Protein HHAT

URN urn:agi-llid:55733
Connectivity 21
Name HHAT
Description hedgehog acyltransferase
Notes 'Skinny hedgehog' (SKI1) encodes an enzyme that acts within the secretory pathway to catalyze amino-terminal palmitoylation of 'hedgehog' (see MIM 600725).[supplied by OMIM]

Pathway Hedgehog signaling pathway

GO Molecular Function nucleotide binding
transferase activity
GTP binding
acyltransferase activity
palmitoyltransferase activity

GO Cellular Component membrane
endoplasmic reticulum membrane
endoplasmic reticulum
integral to membrane

GO Biological Process multicellular organismal development
protein palmitoylation
smoothened signaling pathway

Group multicellular organismal development
protein palmitoylation
smoothened signaling pathway
nucleotide binding
transferase activity
GTP binding
acyltransferase activity
palmitoyltransferase activity
membrane
endoplasmic reticulum membrane
endoplasmic reticulum
integral to membrane

MedScan ID 55733

Hugo ID 18270

Human chromosome position 1q32

LocusLink ID 55733
226861

Alias Skn
SKI1
MART2
FLJ10724
FLJ34867
protein-cysteine N-palmitoyltransferase HHAT
OTTHUMP00000034611
skinny hedgehog protein 1
melanoma antigen recognized by T cells 2
melanoma antigen recognized by T-cells 2
AI462858
MGC11697
2810432O22Rik
AC115917.1
OTTMUSP00000033669
skinny hedgehog protein
2810432O22
hedgehog acyltransferase
hhat
homolog of Drosophila skinny hedgehog,
melanoma antigen recognized by T cells II
OTTHUMP00000034608
SKI
skinny hedgehog, Drosophila, homolog of

Organism Homo sapiens
Mus musculus

GenBank ID NC_000001
NM_001122834
NP_001116306
NM_018194
NP_060664
NT_167186
NW_001838537
NW_926794
AC_000133
AC_000044
NM_001170564
NM_001170580
NM_001170587
NM_001170588
AC096636
AL034351
CAI23102
CAI23103
CAI23104
AL035414
CAI22284
AL590653
CAH70522
CAH70523
AL691441
CAI17038
CAI17039
BX255872
CH471100
EAW93426
EAW93427
EAW93428
EAW93429
EAW93430
AK001586
BAA91772
AK092186
BAG52495
AK295130
BAH11984
AK297193
BAH12521
AK298991
BAH12917
AK299200
BAH12967
AK302955
BAH13854
AK316190
BAH14561
AK316524
BAH14895
AL049848
CAB42852
BC039071
AAH39071
BC051191
BC117130
AAI17131
CR936628
CAI56771
DA336461
DB077466
DB080645
Q05BM0
Q5VTY9
NC_000067
NM_144881
NP_659130
NT_039190
NW_001030678
AC_000023
AC105325
AC115917
AL365317
CAO82114
CAO82115
CAO82116
CAO82117
CH466555
EDL12965
EDL12966
AK028230
BAC25829
AK052669
BAC35090
AK134661
AK163268
BAE37267
AK172126
BAE42837
BC008159
AAH08159
BY087228
Q3TQW5
Q8BMT9
Q8BWF5

OMIM ID 605743

Mouse chromosome position 1

GO ID 0005525
0008415
0000166
0016740
0007275
0005783
0005789
0016021
0016020
0016409
0018345
0007224

Swiss-Prot Accession Q05BM0
Q5VTY9
Q8BMT9
Q3TQW5
Q8BWF5
Q17RZ7
Q4G0K3
Q5CZ95
Q5TGI2
Q9NVH9
Q9Y3N8
B1ANS0
Q3TA33
Q922G3
B7Z4D5
B7Z868
B7Z5I1
D3DT91
B7Z5N1

Unigene ID Hs.58650
Mm.145857

KEGG ID hsa:55733
mmu:226861

EC Number 2.3.1.-

Swiss-Prot ID HHAT_HUMAN
HHAT_MOUSE
B7Z4D5_HUMAN
B7Z868_HUMAN
B7Z5I1_HUMAN
D3DT91_HUMAN
B7Z5N1_HUMAN
B1ANS0_MOUSE

Cell Localization Endoplasmic reticulum membrane

IPI ID IPI00018902
IPI00163890
IPI00657747
IPI00923457
IPI00223115
IPI00670095
IPI00922056
IPI00554791
IPI00653855
IPI00473977
IPI00856718
IPI00856955

Homologene ID 41232

RGD ID 1351064

MGI ID 2444681