ONTOLOGY REPORT - ANNOTATIONS


Term:metabolic pathway of other amino acids
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Accession:PW:0000132 term browser browse the term
Definition:Those metabolic reactions involved in the synthesis, utilization and/or degradation of amino acids other than the common 20 amino acids found in protein. Some of these amino acids like carnitine or homocysteine derive from primary amino acids.


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beta-alanine metabolic pathway term browser
Symbol Object Name GBrowse Evidence Chr Start Stop Reference Source
G Abat 4-aminobutyrate aminotransferase GBrowse link IEA 10 7,040,725 7,137,154 RGD:6907045 KEGG
G Acadm acyl-CoA dehydrogenase, C-4 to C-12 straight chain GBrowse link IEA 2 251,866,645 251,890,729 RGD:6907045 KEGG
G Aldh1a1 aldehyde dehydrogenase 1 family, member A1 GBrowse link IEA 1 223,731,675 223,773,285 RGD:6907045 KEGG
G Aldh1a3 aldehyde dehydrogenase 1 family, member A3 GBrowse link IEA 1 120,847,746 120,881,883 RGD:6907045 KEGG
G Aldh1a7 aldehyde dehydrogenase family 1, subfamily A7 GBrowse link IEA 1 223,822,536 223,875,238 RGD:6907045 KEGG
G Aldh1b1 aldehyde dehydrogenase 1 family, member B1 GBrowse link IEA 5 62,311,268 62,316,276 RGD:6907045 KEGG
G Aldh2 aldehyde dehydrogenase 2 family (mitochondrial) GBrowse link IEA 12 36,081,778 36,116,445 RGD:6907045 KEGG
G Aldh3a1 aldehyde dehydrogenase 3 family, member A1 GBrowse link IEA 10 47,365,195 47,374,880 RGD:6907045 KEGG
G Aldh3a2 aldehyde dehydrogenase 3 family, member A2 GBrowse link IEA 10 47,400,518 47,421,064 RGD:6907045 KEGG
G Aldh3b1 aldehyde dehydrogenase 3 family, member B1 GBrowse link IEA 1 206,438,325 206,455,477 RGD:6907045 KEGG
G Aldh7a1 aldehyde dehydrogenase 7 family, member A1 GBrowse link IEA 18 52,300,899 52,333,149 RGD:6907045 KEGG
G Aldh9a1 aldehyde dehydrogenase 9 family, member A1 GBrowse link IEA 13 83,017,312 83,034,047 RGD:6907045 KEGG
G Aoc3 amine oxidase, copper containing 3 GBrowse link IEA 10 90,357,094 90,365,040 RGD:6907045 KEGG
G Cndp1 carnosine dipeptidase 1 (metallopeptidase M20 family) GBrowse link IEA 18 81,160,681 81,183,558 RGD:6907045 KEGG
G Dpyd dihydropyrimidine dehydrogenase GBrowse link IEA 2 214,931,901 215,818,809 RGD:6907045 KEGG
G Dpys dihydropyrimidinase GBrowse link IEA 7 75,368,238 75,446,160 RGD:6907045 KEGG
G Echs1 enoyl CoA hydratase, short chain, 1, mitochondrial GBrowse link IEA 1 199,901,585 199,910,412 RGD:6907045 KEGG
G Ehhadh enoyl-CoA, hydratase/3-hydroxyacyl CoA dehydrogenase GBrowse link IEA 11 81,474,161 81,507,645 RGD:6907045 KEGG
G Gad1 glutamate decarboxylase 1 GBrowse link IEA 3 52,789,370 52,830,038 RGD:6907045 KEGG
G Gad2 glutamate decarboxylase 2 GBrowse link IEA 17 96,259,430 96,321,857 RGD:6907045 KEGG
G Hadha hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), alpha subunit GBrowse link IEA 6 26,173,798 26,191,433 RGD:6907045 KEGG
G Hibch 3-hydroxyisobutyryl-CoA hydrolase GBrowse link IEA 9 45,564,702 45,645,252 RGD:6907045 KEGG
