ONTOLOGY REPORT - ANNOTATIONS
Term: mitochondrial translation
Accession: GO:0032543
browse the term
Definition: The chemical reactions and pathways resulting in the formation of a protein in a mitochondrion. This is a ribosome-mediated process in which the information in messenger RNA (mRNA) is used to specify the sequence of amino acids in the protein; the mitochondrion has its own ribosomes and transfer RNAs, and uses a genetic code that differs from the nuclear code.
Synonyms: exact_synonym: mitochondrial protein anabolism; mitochondrial protein biosynthesis; mitochondrial protein formation; mitochondrial protein synthesis; mitochondrial protein translation
only_in_taxon: NCBITaxon:2759 ! Eukaryota
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Chchd1
coiled-coil-helix-coiled-coil-helix domain containing 1
involved_in
IEA
GO_REF:0000002
InterPro
GO_REF:0000002
NCBI chr15:3,592,719...3,593,901
Ensembl chr15:3,592,727...3,593,901
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ENSRNOG00000064147
involved_in
IEA
GO_REF:0000118
TreeGrafter
GO_REF:0000118
Ensembl chr15:54,413,775...54,415,497
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Fastkd2
FAST kinase domains 2
involved_in
ISO IEA ISS
(PMID:26370583) GO_REF:0000107 GO_REF:0000024
RGD Ensembl UniProt
PMID:26370583
GO_REF:0000024 GO_REF:0000107
NCBI chr 9:65,166,148...65,188,184
Ensembl chr 9:65,168,228...65,188,174
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Gatb
glutamyl-tRNA amidotransferase subunit B
involved_in
ISO IBA
(PMID:19805282) GO_REF:0000033
RGD GO_Central
PMID:19805282
GO_REF:0000033
NCBI chr 2:170,930,547...171,017,133
Ensembl chr 2:170,930,542...171,016,695
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Gatc
glutamyl-tRNA amidotransferase subunit C
involved_in
ISO IBA IEA
(PMID:19805282) GO_REF:0000033 GO_REF:0000104
RGD GO_Central UniProt
PMID:19805282
GO_REF:0000033 GO_REF:0000104
NCBI chr12:41,270,096...41,278,067
Ensembl chr12:41,270,087...41,277,995
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Gfm2
GTP dependent ribosome recycling factor mitochondrial 2
involved_in
ISO IBA IEA ISS
(PMID:19716793) GO_REF:0000033 GO_REF:0000104 GO_REF:0000024
RGD GO_Central UniProt
PMID:19716793
GO_REF:0000024 GO_REF:0000033 GO_REF:0000104
NCBI chr 2:28,449,452...28,488,200
Ensembl chr 2:28,449,517...28,488,197
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Hars1
histidyl-tRNA synthetase 1
involved_in
IBA
GO_REF:0000033
GO_Central
GO_REF:0000033
NCBI chr18:28,381,649...28,398,699
Ensembl chr18:28,381,655...28,398,740
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Iars2
isoleucyl-tRNA synthetase 2, mitochondrial
involved_in
IBA
GO_REF:0000033
GO_Central
GO_REF:0000033
NCBI chr13:96,831,484...96,865,518
Ensembl chr13:96,831,484...96,865,501
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Lars2
leucyl-tRNA synthetase 2, mitochondrial
involved_in
IBA
GO_REF:0000033
GO_Central
GO_REF:0000033
NCBI chr 8:123,010,271...123,106,395
Ensembl chr 8:123,010,293...123,106,395
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Mrpl16
mitochondrial ribosomal protein L16
involved_in
IBA IEA
GO_REF:0000033 GO_REF:0000118
GO_Central TreeGrafter
GO_REF:0000033 GO_REF:0000118
NCBI chr 1:208,633,671...208,638,483
Ensembl chr 1:208,633,586...208,640,667
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Mrpl2
mitochondrial ribosomal protein L2
involved_in
IBA
GO_REF:0000033
GO_Central
GO_REF:0000033
NCBI chr 9:14,333,233...14,337,006
