Protein Sufu

URN urn:agi-llid:51684
Connectivity 33
Name Sufu
Description suppressor of fused homolog (Drosophila)
Notes The Hedgehog signaling pathway plays an important role in early human development. The pathway is a signaling cascade that plays a role in pattern formation and cellular proliferation during development. This gene encodes a negative regulator of the hedgehog signaling pathway. Defects in this gene are a cause of medulloblastoma. Alternative splicing results in multiple transcript variants.

Pathway Hedgehog signaling pathway

GO Molecular Function signal transducer activity
beta-catenin binding
transcription factor binding
transcription corepressor activity
specific transcriptional repressor activity

GO Cellular Component cilium
cytoplasm
nucleolus
nucleus

GO Biological Process multicellular organismal development
neural tube closure
spinal cord dorsal-ventral patterning
determination of left-right symmetry
skeletal system development
skin development
heart looping
signal transduction
negative regulation of smoothened signaling pathway
negative regulation of transcription from RNA polymerase II promoter
negative regulation of gene-specific transcription from RNA polymerase II promoter
regulation of transcription, DNA-dependent
cytoplasmic sequestering of transcription factor
proteolysis

Ariadne Ontology Transcription factors

Group Transcription factors
multicellular organismal development
neural tube closure
spinal cord dorsal-ventral patterning
determination of left-right symmetry
skeletal system development
skin development
heart looping
signal transduction
negative regulation of smoothened signaling pathway
negative regulation of transcription from RNA polymerase II promoter
negative regulation of gene-specific transcription from RNA polymerase II promoter
regulation of transcription, DNA-dependent
cytoplasmic sequestering of transcription factor
proteolysis
signal transducer activity
beta-catenin binding
transcription factor binding
transcription corepressor activity
specific transcriptional repressor activity
cilium
cytoplasm
nucleolus
nucleus

MedScan ID 51684

Hugo ID 16466

Human chromosome position 10q24.32

LocusLink ID 51684
24069
361769

Alias SUFUH
SUFUXL
PRO1280
RP11-47A8.1
suppressor of fused homolog
OTTHUMP00000020377
OTTHUMP00000020378
OTTHUMP00000020379
Su(fu)
2810026F04Rik
OTTMUSP00000039625
2810026F04
likely ortholog of mouse suppressor of fused homolog
likely ortholog of suppressor of fused homolog
LOC51684
OTTHUMP00000020374
OTTHUMP00000059161
Sufu
Suppressor of fused
suppressor of fused homolog (Drosophila)

Organism Homo sapiens
Mus musculus
Rattus norvegicus

GenBank ID NC_000010
NM_016169
NP_057253
NT_030059
NW_924884
NW_001838006
AC_000053
AC_000142
NM_001178133
AL121928
CAI12525
CAI12526
CAI12527
AL157386
CAI39611
CAI39612
CAI39614
CAI39615
AL391121
CAI40859
CAI40860
CAI40864
CAI40865
AY081829
AAM08947
CH471066
EAW49681
EAW49682
EAW49683
EAW49684
AF144231
AAF23890
AF159447
AAF23893
AF172319
AAD51655
AF175770
AAD50501
AF222345
AAF35866
AK307370
AK311503
AK312319
BAG35241
AL137465
CAB70752
AY358550
AAQ88914
BC013291
AAH13291
DA248208
Q5JSM0
Q5JSM1
Q9UMX1
DQ892586
ABM83512
DQ895804
ABM86730
NC_000085
NM_015752
NP_056567
NM_001025391
NP_001020562
NT_039687
NW_001030643
AC_000041
AC114539
AC156982
AJ308627
CAC34271
AJ308628
AJ308629
AJ308630
AJ308631
AJ308632
AJ308633
AJ308634
AJ308635
CAAA01041484
CH466534
EDL42000
EDL42001
EDL42002
AF134893
AAF61412
AJ131692
CAB38081
AJ308624
AJ308625
CAC34257
AJ308626
CAC34258
AJ308636
AK015885
BAB30017
AK016976
AK047603
BAC33095
AK156410
BAE33703
AK191814
AK196809
AK200545
AK200795
AK208852
AK215049
BC048168
AAH48168
BC056997
AAH56997
Q3U0Z8
Q9Z0P7
NC_005100
NM_001024899
NP_001020070
NW_047567
NW_001084775
AC_000069
AC096363
CH473986
EDL94350
BC097447
AAH97447
Q4V8C6

OMIM ID 607035
155255

Mouse chromosome position 19 47.0 cM

GO ID 0008013
0004871
0016566
0003714
0008134
0042994
0007368
0001947
0007275
0010553
0045879
0001843
0006508
0006355
0007165
0001501
0043588
0021513
0005929
0005737
0005730
0005634
0000122

Rat chromosome position 1q54

Swiss-Prot Accession Q9UMX1
Q5JSM0
Q5JSM1
Q9Z0P7
Q3U0Z8
Q4V8C6
Q8C8B4
Q99JG0
Q9D521
Q9JLU1
Q7LCP7
Q9NT90
Q9NZ07
Q9UHK2
Q9UHM8
Q9UMY0

PIR ID T46409

Unigene ID Hs.404089
Mm.41210
Rn.211670

KEGG ID hsa:51684
mmu:24069
rno:361769

Swiss-Prot ID SUFU_MOUSE
SUFU_HUMAN
Q4V8C6_RAT
Q3U0Z8_MOUSE

Cell Localization Cytoplasm
Nucleus

IPI ID IPI00124718
IPI00137696
IPI00466980
IPI00554964
IPI00099179
IPI00556458
IPI00556521
IPI00372535
IPI00643793
IPI00644765
IPI00643995
IPI00885402
IPI00203200

Homologene ID 9262

RGD ID 1559462

MGI ID 1345643