ONTOLOGY REPORT - ANNOTATIONS
Term: metabolic pathway of other amino acids
Accession: PW:0000132
browse the term
Definition: Those metabolic reactions involved in the synthesis, utilization and/or degradation of amino acids other than the common 20 amino acids found in protein. Some of these amino acids like carnitine or homocysteine derive from primary amino acids.
beta-alanine metabolic pathway
G
Abat
4-aminobutyrate aminotransferase
IEA
10
7,040,725
7,137,154
RGD:6907045
KEGG
G
Acadm
acyl-CoA dehydrogenase, C-4 to C-12 straight chain
IEA
2
251,866,645
251,890,729
RGD:6907045
KEGG
G
Aldh1a1
aldehyde dehydrogenase 1 family, member A1
IEA
1
223,731,675
223,773,285
RGD:6907045
KEGG
G
Aldh1a3
aldehyde dehydrogenase 1 family, member A3
IEA
1
120,847,746
120,881,883
RGD:6907045
KEGG
G
Aldh1a7
aldehyde dehydrogenase family 1, subfamily A7
IEA
1
223,822,536
223,875,238
RGD:6907045
KEGG
G
Aldh1b1
aldehyde dehydrogenase 1 family, member B1
IEA
5
62,311,268
62,316,276
RGD:6907045
KEGG
G
Aldh2
aldehyde dehydrogenase 2 family (mitochondrial)
IEA
12
36,081,778
36,116,445
RGD:6907045
KEGG
G
Aldh3a1
aldehyde dehydrogenase 3 family, member A1
IEA
10
47,365,195
47,374,880
RGD:6907045
KEGG
G
Aldh3a2
aldehyde dehydrogenase 3 family, member A2
IEA
10
47,400,518
47,421,064
RGD:6907045
KEGG
G
Aldh3b1
aldehyde dehydrogenase 3 family, member B1
IEA
1
206,438,325
206,455,477
RGD:6907045
KEGG
G
Aldh7a1
aldehyde dehydrogenase 7 family, member A1
IEA
18
52,300,899
52,333,149
RGD:6907045
KEGG
G
Aldh9a1
aldehyde dehydrogenase 9 family, member A1
IEA
13
83,017,312
83,034,047
RGD:6907045
KEGG
G
Aoc3
amine oxidase, copper containing 3
IEA
10
90,357,094
90,365,040
RGD:6907045
KEGG
G
Cndp1
carnosine dipeptidase 1 (metallopeptidase M20 family)
IEA
18
81,160,681
81,183,558
RGD:6907045
KEGG
G
Dpyd
dihydropyrimidine dehydrogenase
IEA
2
214,931,901
215,818,809
RGD:6907045
KEGG
G
Dpys
dihydropyrimidinase
IEA
7
75,368,238
75,446,160
RGD:6907045
KEGG
G
Echs1
enoyl CoA hydratase, short chain, 1, mitochondrial
IEA
1
199,901,585
199,910,412
RGD:6907045
KEGG
G
Ehhadh
enoyl-CoA, hydratase/3-hydroxyacyl CoA dehydrogenase
IEA
11
81,474,161
81,507,645
RGD:6907045
KEGG
G
Gad1
glutamate decarboxylase 1
IEA
3
52,789,370
52,830,038
RGD:6907045
KEGG
G
Gad2
glutamate decarboxylase 2
IEA
17
96,259,430
96,321,857
RGD:6907045
KEGG
G
Hadha
hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), alpha subunit
IEA
6
26,173,798
26,191,433
RGD:6907045
KEGG
G
Hibch
3-hydroxyisobutyryl-CoA hydrolase
IEA
9
45,564,702
45,645,252
RGD:6907045
KEGG
G
Mlycd
malonyl-CoA decarboxylase
IEA
19
49,637,193
49,653,016
RGD:6907045
KEGG
G
Srm
spermidine synthase
IEA
5
165,672,516
165,675,673
RGD:6907045
KEGG
G
Upb1
ureidopropionase, beta
IEA
20
13,715,995
13,743,261
RGD:6907045
KEGG
creatine metabolic pathway
G
Ckm
creatine kinase, muscle
IDA
1
78,762,202
78,772,681
RGD:1359082
RGD
G
Gamt
guanidinoacetate N-methyltransferase
IDA
7
10,959,990
10,962,720
RGD:1359082
RGD
G
Gatm
glycine amidinotransferase (L-arginine:glycine amidinotransferase)
TAS
3
109,558,043
