Protein Ercc4

URN urn:agi-llid:2072
Connectivity 12
Name Ercc4
Description excision repair cross-complementing rodent repair deficiency, complementation group 4
Notes The protein encoded by this gene forms a complex with ERCC1 and is involved in the 5' incision made during nucleotide excision repair. This complex is a structure specific DNA repair endonuclease that interacts with EME1. Defects in this gene are a cause of xeroderma pigmentosum complementation group F (XP-F), or xeroderma pigmentosum VI (XP6).

Pathway nucleotide excision repair pathway

GO Molecular Function nucleic acid binding
hydrolase activity
protein N-terminus binding
protein C-terminus binding
DNA binding
damaged DNA binding
structure-specific DNA binding
single-stranded DNA binding
magnesium ion binding
nuclease activity
endonuclease activity
endodeoxyribonuclease activity

GO Cellular Component chromosome, telomeric region
nucleoplasm
nucleotide-excision repair complex
nuclear chromosome, telomeric region
nucleus

GO Biological Process negative regulation of telomere maintenance
DNA metabolic process
nucleotide-excision repair, DNA incision
telomere maintenance
DNA repair
nucleotide-excision repair, DNA incision, 3'-to lesion
nucleotide-excision repair, DNA incision, 5'-to lesion
nucleotide-excision repair
nucleotide-excision repair, DNA damage removal
telomere maintenance via telomere shortening
double-strand break repair via homologous recombination
response to DNA damage stimulus
response to UV
UV protection

Ariadne Ontology DNA repair

Group DNA repair
negative regulation of telomere maintenance
DNA metabolic process
nucleotide-excision repair, DNA incision
telomere maintenance
DNA repair
nucleotide-excision repair, DNA incision, 3'-to lesion
nucleotide-excision repair, DNA incision, 5'-to lesion
nucleotide-excision repair
nucleotide-excision repair, DNA damage removal
telomere maintenance via telomere shortening
double-strand break repair via homologous recombination
response to DNA damage stimulus
response to UV
UV protection
nucleic acid binding
hydrolase activity
protein N-terminus binding
protein C-terminus binding
DNA binding
damaged DNA binding
structure-specific DNA binding
single-stranded DNA binding
magnesium ion binding
nuclease activity
endonuclease activity
endodeoxyribonuclease activity
chromosome, telomeric region
nucleoplasm
nucleotide-excision repair complex
nuclear chromosome, telomeric region
nucleus

MedScan ID 2072

Hugo ID 3436

Human chromosome position 16p13.12

LocusLink ID 2072
50505
304719

Alias XPF
RAD1
ERCC11
DNA repair endonuclease XPF
OTTHUMP00000045868
DNA excision repair protein ERCC-4
DNA repair protein complementing XP-F cells
xeroderma pigmentosum, complementation group F
xeroderma pigmentosum group F-complementing protein
excision-repair, complementing defective, in Chinese hamster
AI606920
OTTMUSP00000028967
OTTMUSP00000028969
DNA repair endonuclease subunit
RGD1560340
excision repair cross-complementing rodent repair deficiency, complementation group 4
DNA excision repair protein ERCC IV
DNA-repair protein complementing XP-F cell
Ercc4
LOC161866
LOC197172
LOC683847
Xeroderma pigmentosum group F complementing protein
xeroderma pigmentosum, complementing group F

Organism Homo sapiens
Mus musculus
Rattus norvegicus

GenBank ID NC_000016
NM_005236
NP_005227
NT_010393
NW_001838343
NW_926018
NG_011442
AC_000148
AC_000059
AC009173
AC010401
AF491814
AAL91593
CH471112
EAW85117
EAW85118
L76568
L77890
AAB50174
AI470593
AK289726
BAF82415
AK301930
BAG63350
AK308341
BC020741
AAH20741
BC142631
AAI42632
U64315
AAB07689
Q92889
BC160102
AAI60102
NC_000082
NM_015769
NP_056584
NT_039624
NT_039629
NW_001030584
AC_000038
AC004155
AAC03240
AC166826
CH466521
EDK97360
AF189285
AAF03157
AK018375
BAB31184
AK043366
AK081080
AK138588
BAE23706
AK149326
BAE28815
BC026792
AAH26792
BC051036
BQ559127
CD352377
CO433666
CX210668
Q3UEU6
Q3UUC1
Q9CXC7
Q9QZD4
NC_005109
XM_222534
XP_222534
NW_047332
AABR03074893
AABR03075152
AABR03075467

OMIM ID 133520
278760
610965

Mouse chromosome position 16

GO ID 0003684
0004520
0016787
0008022
0047485
0003697
0043566
0006281
0009650
0000724
0032205
0006289
0000718
0033683
0006295
0006296
0009411
0000723
0010834
0000781
0000784
0005654
0000109
0005634
0003677
0004519
0004518
0003676
0006259
0006974
0000287

Rat chromosome position 10q11

Swiss-Prot Accession Q92889
Q3UEU6
Q9QZD4
Q3UUC1
Q9CXC7
A8K111
O00140
Q8TD83
O54810
Q8R0I3

Unigene ID Hs.567265
Mm.287837

KEGG ID hsa:2072
mmu:50505
rno:304719

EC Number 3.1.-.-

Swiss-Prot ID XPF_HUMAN
XPF_MOUSE
Q3UEU6_MOUSE

Cell Localization Nucleus

IPI ID IPI00219179
IPI00137263
IPI00657932
IPI00461363
IPI00856677
IPI00857198
IPI00371802

Homologene ID 3836

RGD ID 1560340

MGI ID 1354163