G Mlycd malonyl-CoA decarboxylase GBrowse link IEA 19 49,637,193 49,653,016 RGD:6907045 KEGG
G Srm spermidine synthase GBrowse link IEA 5 165,672,516 165,675,673 RGD:6907045 KEGG
G Upb1 ureidopropionase, beta GBrowse link IEA 20 13,715,995 13,743,261 RGD:6907045 KEGG
creatine metabolic pathway term browser
Symbol Object Name GBrowse Evidence Chr Start Stop Reference Source
G Ckm creatine kinase, muscle GBrowse link IDA 1 78,762,202 78,772,681 RGD:1359082 RGD
G Gamt guanidinoacetate N-methyltransferase GBrowse link IDA 7 10,959,990 10,962,720 RGD:1359082 RGD
G Gatm glycine amidinotransferase (L-arginine:glycine amidinotransferase) GBrowse link TAS 3 109,558,043 109,565,432 RGD:70746 RGD
G Slc6a8 solute carrier family 6 (neurotransmitter transporter, creatine), member 8 GBrowse link IDA X 159,570,789 159,580,093 RGD:1359082 RGD
cyanoamino acid metabolic pathway term browser
Symbol Object Name GBrowse Evidence Chr Start Stop Reference Source
G Gba3 glucosidase, beta, acid 3 (cytosolic) GBrowse link IEA 14 65,467,770 65,550,278 RGD:6907045 KEGG
G Ggt1 gamma-glutamyltransferase 1 IEA RGD:6907045 KEGG
G Ggt5 gamma-glutamyltransferase 5 IEA RGD:6907045 KEGG
G Ggt6 gamma-glutamyl transferase 6 GBrowse link IEA 10 59,320,455 59,322,932 RGD:6907045 KEGG
G Ggt7 gamma-glutamyltransferase 7 GBrowse link IEA 3 145,987,531 146,010,922 RGD:6907045 KEGG
G Shmt1 serine hydroxymethyltransferase 1 (soluble) GBrowse link IEA 10 46,936,605 46,964,779 RGD:6907045 KEGG
G Shmt2 serine hydroxymethyltransferase 2 (mitochondrial) GBrowse link IEA 7 67,494,470 67,499,540 RGD:6907045 KEGG
D-arginine and D-ornithine metabolic pathway term browser
Symbol Object Name GBrowse Evidence Chr Start Stop Reference Source
G Dao D-amino-acid oxidase GBrowse link IEA 12 43,627,593 43,648,332 RGD:6907045 KEGG
D-glutamine and D-glutamate metabolic pathway term browser
Symbol Object Name GBrowse Evidence Chr Start Stop Reference Source
G Gls glutaminase GBrowse link IEA 9 46,380,165 46,452,974 RGD:6907045 KEGG
G Gls2 glutaminase 2 (liver, mitochondrial) GBrowse link IEA 7 1,484,397 1,495,283 RGD:6907045 KEGG
G Glud1 glutamate dehydrogenase 1 GBrowse link IEA 16 9,965,718 9,999,254 RGD:6907045 KEGG
glutathione metabolic pathway term browser
Symbol Object Name GBrowse Evidence Chr Start Stop Reference Source
G Anpep alanyl (membrane) aminopeptidase GBrowse link IEA 1 135,600,751 135,619,208 RGD:6907045 KEGG
G G6pd glucose-6-phosphate dehydrogenase GBrowse link IEA X 160,186,450 160,192,316 RGD:6907045 KEGG
G Gclc glutamate-cysteine ligase, catalytic subunit GBrowse link IEA 8 82,724,429 82,762,848 RGD:6907045 KEGG
G Gclc glutamate-cysteine ligase, catalytic subunit GBrowse link IMP 8 82,724,429 82,762,848 RGD:1582661 RGD
G Gclc glutamate-cysteine ligase, catalytic subunit GBrowse link IDA 8 82,724,429 82,762,848 RGD:1582663 RGD
G Gclm glutamate cysteine ligase, modifier subunit GBrowse link IEA 2 218,895,434 218,915,491 RGD:6907045 KEGG
G Gclm glutamate cysteine ligase, modifier subunit GBrowse link IMP 2 218,895,434 218,915,491 RGD:1582661 RGD
