Protein Ercc3

URN urn:agi-llid:2071
Connectivity 58
Name Ercc3
Description excision repair cross-complementing rodent repair deficiency, complementation group 3 (xeroderma pigmentosum group B complementing)
Notes ERCC3 is an ATP-dependent DNA helicase that functions in nucleotide excision repair and complements xeroderma pigmentosum group B mutations. It also is the 89 kDa subunit of basal transcription factor 2 (TFIIH) and thus functions in class II transcription. [provided by RefSeq]

Pathway nucleotide excision repair pathway

GO Molecular Function nucleotide binding
peptide binding
nucleic acid binding
hydrolase activity
protein N-terminus binding
transcription factor binding
protein C-terminus binding
DNA binding
ATP binding
dATP binding
GTP binding
damaged DNA binding
protein kinase activity
RNA polymerase II carboxy-terminal domain kinase activity
helicase activity
ATPase activity
DNA-dependent ATPase activity
ATP-dependent DNA helicase activity
3'-5' DNA helicase activity

GO Cellular Component nucleoplasm
holo TFIIH complex
nucleus
SSL2-core TFIIH complex

GO Biological Process interspecies interaction between organisms
hair cell differentiation
DNA topological change
cell cycle checkpoint
regulation of transcription
positive regulation of transcription from RNA polymerase II promoter
induction of apoptosis
ATP catabolic process
transcription
transcription from RNA polymerase II promoter
nucleotide-excision repair, DNA incision
DNA repair
RNA elongation from RNA polymerase II promoter
nucleotide-excision repair
nucleotide-excision repair, DNA damage removal
transcription-coupled nucleotide-excision repair
protein amino acid phosphorylation
nucleotide-excision repair, DNA duplex unwinding
response to DNA damage stimulus
response to oxidative stress
response to hypoxia
response to UV
UV protection
transcription initiation from RNA polymerase II promoter
protein localization

Ariadne Ontology Glucose metabolism
Polymerase II transcription
DNA repair

Group Glucose metabolism
Polymerase II transcription
DNA repair
interspecies interaction between organisms
hair cell differentiation
DNA topological change
cell cycle checkpoint
regulation of transcription
positive regulation of transcription from RNA polymerase II promoter
induction of apoptosis
ATP catabolic process
transcription
transcription from RNA polymerase II promoter
nucleotide-excision repair, DNA incision
DNA repair
RNA elongation from RNA polymerase II promoter
nucleotide-excision repair
nucleotide-excision repair, DNA damage removal
transcription-coupled nucleotide-excision repair
protein amino acid phosphorylation
nucleotide-excision repair, DNA duplex unwinding
response to DNA damage stimulus
response to oxidative stress
response to hypoxia
response to UV
UV protection
transcription initiation from RNA polymerase II promoter
protein localization
nucleotide binding
peptide binding
nucleic acid binding
hydrolase activity
protein N-terminus binding
transcription factor binding
protein C-terminus binding
DNA binding
ATP binding
dATP binding
GTP binding
damaged DNA binding
protein kinase activity
RNA polymerase II carboxy-terminal domain kinase activity
helicase activity
ATPase activity
DNA-dependent ATPase activity
ATP-dependent DNA helicase activity
3'-5' DNA helicase activity
nucleoplasm
holo TFIIH complex
nucleus
SSL2-core TFIIH complex

MedScan ID 2071

Hugo ID 3435

Human chromosome position 2q21

LocusLink ID 2071
13872
291703

Alias XPB
BTF2
GTF2H
RAD25
TFIIH
TFIIH basal transcription factor complex helicase XPB subunit
BTF2 p89
TFIIH p89
TFIIH 89 kDa subunit
DNA excision repair protein ERCC-3
DNA repair protein complementing XP-B cells
basic transcription factor 2 89 kDa subunit
xeroderma pigmentosum, complementation group B
xeroderma pigmentosum group B-complementing protein
TFIIH basal transcription factor complex 89 kDa subunit
Ercc-3
BTF2-p89
excision repair 3
OTTMUSP00000028389
MGC112916
Xpbc
complementation group 3
complementation group III
DNA excision repair protein ERCC III
DNA-repair protein complementing XP-B cells
Ercc3
excision repair cross-complementing rodent repair deficiency, complementation group 3
excision repair cross-complementing rodent repair deficiency, complementation group 3 (xeroderma pigmentosum group B complementing)
excision repair III
Excision-repair cross-complementing rodent repair deficiency
OTTHUMP00000162265
TFIIH-p89
Xeroderma pigmentosum group B complementing protein
xeroderma pigmentosum, complementing group B
XPB_HUMAN
XPBC/ERCC-3

Organism Homo sapiens
Mus musculus
Rattus norvegicus

GenBank ID NC_000002
NM_000122
NP_000113
NT_022135
NW_921507
NW_001838849
NG_007454
AC_000045
AC_000134
AC110926
AAY15069
AY163769
AAN46739
CH471103
EAW95311
EAW95312
EAW95313
EAW95314
AK091500
BAG52374
AK095557
BAG53083
AK127469
AK222465
BAD96185
AK290474
BAF83163
AK300250
BAG62016
AK307338
AK309405
BC008820
AAH08820
CR612390
M31899
AAA52396
P19447
Q53HW5
DQ893802
ABM84728
EU176179
ABW03630
NC_000084
NM_133658
NP_598419
NT_039674
NW_001030631
AC_000040
AC126686
CH466557
EDK97057
EDK97058
S71189
AK151188
AK152347
AK152988
AK154745
BAE32801
AK160187
BAE35681
BC016595
AAH16595
BC022956
BC024446
AAH24446
BC026575
AAH26575
S71186
AAB20614
P49135
Q3TVD8
Q3U3I5
Q8R1K9
NC_005117
NM_001031644
NP_001026814
NW_047510
NW_001084735
AC_000086
CH473974
EDL76187
BC098856
AAH98856
Q4G005

OMIM ID 133510
601675
610651

Mouse chromosome position 18

GO ID 0043138
0005524
0004003
0016887
0003677
0008094
0005525
0008353
0032564
0003684
0004386
0016787
0000166
0042277
0008022
0047485
0004672
0008134
0006281
0006265
0006368
0009650
0000075
0035315
0006917
0044419
0006289
0000718
0000717
0033683
0045944
0006468
0008104
0045449
0009411
0001666
0006979
0006366
0006367
0006283
0000441
0005675
0005654
0005634
0003676
0006200
0006974
0006350

Rat chromosome position 18p12

Swiss-Prot Accession P19447
Q53QM0
Q53HW5
P49135
Q3TVD8
Q3U3I5
Q8R1K9
Q4G005

PIR ID A48994
A35661

Unigene ID Hs.469872
Mm.282335
Rn.44012

KEGG ID hsa:2071
mmu:13872
rno:291703

EC Number 3.6.1.-

Swiss-Prot ID ERCC3_MOUSE
ERCC3_RAT
ERCC3_HUMAN
Q53QM0_HUMAN

Cell Localization Nucleus
Cytoplasm

IPI ID IPI00113070
IPI00363457
IPI00747053

Homologene ID 96

RGD ID 1307139

MGI ID 95414