Ensembl chr 9:14,333,234...14,337,040
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Mrpl23
mitochondrial ribosomal protein L23
involved_in
IEA IBA
GO_REF:0000118 GO_REF:0000033
TreeGrafter GO_Central
GO_REF:0000033 GO_REF:0000118
NCBI chr 1:197,687,452...197,695,222
Ensembl chr 1:197,687,347...197,695,222
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Mrpl43
mitochondrial ribosomal protein L43
involved_in
IEA
GO_REF:0000002
InterPro
GO_REF:0000002
NCBI chr 1:243,866,848...243,868,285
Ensembl chr 1:243,866,931...243,868,281
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Mrpl47
mitochondrial ribosomal protein L47
involved_in
IBA
GO_REF:0000033
GO_Central
GO_REF:0000033
NCBI chr 2:115,507,842...115,520,093
Ensembl chr 2:115,500,264...115,518,994
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Mrpl57
mitochondrial ribosomal protein L57
involved_in
IEA
GO_REF:0000118
TreeGrafter
GO_REF:0000118
NCBI chr15:31,970,904...31,971,766
Ensembl chr15:31,970,860...31,973,993
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Mrps11
mitochondrial ribosomal protein S11
involved_in
IEA
GO_REF:0000118
TreeGrafter
GO_REF:0000118
NCBI chr 1:132,707,601...132,717,253
Ensembl chr 1:132,680,420...132,717,253
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Mrps14
mitochondrial ribosomal protein S14
involved_in
ISO
(PMID:30358850)
RGD
PMID:30358850
NCBI chr13:72,429,168...72,434,915
Ensembl chr13:72,408,558...72,434,915
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Mrps15
mitochondrial ribosomal protein S15
involved_in
IEA
GO_REF:0000118
TreeGrafter
GO_REF:0000118
NCBI chr 5:138,321,610...138,332,205
Ensembl chr 5:138,321,593...138,332,205
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Mrps16
mitochondrial ribosomal protein S16
involved_in
IEA
GO_REF:0000118
TreeGrafter
GO_REF:0000118
NCBI chr15:3,918,621...3,921,024
Ensembl chr15:3,918,615...3,921,656
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Mrps17
mitochondrial ribosomal protein S17
involved_in
IEA
GO_REF:0000118
TreeGrafter
GO_REF:0000118
NCBI chr12:26,948,535...26,951,828
Ensembl chr12:26,948,730...26,951,737 Ensembl chr12:26,948,730...26,951,737
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Mrps18a
mitochondrial ribosomal protein S18A
involved_in
IEA
GO_REF:0000118
TreeGrafter
GO_REF:0000118
NCBI chr 9:14,853,322...14,869,819
Ensembl chr 9:14,853,291...14,869,835
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Mrps18b
mitochondrial ribosomal protein S18B
involved_in
IEA
GO_REF:0000002
InterPro
GO_REF:0000002
NCBI chr20:2,838,174...2,844,260
Ensembl chr20:2,838,030...2,844,260
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Mrps18c
mitochondrial ribosomal protein S18C
involved_in
IEA
GO_REF:0000118
TreeGrafter
GO_REF:0000118
NCBI chr14:8,812,301...8,818,538
Ensembl chr14:8,791,330...8,818,516
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Mrps28
mitochondrial ribosomal protein S28
involved_in
ISO
(PMID:30566640)
RGD
PMID:30566640
NCBI chr 2:92,820,676...92,951,302
Ensembl chr 2:92,820,606...92,951,284
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Mrps34
mitochondrial ribosomal protein S34
involved_in
ISO IBA
(PMID:28777931) GO_REF:0000033 (MGI:5645169|PMID:25816300)
RGD GO_Central
PMID:25816300 PMID:28777931
GO_REF:0000033 MGI:5645169
NCBI chr10:13,916,024...13,917,155
Ensembl chr10:13,916,026...13,918,406
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Mrps35
mitochondrial ribosomal protein S35
involved_in
IEA
GO_REF:0000002
