Protein Enpp1

URN urn:agi-llid:5167
Connectivity 64
Name Enpp1
Description ectonucleotide pyrophosphatase/phosphodiesterase 1
Notes mutation of the human homolog is detected in patients with idiopathic infantile arterial calcification [RGD]

Pathway insulin signaling pathway
insulin signaling pathway
altered insulin signaling pathway
insulin signaling pathway

GO Molecular Function catalytic activity
nucleic acid binding
hydrolase activity
polysaccharide binding
protein homodimerization activity
insulin receptor binding
3'-phosphoadenosine 5'-phosphosulfate binding
ATP binding
metal ion binding
phosphodiesterase I activity
nucleotide diphosphatase activity
nucleoside-triphosphate diphosphatase activity
scavenger receptor activity

GO Cellular Component cell surface
membrane
extracellular space
plasma membrane
basolateral plasma membrane
integral to membrane

GO Biological Process metabolic process
immune response
negative regulation of ossification
regulation of bone mineralization
biomineral formation
negative regulation of fat cell differentiation
bone remodeling
negative regulation of cell growth
generation of precursor metabolites and energy
negative regulation of insulin receptor signaling pathway
negative regulation of glycogen biosynthetic process
negative regulation of protein amino acid autophosphorylation
phosphate metabolic process
3'-phosphoadenosine 5'-phosphosulfate metabolic process
nucleoside triphosphate catabolic process
cellular phosphate ion homeostasis
cellular response to insulin stimulus
negative regulation of glucose import
inorganic diphosphate transport
sequestering of triglyceride

Ariadne Ontology Glucose metabolism

Group Glucose metabolism
catalytic activity
metabolic process
immune response
negative regulation of ossification
regulation of bone mineralization
biomineral formation
negative regulation of fat cell differentiation
bone remodeling
negative regulation of cell growth
generation of precursor metabolites and energy
negative regulation of insulin receptor signaling pathway
negative regulation of glycogen biosynthetic process
negative regulation of protein amino acid autophosphorylation
phosphate metabolic process
3'-phosphoadenosine 5'-phosphosulfate metabolic process
nucleoside triphosphate catabolic process
cellular phosphate ion homeostasis
cellular response to insulin stimulus
negative regulation of glucose import
inorganic diphosphate transport
sequestering of triglyceride
nucleic acid binding
hydrolase activity
polysaccharide binding
protein homodimerization activity
insulin receptor binding
3'-phosphoadenosine 5'-phosphosulfate binding
ATP binding
metal ion binding
phosphodiesterase I activity
nucleotide diphosphatase activity
nucleoside-triphosphate diphosphatase activity
scavenger receptor activity
cell surface
membrane
extracellular space
plasma membrane
basolateral plasma membrane
integral to membrane

MedScan ID 5167

Hugo ID 3356

Human chromosome position 6q22-q23

LocusLink ID 5167
18605
85496
97628
615535
562399

Alias M6S1
NPP1
NPPS
PC-1
PCA1
ARHR2
PDNP1
ectonucleotide pyrophosphatase/phosphodiesterase family member 1
E-NPP 1
Ly-41 antigen
alkaline phosphodiesterase 1
plasma-cell membrane glycoprotein 1
plasma-cell membrane glycoprotein PC-1
membrane component chromosome 6 surface marker 1
phosphodiesterase I/nucleotide pyrophosphatase 1
membrane component, chromosome 6, surface marker 1
Pca
ttw
twy
Ly-41
Pca-1
C76301
CD203c
E-NPP1
AI428932
4833416E15Rik
tiptoe walking
OTTMUSP00000021307
lymphocyte antigen 41
1 ectonucleotide pyrophosphatase/phosphodiesterase 1
phosphodiesterase I/nucleotide pyrophosphatase 1; 1 ectonucleotide pyrophosphatase/phosphodiesterase 1
Pc1
1 ectonucleotide pyrophosphatase/phosphodiesterase I
4833416E15
alkaline phosphodiesterase I
ectonucleotide pyrophosphatase/phosphodiesterase 1
ectonucleotide pyrophosphatase/phosphodiesterase I
ENPP I
E-NPP I
ENPP1
homologous to Ly-41 antigen
LOC209552
M6S I
membrane component, chromosome 6, surface marker I
NPP I
nucleotide pyrophosphatase 1
nucleotide pyrophosphatase I
OTTHUMP00000043194
PCA I
PDNP I
phosphodiesterase I/nucleotide pyrophosphatase I
plasma-cell membrane glycoprotein
plasma-cell membrane glycoprotein I
Plasma-cell membrane glycoprotein PC I
Plasma-cell membrane glycoprotein PC-1
homologous to Ly-41 antigen
Plasma-cell membrane glycoprotein PC I
C76301s
E-NPP1s
E-NPP Is
PC I
PC(I)
PC-I
CH211-142E24.2
chromosome
ectonucleotide pyrophosphatase/phosphodiesterase-like
scaffold
si:ch211-142e24.2