G Gclm glutamate cysteine ligase, modifier subunit GBrowse link IDA 2 218,895,434 218,915,491 RGD:1582663 RGD
G Ggct gamma-glutamyl cyclotransferase GBrowse link IEA 4 83,459,924 83,467,120 RGD:6907045 KEGG
G Ggt1 gamma-glutamyltransferase 1 IEA RGD:6907045 KEGG
G Ggt5 gamma-glutamyltransferase 5 IEA RGD:6907045 KEGG
G Ggt6 gamma-glutamyl transferase 6 GBrowse link IEA 10 59,320,455 59,322,932 RGD:6907045 KEGG
G Ggt7 gamma-glutamyltransferase 7 GBrowse link IEA 3 145,987,531 146,010,922 RGD:6907045 KEGG
G Gpx1 glutathione peroxidase 1 IEA RGD:6907045 KEGG
G Gpx2 glutathione peroxidase 2 GBrowse link IEA 6 99,372,418 99,376,230 RGD:6907045 KEGG
G Gpx3 glutathione peroxidase 3 GBrowse link IEA 10 40,311,094 40,319,382 RGD:6907045 KEGG
G Gpx4 glutathione peroxidase 4 GBrowse link IEA 7 11,162,521 11,165,318 RGD:6907045 KEGG
G Gpx5 glutathione peroxidase 5 IEA RGD:6907045 KEGG
G Gpx6 glutathione peroxidase 6 GBrowse link IEA 17 51,063,379 51,068,058 RGD:6907045 KEGG
G Gpx7 glutathione peroxidase 7 GBrowse link IEA 5 129,506,986 129,514,830 RGD:6907045 KEGG
G Gpx8 glutathione peroxidase 8 GBrowse link IEA 2 44,424,009 44,427,603 RGD:6907045 KEGG
G Gsr glutathione reductase GBrowse link IEA 16 62,255,562 62,298,458 RGD:6907045 KEGG
G Gss glutathione synthetase GBrowse link IEA 3 146,057,517 146,087,820 RGD:6907045 KEGG
G Gsta2 glutathione S-transferase alpha 2 GBrowse link IEA 8 83,299,249 83,312,958 RGD:6907045 KEGG
G Gsta3 glutathione S-transferase alpha 3 GBrowse link IEA 9 20,005,570 20,032,031 RGD:6907045 KEGG
G Gsta4 glutathione S-transferase alpha 4 GBrowse link IEA 8 83,165,139 83,183,055 RGD:6907045 KEGG
G Gsta5 glutathione S-transferase alpha 5 GBrowse link IEA 8 83,202,554 83,211,997 RGD:6907045 KEGG
G Gstk1 glutathione S-transferase kappa 1 GBrowse link IEA 4 69,999,767 70,004,086 RGD:6907045 KEGG
G Gstm1 glutathione S-transferase mu 1 GBrowse link IEA 2 203,575,444 203,580,821 RGD:6907045 KEGG
G Gstm2 glutathione S-transferase mu 2 GBrowse link IEA 2 203,549,022 203,553,380 RGD:6907045 KEGG
G Gstm3 glutathione S-transferase mu 3 GBrowse link IEA 2 203,532,363 203,537,135 RGD:6907045 KEGG
G Gstm4 glutathione S-transferase mu 4 GBrowse link IEA 2 203,605,593 203,610,817 RGD:6907045 KEGG
G Gstm5 glutathione S-transferase, mu 5 GBrowse link IEA 2 203,456,122 203,458,917 RGD:6907045 KEGG
G Gstm6 glutathione S-transferase, mu 6 GBrowse link IEA 2 203,504,228 203,509,002 RGD:6907045 KEGG
G Gstm7 glutathione S-transferase, mu 7 GBrowse link IEA 2 203,491,366 203,496,812 RGD:6907045 KEGG
G Gsto1 glutathione S-transferase omega 1 GBrowse link IEA 1 253,228,547 253,238,531 RGD:6907045 KEGG
G Gsto2 glutathione S-transferase omega 2 GBrowse link IEA 1 253,239,392 253,275,110 RGD:6907045 KEGG
G Gstp1 glutathione S-transferase pi 1 GBrowse link IEA 1 206,627,398 206,629,866 RGD:6907045 KEGG
G Gstt1 glutathione S-transferase theta 1 GBrowse link IEA 20 13,604,355 13,621,456 RGD:6907045 KEGG
G Gstt2 glutathione S-transferase, theta 2 GBrowse link IEA 20 13,221,696 13,225,367 RGD:6907045 KEGG
