ATED WITH abnormal coat/hair pigmentation; abnormal platelet dense granule number; abnormal surfactant secretion; ASSOCIATED WITH Albuminuria; Hermansky-Pudlak syndrome; proteinuria; FOUND IN cell body; melanosome; perinuclear region of cytoplasm; INTERACTS WITH 1-[(4-chlorophenyl)-phenylmethyl]-4-methylpiperazine; 2,3,7,8-tetrachlorodibenzodioxine; 2,4-dinitrotoluene