almitoyltransferase I deficiency pathway; ethylmalonic encephalopathy pathway; ASSOCIATED WITH congenital dyserythropoietic anemia type IVa (ortholog); genetic disease (ortholog); glutaric acidemia I (ortholog); FOUND IN mitochondrion (ortholog); INTERACTS WITH (+)-schisandrin B; 17beta-estradiol; 2,3,7,8-tetrachlorodibenzodioxine