G Gstz1 glutathione S-transferase zeta 1 IEA RGD:6907045 KEGG
G Idh1 isocitrate dehydrogenase 1 (NADP+), soluble GBrowse link IEA 9 63,769,401 63,790,622 RGD:6907045 KEGG
G Idh2 isocitrate dehydrogenase 2 (NADP+), mitochondrial GBrowse link IEA 1 135,876,052 135,895,373 RGD:6907045 KEGG
G Lap3 leucine aminopeptidase 3 GBrowse link IEA 14 70,680,077 70,699,061 RGD:6907045 KEGG
G Mgst1 microsomal glutathione S-transferase 1 GBrowse link IEA 4 175,248,654 175,263,881 RGD:6907045 KEGG
G Mgst2 microsomal glutathione S-transferase 2 GBrowse link IEA 2 140,546,939 140,568,616 RGD:6907045 KEGG
G Mgst3 microsomal glutathione S-transferase 3 GBrowse link IEA 13 83,038,049 83,058,802 RGD:6907045 KEGG
G Odc1 ornithine decarboxylase 1 GBrowse link IEA 6 41,309,211 41,315,796 RGD:6907045 KEGG
G Oplah 5-oxoprolinase (ATP-hydrolysing) GBrowse link IEA 7 114,326,739 114,341,949 RGD:6907045 KEGG
G RGD1562107 similar to class-alpha glutathione S-transferase GBrowse link IEA 9 19,965,797 19,978,363 RGD:6907045 KEGG
G Rrm1 ribonucleotide reductase M1 GBrowse link IEA 1 159,930,994 159,937,860 RGD:6907045 KEGG
G Rrm2 ribonucleotide reductase M2 GBrowse link IEA 6 42,350,541 42,356,748 RGD:6907045 KEGG
G Rrm2b ribonucleotide reductase M2 B (TP53 inducible) GBrowse link IEA 7 73,432,161 73,459,541 RGD:6907045 KEGG
G Srm spermidine synthase GBrowse link IEA 5 165,672,516 165,675,673 RGD:6907045 KEGG
G Txndc12 thioredoxin domain containing 12 (endoplasmic reticulum) GBrowse link IEA 5 130,142,600 130,167,629 RGD:6907045 KEGG
homocysteine metabolic pathway term browser
Symbol Object Name GBrowse Evidence Chr Start Stop Reference Source
G Ahcy adenosylhomocysteinase GBrowse link TAS 3 145,544,834 145,560,058 RGD:730275 RGD
G Ahcy adenosylhomocysteinase GBrowse link ISS 3 145,544,834 145,560,058 RGD:7242426 RGD
G As3mt arsenic (+3 oxidation state) methyltransferase GBrowse link TAS 1 252,029,638 252,061,352 RGD:625365 RGD
G Asmt acetylserotonin O-methyltransferase GBrowse link NAS 12 16,811,892 16,817,186 RGD:1359073 RGD
G Carm1 coactivator-associated arginine methyltransferase 1 GBrowse link ISS 8 20,650,468 20,695,147 RGD:1359044 RGD
G Comt catechol-O-methyltransferase GBrowse link TAS 11 84,561,591 84,581,713 RGD:1359089 RGD
G Dnmt1 DNA (cytosine-5-)-methyltransferase 1 GBrowse link TAS 8 19,926,995 19,973,256 RGD:1359078 RGD
G Dot1l DOT1-like histone H3K79 methyltransferase GBrowse link ISS 7 10,428,275 10,466,913 RGD:1359080 RGD
G Ftsj2 FtsJ RNA methyltransferase homolog 2 (E. coli) GBrowse link ISS 12 14,782,565 14,787,472 RGD:1359074 RGD
G Gamt guanidinoacetate N-methyltransferase GBrowse link IDA 7 10,959,990 10,962,720 RGD:1359081 RGD
G Gnmt glycine N-methyltransferase GBrowse link IDA 9 10,127,092 10,130,444 RGD:1359070 RGD
G Hnmt histamine N-methyltransferase GBrowse link ISS 3 2,057,938 2,089,955 RGD:1359041 RGD
G Icmt isoprenylcysteine carboxyl methyltransferase GBrowse link ISS 5 169,526,961 169,533,722 RGD:1359083 RGD
