Protein Pklr

URN urn:agi-llid:5313
Connectivity 77
Name Pklr
Description pyruvate kinase, liver and RBC
Notes The protein encoded by this gene is a pyruvate kinase that catalyzes the production of phohsphoenolpyruvate from pyruvate and ATP. Defects in this enzyme, due to gene mutations or genetic variations, are the common cause of chronic hereditary nonspherocytic hemolytic anemia (CNSHA or HNSHA). Alternatively spliced transcript variants encoding distinct isoforms have been described.

Pathway pyruvate metabolic pathway
New Pathway
glycolysis/gluconeogenesis pathway
glycolysis pathway
pyruvate metabolic pathway

GO Molecular Function catalytic activity
nucleotide binding
transferase activity
ATP binding
metal ion binding
magnesium ion binding
potassium ion binding
kinase activity
pyruvate kinase activity

GO Cellular Component soluble fraction
cytosol

GO Biological Process response to other organism
glycolysis
ATP biosynthetic process
pyruvate biosynthetic process
cellular response to insulin stimulus
response to nutrient
response to hypoxia
response to heat
response to metal ion
response to organic cyclic substance
response to cAMP
response to ATP
response to lithium ion
response to glucose stimulus
carbohydrate metabolic process

Ariadne Ontology Glucose metabolism
Purine metabolism

Group Glucose metabolism
Purine metabolism
catalytic activity
response to other organism
glycolysis
ATP biosynthetic process
pyruvate biosynthetic process
cellular response to insulin stimulus
response to nutrient
response to hypoxia
response to heat
response to metal ion
response to organic cyclic substance
response to cAMP
response to ATP
response to lithium ion
response to glucose stimulus
carbohydrate metabolic process
nucleotide binding
transferase activity
ATP binding
metal ion binding
magnesium ion binding
potassium ion binding
kinase activity
pyruvate kinase activity
soluble fraction
cytosol

MedScan ID 5313

Hugo ID 9020

Human chromosome position 1q21

LocusLink ID 5313
18770
24651

Alias PK1
PKL
PKR
RPK
PKRL
pyruvate kinase isozymes R/L
pyruvate kinase 1
OTTHUMP00000034069
pyruvate kinase type L
pyruvate kinase isozyme R/L
R-type/L-type pyruvate kinase
red cell/liver pyruvate kinase
pyruvate kinase, liver and blood cell
Pk-1
R-PK
L-PK
OTTMUSP00000019089
Pklg
pyruvate kinase, liver and red blood cell
L-type pyruvate kinase
PKLR
pyruvate kinase I
pyruvate kinase isozyme L
pyruvate kinase isozyme R
pyruvate kinase liver and red blood cell
pyruvate kinase type R
Pyruvate kinase, isozymes R/L
pyruvate kinase, liver and RBC
R-type pyruvate kinase
R-type/L-type pyruvate kinase
PK I
pyruvate kinase, liver and RBC type
liver and rbc
liver and red blood cell

Organism Homo sapiens
Mus musculus
Rattus norvegicus

GenBank ID NC_000001
NM_000298
NP_000289
NM_181871
NP_870986
NT_004487
NW_001838531
NW_925683
NG_011677
AC_000133
AC_000044
AL353760
AL713999
CAI95101
CAI95102
AY316591
AAP69527
CH471121
EAW53079
EAW53080
D13243
BAA02515
S59798
S59799
S59800
S59801
S59803
S59804
S59806
S59807
S59809
S59810
S59811
S59812
S59813
S59814
S59815
S59817
S59819
S59820
S59821
S59822
S59823
S59829
S59832
U47654
AAA92535
AAA92536
Z18922
AB015983
BAA31706
AK225947
AK298399
BAG60632
BC025737
AAH25737
BF110802
M15465
AAA60104
S60712
AAB26262
O75758
P30613
Q16715
Q16716
EU176228
ABW03679
NC_000069
NM_013631
NP_038659
NT_039240
NW_001030721
AC_000025
NM_001099779
AC161600
CH466547
EDL15236
AK149508
BAE28927
AK149524
BAE28937
BC152327
AAI52328
BC152542
BY107231
BY781095
D63764
BAA23642
S79731
AAB35435
P53657
Q3UEH4
Q3UEI4
BC160353
AAI60353
NC_005101
NM_012624
NP_036756
NW_047626
NW_001084805
AC_000070
CH473976
EDM00668
M17091
AAA41883
X05684
CAA29169
BC161827
AAI61827
M11709
AAA41880
P12928
Q4VX10
Q4VX11

OMIM ID 609712
102900
266200

Mouse chromosome position 3 44.0 cM

GO ID 0005524
0000287
0000166
0030955
0004743
0016740
0006096
0003824
0016301
0046872
0006754
0005975
0032869
0042866
0033198
0051591
0009408
0010226
0051707
0005829
0005625
0009749
0001666
0010038
0007584
0014070
0005575

Rat chromosome position 2q34

Swiss-Prot Accession P30613
O75758
Q16715
Q16716
Q3UEH4
Q3UEI4
P53657
B1WBN9
P12928
P04763
Q64618
P11973

PIR ID A27427
A92940
I52269

Unigene ID Hs.95990
Mm.383180
Rn.48821

KEGG ID hsa:5313
mmu:18770
rno:24651

EC Number 2.7.1.40

Swiss-Prot ID KPYR_RAT
KPYR_HUMAN
B1WBN9_RAT
Q3UEI4_MOUSE
Q3UEH4_MOUSE

Cell Localization Cytoplasm

IPI ID IPI00202549
IPI00231683
IPI00027165
IPI00941093
IPI00775829
IPI00133605
IPI00743713
IPI00871353
IPI00776364

Homologene ID 37286

RGD ID 3336

MGI ID 97604