Organism Homo sapiens
Mus musculus
Rattus norvegicus
Bos taurus
Danio rerio

GenBank ID NC_000006
NM_006208
NP_006199
NT_025741
NW_001838990
NW_923184
NG_008206
AC_000138
AC_000049
AB032016
BAA97562
AF067177
AAD38420
AF067178
AAD38421
AF110280
AAF36094
AF110281
AF110283
AF110284
AF110285
AF110286
AF110287
AF110288
AF110289
AF110290
AF110291
AF110292
AF110293
AF110294
AF110295
AF110296
AF110297
AF110298
AF110299
AF110300
AF110301
AF110302
AF110303
AF110304
AJ242020
CAC39442
AL117378
CAI19514
AL139805
CAI20161
CH471051
EAW48041
EAW48042
AK314870
BAG37385
BC033008
BC059375
AAH59375
BX537580
CAD97789
D12485
BAA02054
M57736
AAA63237
P22413
Q7Z3P5
Q9NS95
NC_000076
NM_008813
NP_032839
NT_039492
NW_001030413
AC_000032
AC099695
AC158616
CH466540
EDL04784
EDL04785
EDL04786
EDL04787
L04516
AF339910
AAK84174
AK014707
AK029600
AK035402
AK036952
AK041894
BAE43316
AK088857
BAC40616
AK145233
AK164619
BC050011
J02700
AAA39893
M12552
AAA39892
P06802
Q3V3C8
BC160371
AAI60371
NC_005100
NM_053535
NP_445987
NW_047548
NW_001084748
AC_000069
AC127189
CH474002
EDL87772
EDL87773
AB017596
BAA33393
AF320054
AAL26912
AF340185
AAK69653
AF340186
AAK69654
O88827
Q924C3
Q5T9R6
NW_000024
Q542E9
NT_086697
14270511
189650
219945
23503088
31873658
37748469
5052055
5052057
56203677
56204744
7106723
74719161
74750062
8918269
123781000
12484394
15099945
200235
23503085
26353972
74186817
81867645
81887522
Q924C4
14582806
14582808
16588834
23396766
3641684
81861549
NC_007307
NW_001495585
XM_867376
XP_872469
123887403
55962435
82078422
BX293547
CAI11601
NC_007131
NM_001030168
NP_001025339
NW_001512108
Q1JQ65
Q5RI82
119568426
119568427
133777224
148672837
148672838
148672839
148672840
149032917
149032918
71834481
126007383
71834482
562399
Dr.78641
ZDB-GENE-040724-172
dre:562399

OMIM ID 173335
208000
125853
613312
601665
602475

Mouse chromosome position 10 19.0 cM

GO ID 0050656
0005524
0016787
0005158
0046872
0003676
0047429
0004551
0004528
0030247
0042803
0005044
0050427
0031214
0046849
0030643
0032869
0006091
0006955
0030505
0008152
0030308
0045599
0046325
0045719
0046627
0030279
0031953
0009143
0006796
0030500
0030730
0016323
0009986
0005615
0016021
0005886
0003824
0016020
0005515
0001503
0003674
0008150
0005575
0004519
0032403
0016791
0009117
0007584
0001501

Rat chromosome position 1p12

Swiss-Prot Accession P22413
Q7Z3P5
Q9NS95
Q3V3C8
P06802
Q924C3
O88827
Q91XQ3
Q920C8
Q5T9R6
Q9NPZ3
Q9P1P6
Q9UP61
Q9Y6K3
Q542E9

PIR ID A39216

Unigene ID Hs.527295
Mm.478860
Rn.1199
Mm.477765
Mm.27254
Bt.60975
Dr.78641

KEGG ID hsa:5167
mmu:18605
rno:85496

EC Number 3.6.1.9
3.1.4.1

Swiss-Prot ID ENPP1_RAT
ENPP1_HUMAN
Q3V3C8_MOUSE

Cell Localization Membrane
Basolateral cell membrane
Cytoplasm
Plasma membrane

IPI ID IPI00339118
IPI00390328
IPI00184311
IPI00265291
IPI00478248
IPI00877960
IPI00128859

Homologene ID 38151

RGD ID 628825

MGI ID 97370
2143909

Microarray ID 104174_at

FunctionalClass endonuclease
hydrolase
nucleic acid binding
nucleotide diphosphatase
catalytic
phosphodiesterase I
metal ion binding
molecular_function

Mus musculus Chromosome position 10 19.0 cM
10

MedLine Reference 1315502
7830796
9662402
10389840
12121276
12837632
10453738
10524196
10615944
11159191
11739459
11771660
12126783
12147786
12147787
12441313
12477932
12483464
12547881
12715715
12881724
14671192
15001634
15126519
15374726
15677494
15793263
15802034
15834329
16186408
16272817
16278247
16527214
16607460
16936213
16968801
17065358
17065359
17143316
2211644
8040311
10024383
10349636
10725249
11027689
11042159
11076861
11217851
11856874
12082181
12466851
12533192
12817751
1351877
15039209
15075217
15096095
15625282
15833911
15920156
16141072
16141073
1647027
16680148
16813524
2943419
3001713
3076405
3104326
5033423
5419273
6292294
7344126
7678057
7736322
8055108
8474452
8507976
8750545
9359030
9392042
9457678
9541520
9685524
9840350
17046728
10480624
14574404
15072822
15489334
16865358
17129580
17287921
17493546
7737162
8001561
9344668
11598187
17552941
3917281
8223581
17187902

Source GO component

KEGG pathway Nicotinate and nicotinamide metabolism
Pantothenate and CoA biosynthesis
Purine metabolism
Riboflavin metabolism
Starch and sucrose metabolism

Homo sapiens Chromosome position 6q22-q23

Bos taurus Chromosome position 9

Rattus norvegicus Chromosome position 1p12