Protein Hmgcs2

URN urn:agi-llid:3158
Connectivity 18
Name Hmgcs2
Description 3-hydroxy-3-methylglutaryl-Coenzyme A synthase 2 (mitochondrial)
Notes HMG-CoA cycle enzyme that catalyzes a step in ketone-body biosynthesis [RGD]

Pathway ketone bodies metabolic pathway

Ariadne Ontology Branced aminoacid metabolism

GO Molecular Function transferase activity
hydroxymethylglutaryl-CoA synthase activity

GO Cellular Component mitochondrion
mitochondrial matrix
mitochondrial inner membrane

GO Biological Process metabolic process
sterol biosynthetic process
cholesterol biosynthetic process
ketone body biosynthetic process
steroid biosynthetic process
isoprenoid biosynthetic process
lipid biosynthetic process
response to drug
response to nutrient
response to peptide hormone stimulus

Group Branced aminoacid metabolism
mitochondrion
mitochondrial matrix
mitochondrial inner membrane
transferase activity
hydroxymethylglutaryl-CoA synthase activity
metabolic process
sterol biosynthetic process
cholesterol biosynthetic process
ketone body biosynthetic process
steroid biosynthetic process
isoprenoid biosynthetic process
lipid biosynthetic process
response to drug
response to nutrient
response to peptide hormone stimulus

Hugo ID 5008

Human chromosome position 1p13-p12

GenBank ID NC_000001
NM_005518
NP_005509
NT_019273
NW_001838594
NW_922462
AC_000133
AC_000044
AL589734
CAI22408
CH471122
EAW56709
EAW56710
U81859
AAB72036
AK301594
BAH13520
AK302276
BAH13664
AK303777
BAH14049
AK313590
BC044217
AAH44217
BF964973
CR456850
CAG33131
CR618114
U12788
AAA92673
U12789
AAA92674
X83618
CAA58593
P54868
Q5SZU2
Q6IBF4
NC_000069
NM_008256
NP_032282
NT_039240
NW_001030728
AC_000025
AC121771
AC147476
CH466620
EDL38955
EDL38956
EDL38957
EDL38958
U12790
AAA92675
U12791
AAA92676
AK004865
BAB23626
AK004902
BAB23657
AK098104
BAC05233
BC014714
AAH14714
BC024744
AAH24744
P54869
Q8N7N8
NC_005101
NM_173094
NP_775117
NW_001084807
NW_047627
AC_000070
CH474015
EDL85567
EDL85568
M63800
BC078695
AAH78695
BC083543
AAH83543
M33648
AAA41336
P22791
Q68G44

LocusLink ID 3158
15360
24450

Alias hydroxymethylglutaryl-CoA synthase 2
OTTHUMP00000013928
mHS
1300002P16
Hmgcs1
Mt3h3mg
3-hydroxy-3-methylglutary-Coenzyme A synthase 2
mitochondrial 3-hydroxy-3-methylglutaryl-Coenzyme A synthase 2
3-hydroxy-3-methylglutary-Coenzyme A synthase II
Hmgcs2
HMG-CoA synthase II
3-hydroxy-3-methylglutary-Coenzyme A synthase
3-hydroxy-3-methylglutaryl-Coenzyme A synthase 2
3-hydroxy-3-methylglutaryl-Coenzyme A synthase 2 (mitochondrial)
HMG-CoA synthase 2
Hydroxymethylglutaryl-CoA synthase, mitochondrial precursor
3-hydroxy-3-methylglutaryl-Coenzyme A synthase II
Hydroxymethylglutaryl-CoA synthase II
mitochondrial 3-hydroxy-3-methylglutaryl-Coenzyme A synthase II
Hmgcs2s

Organism Homo sapiens
Mus musculus
Rattus norvegicus

OMIM ID 600234
605911

Swiss-Prot Accession P54868
Q5SZU2
Q6IBF4
P54869
Q8N7N8
P22791
Q68G44

Unigene ID Hs.59889
Mm.289131
Rn.29594

KEGG ID hsa:3158
mmu:15360
rno:24450

EC Number 4.1.3.5
2.3.3.10

Swiss-Prot ID HMCS2_HUMAN
HMCS2_MOUSE
HMCS2_RAT
Q5SZU2_HUMAN

Cell Localization Cytoplasm

GO ID 0004421
0016740
0006695
0008299
0008152
0042493
0007584
0043434
0005743
0005759
0005739
0008610
0006694
0016126
0046951

IPI ID IPI00008934
IPI00420718
IPI00210444

Mouse chromosome position 3 48.0 cM

Homologene ID 38066

MGI ID 101939

Rat chromosome position 2q34

RGD ID 2804