109,565,432
RGD:70746
RGD
G
Slc6a8
solute carrier family 6 (neurotransmitter transporter, creatine), member 8
IDA
X
159,570,789
159,580,093
RGD:1359082
RGD
cyanoamino acid metabolic pathway
G
Gba3
glucosidase, beta, acid 3 (cytosolic)
IEA
14
65,467,770
65,550,278
RGD:6907045
KEGG
G
Ggt1
gamma-glutamyltransferase 1
IEA
RGD:6907045
KEGG
G
Ggt5
gamma-glutamyltransferase 5
IEA
RGD:6907045
KEGG
G
Ggt6
gamma-glutamyl transferase 6
IEA
10
59,320,455
59,322,932
RGD:6907045
KEGG
G
Ggt7
gamma-glutamyltransferase 7
IEA
3
145,987,531
146,010,922
RGD:6907045
KEGG
G
Shmt1
serine hydroxymethyltransferase 1 (soluble)
IEA
10
46,936,605
46,964,779
RGD:6907045
KEGG
G
Shmt2
serine hydroxymethyltransferase 2 (mitochondrial)
IEA
7
67,494,470
67,499,540
RGD:6907045
KEGG
D-arginine and D-ornithine metabolic pathway
G
Dao
D-amino-acid oxidase
IEA
12
43,627,593
43,648,332
RGD:6907045
KEGG
D-glutamine and D-glutamate metabolic pathway
G
Gls
glutaminase
IEA
9
46,380,165
46,452,974
RGD:6907045
KEGG
G
Gls2
glutaminase 2 (liver, mitochondrial)
IEA
7
1,484,397
1,495,283
RGD:6907045
KEGG
G
Glud1
glutamate dehydrogenase 1
IEA
16
9,965,718
9,999,254
RGD:6907045
KEGG
glutathione metabolic pathway
G
Anpep
alanyl (membrane) aminopeptidase
IEA
1
135,600,751
135,619,208
RGD:6907045
KEGG
G
G6pd
glucose-6-phosphate dehydrogenase
IEA
X
160,186,450
160,192,316
RGD:6907045
KEGG
G
Gclc
glutamate-cysteine ligase, catalytic subunit
IEA
8
82,724,429
82,762,848
RGD:6907045
KEGG
G
Gclc
glutamate-cysteine ligase, catalytic subunit
IMP
8
82,724,429
82,762,848
RGD:1582661
RGD
G
Gclc
glutamate-cysteine ligase, catalytic subunit
IDA
8
82,724,429
82,762,848
RGD:1582663
RGD
G
Gclm
glutamate cysteine ligase, modifier subunit
IEA
2
218,895,434
218,915,491
RGD:6907045
KEGG
G
Gclm
glutamate cysteine ligase, modifier subunit
IMP
2
218,895,434
218,915,491
RGD:1582661
RGD
G
Gclm
glutamate cysteine ligase, modifier subunit
IDA
2
218,895,434
218,915,491
RGD:1582663
RGD
G
Ggct
gamma-glutamyl cyclotransferase
IEA
4
83,459,924
83,467,120
RGD:6907045
KEGG
G
Ggt1
gamma-glutamyltransferase 1
IEA
RGD:6907045
KEGG
G
Ggt5
gamma-glutamyltransferase 5
IEA
RGD:6907045
KEGG
G
Ggt6
gamma-glutamyl transferase 6
IEA
10
59,320,455
59,322,932
RGD:6907045
KEGG
G
Ggt7
gamma-glutamyltransferase 7
IEA
3
145,987,531
146,010,922
RGD:6907045
KEGG
G
Gpx1
glutathione peroxidase 1
IEA
RGD:6907045
KEGG
G
Gpx2
glutathione peroxidase 2
IEA
6
99,372,418
99,376,230
RGD:6907045
KEGG
G
Gpx3
glutathione peroxidase 3
IEA
10
40,311,094
40,319,382
RGD:6907045
KEGG
G
Gpx4
glutathione peroxidase 4
IEA
7
11,162,521
11,165,318
RGD:6907045
KEGG
G
Gpx5
glutathione peroxidase 5
IEA
RGD:6907045
KEGG
G
Gpx6
glutathione peroxidase 6
IEA
17
51,063,379
51,068,058
RGD:6907045
KEGG
G
Gpx7
glutathione peroxidase 7
IEA
5
129,506,986
129,514,830
RGD:6907045
KEGG
G
Gpx8
glutathione peroxidase 8
IEA
2
44,424,009
44,427,603
RGD:6907045
KEGG
G
Gsr
glutathione reductase
IEA
16
62,255,562
62,298,458
RGD:6907045
KEGG
G
Gss
glutathione synthetase
IEA
3
146,057,517
146,087,820
RGD:6907045
KEGG
G