G Mthfr methylenetetrahydrofolate reductase (NAD(P)H) GBrowse link ISS 5 165,112,850 165,126,885 RGD:7242426 RGD
G Nnmt nicotinamide N-methyltransferase GBrowse link ISS 8 51,871,506 51,883,785 RGD:1359084 RGD
G Ocln occludin GBrowse link TAS 2 31,317,090 31,367,485 RGD:1359811 RGD
G Pcmt1 protein-L-isoaspartate (D-aspartate) O-methyltransferase 1 GBrowse link IDA 1 2,287,981 2,304,638 RGD:729481 RGD
G Pemt phosphatidylethanolamine N-methyltransferase IDA RGD:729486 RGD
G Pnmt phenylethanolamine-N-methyltransferase TAS RGD:1359087 RGD
G Prmt1 protein arginine methyltransferase 1 GBrowse link ISS 1 95,449,061 95,458,267 RGD:1359044 RGD
G Prmt3 protein arginine methyltransferase 3 GBrowse link ISS 1 99,581,943 99,668,604 RGD:1359044 RGD
G Prmt5 protein arginine methyltransferase 5 GBrowse link ISS 15 32,574,951 32,584,336 RGD:1359044 RGD
G Prmt6 protein arginine methyltransferase 6 GBrowse link ISS 2 205,909,919 205,915,148 RGD:1359044 RGD
G Rnmt RNA (guanine-7-) methyltransferase GBrowse link ISS 18 64,690,985 64,711,525 RGD:1359071 RGD
G Setdb1 SET domain, bifurcated 1 GBrowse link ISS 2 190,232,228 190,264,309 RGD:1359072 RGD
G Suv39h2 suppressor of variegation 3-9 homolog 2 (Drosophila) GBrowse link ISS 17 85,875,954 85,894,979 RGD:1359810 RGD
G Trdmt1 tRNA aspartic acid methyltransferase 1 GBrowse link ISS 17 87,791,647 87,824,484 RGD:1359088 RGD
remethylation pathway of homocysteine metabolism - cobalamin dependent term browser
Symbol Object Name GBrowse Evidence Chr Start Stop Reference Source
G Mthfr methylenetetrahydrofolate reductase (NAD(P)H) GBrowse link ISS 5 165,112,850 165,126,885 RGD:7242426 RGD
G Mtr 5-methyltetrahydrofolate-homocysteine methyltransferase GBrowse link IDA 17 68,782,708 68,867,101 RGD:1359026 RGD
G Mtr 5-methyltetrahydrofolate-homocysteine methyltransferase GBrowse link ISS 17 68,782,708 68,867,101 RGD:7242426 RGD
G Mtrr 5-methyltetrahydrofolate-homocysteine methyltransferase reductase GBrowse link ISS 17 5,086,219 5,118,086 RGD:1359037 RGD
G Mtrr 5-methyltetrahydrofolate-homocysteine methyltransferase reductase GBrowse link ISS 17 5,086,219 5,118,086 RGD:7242426 RGD
remethylation pathway of homocysteine metabolism - cobalamin independent, betaine dependent term browser
Symbol Object Name GBrowse Evidence Chr Start Stop Reference Source
G Bhmt betaine-homocysteine S-methyltransferase GBrowse link IDA 2 23,923,651 23,943,320 RGD:1359026 RGD
G Bhmt betaine-homocysteine S-methyltransferase GBrowse link ISS 2 23,923,651 23,943,320 RGD:7242428 RGD
G Bhmt betaine-homocysteine S-methyltransferase GBrowse link ISS 2 23,923,651 23,943,320 RGD:7242426 RGD
selenoamino acid metabolic pathway term browser
Symbol Object Name GBrowse Evidence Chr Start Stop Reference Source
G Ccbl1 cysteine conjugate-beta lyase, cytoplasmic GBrowse link IEA 3 9,195,737 9,209,545 RGD:6907045 KEGG
G Cth cystathionase (cystathionine gamma-lyase) GBrowse link IEA 2 256,056,562 256,082,248 RGD:6907045 KEGG
G Inmt indolethylamine N-methyltransferase GBrowse link IEA 4 83,934,018 83,938,314 RGD:6907045 KEGG
