Protein Mdh2

URN urn:agi-llid:4191
Connectivity 34
Name Mdh2
Description malate dehydrogenase 2, NAD (mitochondrial)
Notes Malate dehydrogenase catalyzes the reversible oxidation of malate to oxaloacetate, utilizing the NAD/NADH cofactor system in the citric acid cycle. The protein encoded by this gene is localized to the mitochondria and may play pivotal roles in the malate-aspartate shuttle that operates in the metabolic coordination between cytosol and mitochondria.

Pathway citrate cycle pathway
citric acid cycle pathway

GO Molecular Function catalytic activity
oxidoreductase activity
protein self-association
oxidoreductase activity, acting on the CH-OH group of donors, NAD or NADP as acceptor
malate dehydrogenase activity
malate dehydrogenase (NADP+) activity
L-malate dehydrogenase activity

GO Cellular Component mitochondrion
mitochondrial inner membrane
mitochondrial matrix

GO Biological Process metabolic process
oxidation reduction
cellular carbohydrate metabolic process
glycolysis
oxaloacetate metabolic process
malate metabolic process
NADH metabolic process
tricarboxylic acid cycle
carbohydrate metabolic process

Ariadne Ontology Tricarboxylic acid cycle

Group Tricarboxylic acid cycle
catalytic activity
metabolic process
oxidation reduction
cellular carbohydrate metabolic process
glycolysis
oxaloacetate metabolic process
malate metabolic process
NADH metabolic process
tricarboxylic acid cycle
carbohydrate metabolic process
oxidoreductase activity
protein self-association
oxidoreductase activity, acting on the CH-OH group of donors, NAD or NADP as acceptor
malate dehydrogenase activity
malate dehydrogenase (NADP+) activity
L-malate dehydrogenase activity
mitochondrion
mitochondrial inner membrane
mitochondrial matrix

MedScan ID 4191

Hugo ID 6971

Human chromosome position 7cen-q22

LocusLink ID 4191
17448
81829

Alias MDH
MOR1
M-MDH
MGC:3559
malate dehydrogenase, mitochondrial
OTTHUMP00000210118
Mdh-2
Mor-1
OTTMUSP00000026139
mitochondrial malate dehydrogenase 2, NAD
malate dehydrogenase 2
malate dehydrogenase 2, NAD (mitochondrial)
malate dehydrogenase II
MDH2
mitochondrial Malate dehydrogenase
mitochondrial malate dehydrogenase 2
mitochondrial similar to Malate dehydrogenase
mitochondrial similar to Malate dehydrogenase precursor

Organism Homo sapiens
Mus musculus
Rattus norvegicus

GenBank ID NC_000007
NM_005918
NP_005909
NT_007933
NT_079595
NW_001839047
NW_923484
AC_000068
AC_000139
AC_000050
AC005077
AAS07425
AC006330
AAS07534
CH471220
EAW71796
EAW71797
EAW71798
AF047470
AAC03787
AK095803
BAG53133
AK290779
BAF83468
AK293460
BAG56955
AK316587
BAG38175
BC001917
AAH01917
CR536548
CAG38785
CR590302
CR591002
CR591867
CR592414
CR592770
CR593897
CR594479
CR595903
CR599784
CR600726
CR602693
CR603586
CR604994
CR608858
CR609305
CR609833
CR611271
CR613026
CR614342
CR615128
CR615222
CR615946
CR618110
CR619490
CR622625
CR624429
CR625644
CR626170
DQ402957
ABD77290
P40926
Q0QF37
Q6FHZ0
Q75MP7
Q75MT9
DQ893080
ABM84006
DQ896341
ABM87340
NC_000071
NM_008617
NP_032643
NT_039314
NW_001030796
AC_000027
AC083948
CH466529
EDL19349
EDL19350
EDL19351
X07295
CAA30274
X07296
X07297
X07298
X07299
X07300
X07301
AK002305
BAC24986
AK135162
BAE22447
AK160553
BAE35869
AK167809
BAE39836
AK204746
BC023482
AAH23482
DQ402950
ABD77283
M16229
AAA39509
P08249
NC_005111
NM_031151
NP_112413
NW_047370
NW_001084677
AC_000080
CH473973
EDM13347
EDM13348
EDM13349
EDM13350
EDM13351
EDM13352
BC063165
AAH63165
DQ402951
ABD77284
X04240
CAA27812
P04636
Q0QF43

OMIM ID 154100

Mouse chromosome position 5 78.0 cM

GO ID 0030060
0046554
0016491
0043621
0006734
0044262
0006096
0006108
0006107
0055114
0006099
0005743
0005759
0005739
0003824
0016615
0016616
0005975
0008152
0005488
0005515

Rat chromosome position 12q12

Swiss-Prot Accession P40926
Q0QF37
Q6FHZ0
Q75MP7
Q75MT9
P08249
P04636
Q0QF43
A8K414
B2RE78
O43682
Q0QF44
Q8CF79
Q8R1P0
Q6GSM4

PIR ID S01350
A25509

Unigene ID Hs.520967
Mm.297096
Rn.1011

KEGG ID hsa:4191
mmu:17448
rno:81829

EC Number 1.1.1.37

Swiss-Prot ID MDHM_HUMAN
MDHM_MOUSE
MDHM_RAT

Cell Localization Mitochondrion matrix
Mitochondria

IPI ID IPI00291006
IPI00323592
IPI00197696

Homologene ID 55938

RGD ID 619719

MGI ID 97050