Gsta2
glutathione S-transferase alpha 2
IEA
8
83,299,249
83,312,958
RGD:6907045
KEGG
G
Gsta3
glutathione S-transferase alpha 3
IEA
9
20,005,570
20,032,031
RGD:6907045
KEGG
G
Gsta4
glutathione S-transferase alpha 4
IEA
8
83,165,139
83,183,055
RGD:6907045
KEGG
G
Gsta5
glutathione S-transferase alpha 5
IEA
8
83,202,554
83,211,997
RGD:6907045
KEGG
G
Gstk1
glutathione S-transferase kappa 1
IEA
4
69,999,767
70,004,086
RGD:6907045
KEGG
G
Gstm1
glutathione S-transferase mu 1
IEA
2
203,575,444
203,580,821
RGD:6907045
KEGG
G
Gstm2
glutathione S-transferase mu 2
IEA
2
203,549,022
203,553,380
RGD:6907045
KEGG
G
Gstm3
glutathione S-transferase mu 3
IEA
2
203,532,363
203,537,135
RGD:6907045
KEGG
G
Gstm4
glutathione S-transferase mu 4
IEA
2
203,605,593
203,610,817
RGD:6907045
KEGG
G
Gstm5
glutathione S-transferase, mu 5
IEA
2
203,456,122
203,458,917
RGD:6907045
KEGG
G
Gstm6
glutathione S-transferase, mu 6
IEA
2
203,504,228
203,509,002
RGD:6907045
KEGG
G
Gstm7
glutathione S-transferase, mu 7
IEA
2
203,491,366
203,496,812
RGD:6907045
KEGG
G
Gsto1
glutathione S-transferase omega 1
IEA
1
253,228,547
253,238,531
RGD:6907045
KEGG
G
Gsto2
glutathione S-transferase omega 2
IEA
1
253,239,392
253,275,110
RGD:6907045
KEGG
G
Gstp1
glutathione S-transferase pi 1
IEA
1
206,627,398
206,629,866
RGD:6907045
KEGG
G
Gstt1
glutathione S-transferase theta 1
IEA
20
13,604,355
13,621,456
RGD:6907045
KEGG
G
Gstt2
glutathione S-transferase, theta 2
IEA
20
13,221,696
13,225,367
RGD:6907045
KEGG
G
Gstz1
glutathione S-transferase zeta 1
IEA
RGD:6907045
KEGG
G
Idh1
isocitrate dehydrogenase 1 (NADP+), soluble
IEA
9
63,769,401
63,790,622
RGD:6907045
KEGG
G
Idh2
isocitrate dehydrogenase 2 (NADP+), mitochondrial
IEA
1
135,876,052
135,895,373
RGD:6907045
KEGG
G
Lap3
leucine aminopeptidase 3
IEA
14
70,680,077
70,699,061
RGD:6907045
KEGG
G
Mgst1
microsomal glutathione S-transferase 1
IEA
4
175,248,654
175,263,881
RGD:6907045
KEGG
G
Mgst2
microsomal glutathione S-transferase 2
IEA
2
140,546,939
140,568,616
RGD:6907045
KEGG
G
Mgst3
microsomal glutathione S-transferase 3
IEA
13
83,038,049
83,058,802
RGD:6907045
KEGG
G
Odc1
ornithine decarboxylase 1
IEA
6
41,309,211
41,315,796
RGD:6907045
KEGG
G
Oplah
5-oxoprolinase (ATP-hydrolysing)
IEA
7
114,326,739
114,341,949
RGD:6907045
KEGG
G
RGD1562107
similar to class-alpha glutathione S-transferase
IEA
9
19,965,797
19,978,363
RGD:6907045
KEGG
G
Rrm1
ribonucleotide reductase M1
IEA
1
159,930,994
159,937,860
RGD:6907045
KEGG
G
Rrm2
ribonucleotide reductase M2
IEA
6
42,350,541
42,356,748
RGD:6907045
KEGG
G
Rrm2b
ribonucleotide reductase M2 B (TP53 inducible)
IEA
7
73,432,161
73,459,541
RGD:6907045
KEGG
G
Srm
spermidine synthase
IEA
5
165,672,516
165,675,673
RGD:6907045
KEGG
G
Txndc12
thioredoxin domain containing 12 (endoplasmic reticulum)
IEA
5
130,142,600
130,167,629
RGD:6907045
KEGG
homocysteine metabolic pathway
G
Ahcy
adenosylhomocysteinase
TAS
3
145,544,834
145,560,058
RGD:730275
RGD
G
Ahcy
adenosylhomocysteinase
ISS
3
145,544,834
145,560,058
RGD:7242426
RGD
G
As3mt