InterPro
GO_REF:0000002
NCBI chr 4:179,958,067...179,988,752
Ensembl chr 4:179,958,083...179,987,710
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Mrps7
mitochondrial ribosomal protein S7
involved_in
ISS
GO_REF:0000024
UniProt
GO_REF:0000024
NCBI chr10:100,843,691...100,846,838
Ensembl chr10:100,843,356...100,847,129
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Mtg1
mitochondrial ribosome-associated GTPase 1
involved_in
IBA
GO_REF:0000033
GO_Central
GO_REF:0000033
NCBI chr 1:194,931,543...194,944,278
Ensembl chr 1:194,931,531...194,944,277
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Ptcd1
pentatricopeptide repeat domain 1
involved_in
IEA
GO_REF:0000107
Ensembl
GO_REF:0000107
NCBI chr12:9,445,656...9,463,434
Ensembl chr12:9,445,714...9,463,508
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Ptcd3
Pentatricopeptide repeat domain 3
involved_in
ISO IBA
(PMID:19427859) GO_REF:0000033
RGD GO_Central
PMID:19427859
GO_REF:0000033
NCBI chr 4:103,922,440...103,957,445
Ensembl chr 4:103,920,566...103,957,538
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Qrsl1
glutaminyl-tRNA amidotransferase subunit QRSL1
involved_in acts_upstream_of_or_within
ISO IBA IEA
(PMID:19805282) (PMID:24579914) GO_REF:0000033 GO_REF:0000104
RGD GO_Central UniProt
PMID:19805282 PMID:24579914
GO_REF:0000033 GO_REF:0000104
NCBI chr20:47,357,206...47,382,160
Ensembl chr20:47,357,216...47,382,135
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Rars1
arginyl-tRNA synthetase 1
involved_in
IEA
GO_REF:0000118
TreeGrafter
GO_REF:0000118
NCBI chr10:20,270,744...20,295,192
Ensembl chr10:20,270,483...20,295,196
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Rars2
arginyl-tRNA synthetase 2, mitochondrial
involved_in
IBA
GO_REF:0000033
GO_Central
GO_REF:0000033
NCBI chr 5:49,181,517...49,238,664
Ensembl chr 5:49,181,565...49,233,276
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Aars2
alanyl-tRNA synthetase 2, mitochondrial
involved_in
ISO IEA
(PMID:21549344) GO_REF:0000107
RGD Ensembl
PMID:21549344
GO_REF:0000107
NCBI chr 9:15,484,639...15,496,116
Ensembl chr 9:15,297,531...15,496,090
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Dars2
aspartyl-tRNA synthetase 2 (mitochondrial)
involved_in
ISS ISO
GO_REF:0000024 (PMID:23275545)
UniProt RGD
PMID:23275545
GO_REF:0000024
NCBI chr13:73,308,726...73,336,558
Ensembl chr13:73,308,726...73,336,934
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Gars1
glycyl-tRNA synthetase 1
involved_in
IBA IEA
GO_REF:0000033 GO_REF:0000118
GO_Central TreeGrafter
GO_REF:0000033 GO_REF:0000118
NCBI chr 4:84,171,596...84,212,609
Ensembl chr 4:84,171,596...84,212,609
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Sars1
seryl-tRNA synthetase 1
involved_in
IEA
GO_REF:0000118
TreeGrafter
GO_REF:0000118
NCBI chr 2:196,065,543...196,081,240
Ensembl chr 2:196,065,430...196,081,277
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Sars2
seryl-tRNA synthetase 2, mitochondrial
involved_in
IBA
GO_REF:0000033
GO_Central
GO_REF:0000033
NCBI chr 1:84,028,972...84,040,725
Ensembl chr 1:84,028,986...84,040,725
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Gfm1
G elongation factor, mitochondrial 1
involved_in
ISO IBA IEA ISS
(PMID:19716793) GO_REF:0000033 GO_REF:0000104 GO_REF:0000024
RGD GO_Central UniProt
PMID:19716793
GO_REF:0000024 GO_REF:0000033 GO_REF:0000104
NCBI chr 2:151,700,573...151,745,477
Ensembl chr 2:151,700,564...151,745,471
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Gfm2