G Kat3 kynurenine aminotransferase III IEA RGD:6907045 KEGG
G Mars methionyl-tRNA synthetase GBrowse link IEA 7 67,252,510 67,269,807 RGD:6907045 KEGG
G Mars2 methionyl-tRNA synthetase 2, mitochondrial GBrowse link IEA 9 54,026,948 54,029,796 RGD:6907045 KEGG
G Mtr 5-methyltetrahydrofolate-homocysteine methyltransferase GBrowse link IEA 17 68,782,708 68,867,101 RGD:6907045 KEGG
G Papss1 3'-phosphoadenosine 5'-phosphosulfate synthase 1 GBrowse link IEA 2 229,005,799 229,040,958 RGD:6907045 KEGG
G Papss2 3'-phosphoadenosine 5'-phosphosulfate synthase 2 GBrowse link IEA 1 236,592,414 236,677,379 RGD:6907045 KEGG
G Scly selenocysteine lyase GBrowse link IEA 9 90,525,575 90,546,159 RGD:6907045 KEGG
G Sephs1 selenophosphate synthetase 1 GBrowse link IEA 17 84,443,153 84,473,434 RGD:6907045 KEGG
G Sephs2 selenophosphate synthetase 2 GBrowse link IEA 1 186,535,717 186,538,035 RGD:6907045 KEGG
G Txnrd1 thioredoxin reductase 1 GBrowse link IEA 7 23,055,544 23,093,815 RGD:6907045 KEGG
G Txnrd2 thioredoxin reductase 2 GBrowse link IEA 11 84,513,361 84,561,673 RGD:6907045 KEGG
G Txnrd3 thioredoxin reductase 3 GBrowse link IEA 4 123,730,278 123,771,572 RGD:6907045 KEGG
taurine and hypotaurine metabolic pathway term browser
Symbol Object Name GBrowse Evidence Chr Start Stop Reference Source
G Ado 2-aminoethanethiol (cysteamine) dioxygenase GBrowse link IEA 20 21,877,141 21,878,612 RGD:6907045 KEGG
G Baat bile acid CoA: amino acid N-acyltransferase (glycine N-choloyltransferase) GBrowse link IEA 5 66,245,786 66,254,757 RGD:6907045 KEGG
G Cdo1 cysteine dioxygenase, type I GBrowse link IEA 18 40,914,028 40,928,671 RGD:6907045 KEGG
G Csad cysteine sulfinic acid decarboxylase GBrowse link IEA 7 140,917,995 140,944,405 RGD:6907045 KEGG
G Gad1 glutamate decarboxylase 1 GBrowse link IEA 3 52,789,370 52,830,038 RGD:6907045 KEGG
G Gad2 glutamate decarboxylase 2 GBrowse link IEA 17 96,259,430 96,321,857 RGD:6907045 KEGG
G Ggt1 gamma-glutamyltransferase 1 IEA RGD:6907045 KEGG
G Ggt5 gamma-glutamyltransferase 5 IEA RGD:6907045 KEGG
G Ggt6 gamma-glutamyl transferase 6 GBrowse link IEA 10 59,320,455 59,322,932 RGD:6907045 KEGG
G Ggt7 gamma-glutamyltransferase 7 GBrowse link IEA 3 145,987,531 146,010,922 RGD:6907045 KEGG
transsulfuration pathway of homocysteine metabolism term browser
Symbol Object Name GBrowse Evidence Chr Start Stop Reference Source
G Cbs cystathionine beta synthase GBrowse link IDA 20 10,047,478 10,075,520 RGD:1359024 RGD
G Cbs cystathionine beta synthase GBrowse link ISS 20 10,047,478 10,075,520 RGD:7242427 RGD
G Cdo1 cysteine dioxygenase, type I GBrowse link ISS 18 40,914,028 40,928,671 RGD:7242427 RGD
G Csad cysteine sulfinic acid decarboxylase GBrowse link ISS 7 140,917,995 140,944,405 RGD:7242427 RGD
G Cth cystathionase (cystathionine gamma-lyase) GBrowse link IDA 2 256,056,562 256,082,248 RGD:1359024 RGD
G Cth cystathionase (cystathionine gamma-lyase) GBrowse link ISS 2 256,056,562 256,082,248 RGD:7242427 RGD

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