits endonuclease activity on 5' and 3' overhangs and hairpins when complexed with protein kinase, DNA-activated, catalytic polypeptide. Mutations in this gene cause Athabascan-type severe combined immunodeficiency (SCIDA). [provided by RefSeq, Jul 2008]

Ariadne Ontology DNA repair

GO Molecular Function hydrolase activity
nuclease activity
exonuclease activity
endonuclease activity
single-stranded DNA specific endodeoxyribonuclease activity
5'-3' exonuclease activity

GO Cellular Component nucleus

GO Biological Process B cell differentiation
nucleic acid phosphodiester bond hydrolysis
DNA repair
DNA recombination
telomere maintenance
double-strand break repair
response to DNA damage stimulus
chromosome organization
response to ionizing radiation

Pathway Double Strand DNA Non-Homologous Repair
non-homologous end joining pathway of double-strand break repair

Group DNA repair
B cell differentiation
nucleic acid phosphodiester bond hydrolysis
DNA repair
DNA recombination
telomere maintenance
double-strand break repair
response to DNA damage stimulus
chromosome organization
response to ionizing radiation
hydrolase activity
nuclease activity
exonuclease activity
endonuclease activity
single-stranded DNA specific endodeoxyribonuclease activity
5'-3' exonuclease activity
nucleus

MedScan ID 6321

Hugo ID 17642

Human chromosome position 10p13

GenBank ID NC_000010
NM_022487
NP_071932
NM_001033855
NP_001029027
NM_001033857
NP_001029029
NM_001033858
NP_001029030
NG_007276
NC_018921
AC_000142
AL360083
CAI40018
CAI40019
CAI40020
CAI40021
CAI40022
CAI40023
CAI40024
CAI40025
CH471072
EAW86248
EAW86249
EAW86250
EAW86251
EAW86252
DQ504427
ABF47101
AF088055
AF395747
AAM53255
AF395748
AAM53256
AF395749
AAM53257
AF395750
AAM53258
AF395751
AAM53259
AF395752
AAM53260
AJ296101
CAC37570
AK021422
BAB13820
AK022922
BAG51137
AK093757
BAG52759
AK290598
BAF83287
AK307912
AW954867
BC000863
AAH00863
BC009185
AAH09185
BC022254
AAH22254
BC108276
BE799340
BX648858
Q96SD1
NC_000068
NM_175683
NP_783614
NM_001110214
NP_001103684
NM_146114
NP_666226
AC_000024
AL732620
CAM16038
CAM16039
CAM16040
CAM16041
CH466542
EDL07928
EDL07929
EDL07930
EDL07931
EDL07932
AF387731
AAM89119
AK037126
BAC29713
AK038788
AK052369
BAC34960
AK052490
AK086575
AK088810
BAC40586
AK162838
AK166324
BAE38706
BC030680
BC108935
AAI08936
BX516565
BY010590
BY729142
Q8K4J0
NC_005116
NM_147145
NP_671486
AC_000085
CH473990
EDL78692
EDL78693
AF395746
AAM89124
BC083546
AAH83546
Q5XIX3

LocusLink ID 6321
64421
227525
259171

Alias SCIDA
SNM1C
A-SCID
hSNM1C
RS-SCID
DCLREC1C
RP11-398C13.5
protein artemis
PSO2 homolog
SNM1 homolog C
SNM1-like protein
DNA cross-link repair 1C protein
severe combined immunodeficiency, type a (Athabascan)
DNA cross-link repair 1C (PSO2 homolog, S. cerevisiae)
Art
Snm1l
AI661365
9930121L06Rik
RP23-167G19.6
mArt
artemis
DNA cross-link repair 1A, PSO2 homolog
OTTMUSP00000011552
OTTMUSP00000011551
OTTMUSP00000011550
OTTHUMP00000019174
OTTHUMP00000019172
OTTHUMP00000045150
RS-SCIDs
OTTHUMP00000019167
severe combined immunodeficiency, type a
SNM1-like
9930121L06
ARTEMISs
OTTHUMP00000019170
DCLRE1C
OTTHUMP00000019171
DNA cross-link repair 1C
FLJ11360
FLJ36438
MGC123409
OTTHUMP00000019166
OTTHUMP00000019168
Athabascan

Organism Homo sapiens
Mus musculus
Rattus norvegicus

OMIM ID 605988
603554
602450

Unigene ID Hs.656065
Mm.23483
Mm.442710
Rn.204346

KEGG ID hsa:64421
mmu:227525
rno:259171

Swiss-Prot Accession Q96SD1
B3KMX5
Q32MX8
Q8K4J0
Q5XIX3
A2AJG6
A2AJG7
A2AJG8
Q8BG72
Q8BTT1
D3DRT6
Q1HCL2
Q5JSR4
Q5JSR5
Q5JSR7
Q5JSR8
Q5JSR9
Q5JSS0
Q5JSS7
Q6PK14
Q8N101
Q8N132
Q8TBW9
Q9BVW9
Q9HAM4
Q8K4H7

EC Number 3.1.-.-

GO ID 0008409
0000014
0030183
0006310
0006302
0010212
0000723
0005634
0004519
0004527
0016787
0004518
0006281
0051276
0006974
0090305

Swiss-Prot ID DCR1C_MOUSE
DCR1C_HUMAN
DCR1C_RAT

Cell Localization Nucleus

IPI ID IPI00170222
IPI00221500
IPI00607937
IPI00290459
IPI00290918
IPI00396624
IPI00607742
IPI00209347

Mouse chromosome position 2

Rat chromosome position 17q12.3

Homologene ID 32547

MGI ID 2441769

RGD ID 708574

Primary Cell Localization Nucleus