GTP dependent ribosome recycling factor mitochondrial 2
NOT|involved_in
ISO
(PMID:19716793)
RGD
PMID:19716793
NCBI chr 2:28,449,452...28,488,200
Ensembl chr 2:28,449,517...28,488,197
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Mrpl44
mitochondrial ribosomal protein L44
involved_in
ISO IBA
(PMID:23315540) GO_REF:0000033
RGD GO_Central
PMID:23315540
GO_REF:0000033
NCBI chr 9:81,106,658...81,111,709
Ensembl chr 9:81,106,655...81,112,812
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mt-Tp
mitochondrially encoded tRNA proline
IDA
RGD
PMID:424302
RGD:2317000
NCBI chr MT:15,348...15,415 NCBI chr MT:15,348...15,415 NCBI chr MT:15,348...15,415
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Tsfm
Ts translation elongation factor, mitochondrial
involved_in
IEA IBA
GO_REF:0000118 GO_REF:0000033
TreeGrafter GO_Central
GO_REF:0000033 GO_REF:0000118
NCBI chr 7:62,828,997...62,864,784
Ensembl chr 7:62,845,488...62,864,769
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Tufm
Tu translation elongation factor, mitochondrial
involved_in
IBA IEA
GO_REF:0000033 GO_REF:0000118
GO_Central TreeGrafter
GO_REF:0000033 GO_REF:0000118
NCBI chr 1:181,073,788...181,077,395
Ensembl chr 1:181,073,788...181,077,395
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Mtif2
mitochondrial translational initiation factor 2
involved_in
ISS IBA
GO_REF:0000024 GO_REF:0000033
BHF-UCL GO_Central
GO_REF:0000024 GO_REF:0000033
NCBI chr14:103,265,808...103,285,733
Ensembl chr14:103,270,039...103,285,728
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Mtif3
mitochondrial translational initiation factor 3
involved_in
ISO IBA
(PMID:12095986) GO_REF:0000033
RGD GO_Central
PMID:12095986
GO_REF:0000033
NCBI chr12:8,126,193...8,140,706
Ensembl chr12:8,126,276...8,140,470
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Mrpl58
mitochondrial ribosomal protein L58
involved_in
ISO IBA
(PMID:20186120) GO_REF:0000033
RGD GO_Central
PMID:20186120
GO_REF:0000033
NCBI chr10:100,646,374...100,652,871
Ensembl chr10:100,646,216...100,652,871
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Mtrf1
mitochondrial translation release factor 1
involved_in
ISO IBA
(PMID:37141370) GO_REF:0000033
RGD GO_Central
PMID:37141370
GO_REF:0000033
NCBI chr15:54,776,885...54,804,699
Ensembl chr15:54,776,937...54,804,704
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Mtrf1l
mitochondrial translation release factor 1 like
involved_in
ISO IBA IEA ISS
(PMID:17803939), (PMID:20075246), (PMID:33878294) GO_REF:0000033 GO_REF:0000107 GO_REF:0000024
RGD GO_Central Ensembl UniProt
PMID:17803939 PMID:20075246 PMID:33878294
GO_REF:0000024 GO_REF:0000033 GO_REF:0000107
NCBI chr 1:42,208,553...42,221,020
Ensembl chr 1:42,210,583...42,220,836
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Wars2
tryptophanyl tRNA synthetase 2 (mitochondrial)
involved_in
IBA
GO_REF:0000033
GO_Central
GO_REF:0000033
NCBI chr 2:186,459,744...186,543,581
Ensembl chr 2:186,459,444...186,543,571
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Yars2
tyrosyl-tRNA synthetase 2
involved_in
ISO IEA
(PMID:20598274) GO_REF:0000107
RGD Ensembl
PMID:20598274
GO_REF:0000107
NCBI chr11:84,632,350...84,638,138
Ensembl chr11:84,624,369...84,638,125
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Malsu1
mitochondrial assembly of ribosomal large subunit 1
involved_in
ISO
(PMID:22829778)
RGD
PMID:22829778
NCBI chr 4:78,051,090...78,059,913
Ensembl chr 4:78,051,059...78,059,905
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C1qbp