arsenic (+3 oxidation state) methyltransferase
TAS
1
252,029,638
252,061,352
RGD:625365
RGD
G
Asmt
acetylserotonin O-methyltransferase
NAS
12
16,811,892
16,817,186
RGD:1359073
RGD
G
Carm1
coactivator-associated arginine methyltransferase 1
ISS
8
20,650,468
20,695,147
RGD:1359044
RGD
G
Comt
catechol-O-methyltransferase
TAS
11
84,561,591
84,581,713
RGD:1359089
RGD
G
Dnmt1
DNA (cytosine-5-)-methyltransferase 1
TAS
8
19,926,995
19,973,256
RGD:1359078
RGD
G
Dot1l
DOT1-like histone H3K79 methyltransferase
ISS
7
10,428,275
10,466,913
RGD:1359080
RGD
G
Ftsj2
FtsJ RNA methyltransferase homolog 2 (E. coli)
ISS
12
14,782,565
14,787,472
RGD:1359074
RGD
G
Gamt
guanidinoacetate N-methyltransferase
IDA
7
10,959,990
10,962,720
RGD:1359081
RGD
G
Gnmt
glycine N-methyltransferase
IDA
9
10,127,092
10,130,444
RGD:1359070
RGD
G
Hnmt
histamine N-methyltransferase
ISS
3
2,057,938
2,089,955
RGD:1359041
RGD
G
Icmt
isoprenylcysteine carboxyl methyltransferase
ISS
5
169,526,961
169,533,722
RGD:1359083
RGD
G
Mthfr
methylenetetrahydrofolate reductase (NAD(P)H)
ISS
5
165,112,850
165,126,885
RGD:7242426
RGD
G
Nnmt
nicotinamide N-methyltransferase
ISS
8
51,871,506
51,883,785
RGD:1359084
RGD
G
Ocln
occludin
TAS
2
31,317,090
31,367,485
RGD:1359811
RGD
G
Pcmt1
protein-L-isoaspartate (D-aspartate) O-methyltransferase 1
IDA
1
2,287,981
2,304,638
RGD:729481
RGD
G
Pemt
phosphatidylethanolamine N-methyltransferase
IDA
RGD:729486
RGD
G
Pnmt
phenylethanolamine-N-methyltransferase
TAS
RGD:1359087
RGD
G
Prmt1
protein arginine methyltransferase 1
ISS
1
95,449,061
95,458,267
RGD:1359044
RGD
G
Prmt3
protein arginine methyltransferase 3
ISS
1
99,581,943
99,668,604
RGD:1359044
RGD
G
Prmt5
protein arginine methyltransferase 5
ISS
15
32,574,951
32,584,336
RGD:1359044
RGD
G
Prmt6
protein arginine methyltransferase 6
ISS
2
205,909,919
205,915,148
RGD:1359044
RGD
G
Rnmt
RNA (guanine-7-) methyltransferase
ISS
18
64,690,985
64,711,525
RGD:1359071
RGD
G
Setdb1
SET domain, bifurcated 1
ISS
2
190,232,228
190,264,309
RGD:1359072
RGD
G
Suv39h2
suppressor of variegation 3-9 homolog 2 (Drosophila)
ISS
17
85,875,954
85,894,979
RGD:1359810
RGD
G
Trdmt1
tRNA aspartic acid methyltransferase 1
ISS
17
87,791,647
87,824,484
RGD:1359088
RGD
remethylation pathway of homocysteine metabolism - cobalamin dependent
G
Mthfr
methylenetetrahydrofolate reductase (NAD(P)H)
ISS
5
165,112,850
165,126,885
RGD:7242426
RGD
G
Mtr
5-methyltetrahydrofolate-homocysteine methyltransferase
IDA
17
68,782,708
68,867,101
RGD:1359026
RGD
G
Mtr
5-methyltetrahydrofolate-homocysteine methyltransferase
ISS
17
68,782,708
68,867,101
RGD:7242426
RGD
G
Mtrr
5-methyltetrahydrofolate-homocysteine methyltransferase reductase
ISS
17
5,086,219
5,118,086
RGD:1359037
RGD
G
Mtrr
5-methyltetrahydrofolate-homocysteine methyltransferase reductase
ISS
17
5,086,219
5,118,086
RGD:7242426
RGD
remethylation pathway of homocysteine metabolism - cobalamin independent, betaine dependent
G
Bhmt
betaine-homocysteine S-methyltransferase
IDA
2
23,923,651
23,943,320
RGD:1359026
RGD
G
Bhmt
betaine-homocysteine S-methyltransferase