complement C1q binding protein
involved_in
ISS ISO
GO_REF:0000024 (MGI:5487496|PMID:22904065)
UniProt RGD
PMID:22904065
GO_REF:0000024 MGI:5487496
NCBI chr10:55,699,954...55,704,605
Ensembl chr10:55,699,954...55,704,649
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Cdk5rap1
CDK5 regulatory subunit associated protein 1
acts_upstream_of_or_within
ISO
MGI:5750452 (PMID:25738458)
RGD
PMID:25738458
NCBI chr 3:142,838,081...142,872,669
Ensembl chr 3:142,708,028...142,872,677
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Coa3
cytochrome C oxidase assembly factor 3
involved_in
ISO
(PMID:23260140)
RGD
PMID:23260140
NCBI chr10:86,220,192...86,221,173
Ensembl chr10:86,220,194...86,221,178
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Fastkd2
FAST kinase domains 2
involved_in
ISO IEA ISS
(PMID:27667664) GO_REF:0000107 GO_REF:0000024
RGD Ensembl UniProt
PMID:27667664
GO_REF:0000024 GO_REF:0000107
NCBI chr 9:65,166,148...65,188,184
Ensembl chr 9:65,168,228...65,188,174
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Fastkd3
FAST kinase domains 3
involved_in
ISO ISS
(PMID:27789713) GO_REF:0000024
RGD UniProt
PMID:27789713
GO_REF:0000024
NCBI chr 1:34,858,342...34,866,988
Ensembl chr 1:34,858,219...34,866,973
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Gm55359
predicted gene, 55359
involved_in
IEA
GO_REF:0000107
Ensembl
GO_REF:0000107
Ensembl chr 7:111,786,726...111,792,148
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LOC134479940
mitochondrial ribosome and complex I assembly factor AltMIEF1
involved_in
ISO
(PMID:30215512)
RGD
PMID:30215512
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Mettl8
methyltransferase 8, tRNA N3-cytidine
involved_in
ISO
(PMID:34774131), (PMID:35017528)
RGD
PMID:34774131 PMID:35017528
NCBI chr 3:55,731,453...55,863,652
Ensembl chr 3:55,770,167...55,863,676
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Mief1
mitochondrial elongation factor 1
involved_in
ISO
(PMID:30215512)
RGD
PMID:30215512
NCBI chr 7:111,786,630...111,802,220
Ensembl chr 7:111,786,709...111,802,220
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Mpv17l2
MPV17 mitochondrial inner membrane protein like 2
involved_in
ISO
(PMID:24948607)
RGD
PMID:24948607
NCBI chr16:18,680,106...18,684,212
Ensembl chr16:18,681,826...18,684,212
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Mrps27
mitochondrial ribosomal protein S27
involved_in
ISO
(PMID:22841715)
RGD
PMID:22841715
NCBI chr 2:30,740,007...30,808,577
Ensembl chr 2:30,740,033...30,808,577
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Ngrn
neugrin, neurite outgrowth associated
involved_in
ISO ISS
(PMID:27667664) GO_REF:0000024
RGD UniProt
PMID:27667664
GO_REF:0000024
NCBI chr 1:134,213,235...134,219,348
Ensembl chr 1:134,213,456...134,219,339
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Nsun4
NOP2/Sun RNA methyltransferase 4
involved_in
ISO
(MGI:5573024|PMID:24516400)
RGD
PMID:24516400
MGI:5573024
NCBI chr 5:129,511,224...129,532,498
Ensembl chr 5:129,512,307...129,532,423 Ensembl chr 5:129,512,307...129,532,423
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Rcc1l
RCC1 like
involved_in
ISO IBA
(PMID:27667664) GO_REF:0000033
RGD GO_Central
PMID:27667664
GO_REF:0000033
NCBI chr12:22,543,125...22,574,042
Ensembl chr12:22,543,734...22,574,036
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Rmnd1
required for meiotic nuclear division 1 homolog
involved_in
ISO IBA
(PMID:25604853) GO_REF:0000033
RGD GO_Central