ISS
2
23,923,651
23,943,320
RGD:7242428
RGD
G
Bhmt
betaine-homocysteine S-methyltransferase
ISS
2
23,923,651
23,943,320
RGD:7242426
RGD
selenoamino acid metabolic pathway
G
Ccbl1
cysteine conjugate-beta lyase, cytoplasmic
IEA
3
9,195,737
9,209,545
RGD:6907045
KEGG
G
Cth
cystathionase (cystathionine gamma-lyase)
IEA
2
256,056,562
256,082,248
RGD:6907045
KEGG
G
Inmt
indolethylamine N-methyltransferase
IEA
4
83,934,018
83,938,314
RGD:6907045
KEGG
G
Kat3
kynurenine aminotransferase III
IEA
RGD:6907045
KEGG
G
Mars
methionyl-tRNA synthetase
IEA
7
67,252,510
67,269,807
RGD:6907045
KEGG
G
Mars2
methionyl-tRNA synthetase 2, mitochondrial
IEA
9
54,026,948
54,029,796
RGD:6907045
KEGG
G
Mtr
5-methyltetrahydrofolate-homocysteine methyltransferase
IEA
17
68,782,708
68,867,101
RGD:6907045
KEGG
G
Papss1
3'-phosphoadenosine 5'-phosphosulfate synthase 1
IEA
2
229,005,799
229,040,958
RGD:6907045
KEGG
G
Papss2
3'-phosphoadenosine 5'-phosphosulfate synthase 2
IEA
1
236,592,414
236,677,379
RGD:6907045
KEGG
G
Scly
selenocysteine lyase
IEA
9
90,525,575
90,546,159
RGD:6907045
KEGG
G
Sephs1
selenophosphate synthetase 1
IEA
17
84,443,153
84,473,434
RGD:6907045
KEGG
G
Sephs2
selenophosphate synthetase 2
IEA
1
186,535,717
186,538,035
RGD:6907045
KEGG
G
Txnrd1
thioredoxin reductase 1
IEA
7
23,055,544
23,093,815
RGD:6907045
KEGG
G
Txnrd2
thioredoxin reductase 2
IEA
11
84,513,361
84,561,673
RGD:6907045
KEGG
G
Txnrd3
thioredoxin reductase 3
IEA
4
123,730,278
123,771,572
RGD:6907045
KEGG
taurine and hypotaurine metabolic pathway
G
Ado
2-aminoethanethiol (cysteamine) dioxygenase
IEA
20
21,877,141
21,878,612
RGD:6907045
KEGG
G
Baat
bile acid CoA: amino acid N-acyltransferase (glycine N-choloyltransferase)
IEA
5
66,245,786
66,254,757
RGD:6907045
KEGG
G
Cdo1
cysteine dioxygenase, type I
IEA
18
40,914,028
40,928,671
RGD:6907045
KEGG
G
Csad
cysteine sulfinic acid decarboxylase
IEA
7
140,917,995
140,944,405
RGD:6907045
KEGG
G
Gad1
glutamate decarboxylase 1
IEA
3
52,789,370
52,830,038
RGD:6907045
KEGG
G
Gad2
glutamate decarboxylase 2
IEA
17
96,259,430
96,321,857
RGD:6907045
KEGG
G
Ggt1
gamma-glutamyltransferase 1
IEA
RGD:6907045
KEGG
G
Ggt5
gamma-glutamyltransferase 5
IEA
RGD:6907045
KEGG
G
Ggt6
gamma-glutamyl transferase 6
IEA
10
59,320,455
59,322,932
RGD:6907045
KEGG
G
Ggt7
gamma-glutamyltransferase 7
IEA
3
145,987,531
146,010,922
RGD:6907045
KEGG
transsulfuration pathway of homocysteine metabolism
G
Cbs
cystathionine beta synthase
IDA
20
10,047,478
10,075,520
RGD:1359024
RGD
G
Cbs
cystathionine beta synthase
ISS
20
10,047,478
10,075,520
RGD:7242427
RGD
G
Cdo1
cysteine dioxygenase, type I
ISS
18
40,914,028
40,928,671
RGD:7242427
RGD
G
Csad
cysteine sulfinic acid decarboxylase
ISS
7
140,917,995
140,944,405
RGD:7242427
RGD
G
Cth
cystathionase (cystathionine gamma-lyase)
IDA
2
256,056,562
256,082,248
RGD:1359024
RGD
G
Cth
cystathionase (cystathionine gamma-lyase)
ISS
2
256,056,562
256,082,248
RGD:7242427
RGD
Term paths to the root one longest all shortest one shortest all one shortest and longest all longest