PMID:25604853
GO_REF:0000033
NCBI chr 1:40,859,829...40,894,376
Ensembl chr 1:40,859,829...40,894,314
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Rpusd3
RNA pseudouridine synthase D3
involved_in
ISO
(PMID:27667664)
RGD
PMID:27667664
NCBI chr 4:146,553,743...146,562,789
Ensembl chr 4:146,558,562...146,562,794
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Rpusd4
RNA pseudouridine synthase D4
involved_in
ISO ISS
(PMID:27667664) GO_REF:0000024
RGD UniProt
PMID:27667664
GO_REF:0000024
NCBI chr 8:33,617,384...33,626,873
Ensembl chr 8:33,617,379...33,626,873
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Trmt10c
tRNA methyltransferase 10C, mitochondrial RNase P subunit
involved_in
ISO IBA ISS
(PMID:27132592) GO_REF:0000033 GO_REF:0000024
RGD GO_Central UniProt
PMID:27132592
GO_REF:0000024 GO_REF:0000033
NCBI chr11:44,584,388...44,589,466
Ensembl chr11:44,584,113...44,589,568
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Trub2
TruB pseudouridine synthase family member 2
involved_in
ISO ISS
(PMID:27667664) GO_REF:0000024
RGD UniProt
PMID:27667664
GO_REF:0000024
NCBI chr 3:13,049,220...13,059,836
Ensembl chr 3:13,033,745...13,059,930
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Uqcc2
ubiquinol-cytochrome c reductase complex assembly factor 2
involved_in
ISS ISO
GO_REF:0000024 (PMID:24385928)
UniProt RGD
PMID:24385928
GO_REF:0000024
NCBI chr20:5,202,837...5,214,541
Ensembl chr20:5,202,837...5,214,164
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Alkbh1
alkB homolog 1, histone H2A dioxygenase
involved_in
ISO
(PMID:27497299)
RGD
PMID:27497299
NCBI chr 6:107,068,301...107,088,784
Ensembl chr 6:107,068,475...107,088,759
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Lrpprc
leucine-rich pentatricopeptide repeat containing
involved_in acts_upstream_of_or_within
IEA ISO IBA
GO_REF:0000107 MGI:5438913 (PMID:22045337) GO_REF:0000033
Ensembl RGD GO_Central
PMID:22045337
GO_REF:0000033 GO_REF:0000107
NCBI chr 6:9,859,816...9,942,294
Ensembl chr 6:9,859,867...9,942,293
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Mtg1
mitochondrial ribosome-associated GTPase 1
involved_in
ISO
(PMID:23396448)
RGD
PMID:23396448
NCBI chr 1:194,931,543...194,944,278
Ensembl chr 1:194,931,531...194,944,277
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Mtg2
mitochondrial ribosome-associated GTPase 2
involved_in
ISO
(PMID:23396448)
RGD
PMID:23396448
NCBI chr 3:167,165,542...167,181,358
Ensembl chr 3:167,165,982...167,181,358
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Nsun3
NOP2/Sun RNA methyltransferase 3
involved_in
ISO
(PMID:27356879), (PMID:27497299)
RGD
PMID:27356879 PMID:27497299
NCBI chr11:37,490,832...37,575,607
Ensembl chr11:37,490,838...37,568,543
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Shmt2
serine hydroxymethyltransferase 2
involved_in
ISO
(PMID:29364879), (PMID:29452640) (MGI:6148506|PMID:29323231), (MGI:6148666|PMID:29452640)
RGD
PMID:29323231 PMID:29364879 PMID:29452640
MGI:6148506 MGI:6148666
NCBI chr 7:63,358,961...63,364,293
Ensembl chr 7:63,358,961...63,364,236
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Taco1
translational activator of cytochrome c oxidase I
involved_in acts_upstream_of_or_within
IEA ISO
GO_REF:0000107 MGI:5905291 (PMID:27319982)
Ensembl RGD
PMID:27319982
GO_REF:0000107
NCBI chr10:91,002,590...91,010,494
Ensembl chr10:91,002,640...91,012,042
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Tsfm
Ts translation elongation factor, mitochondrial
involved_in
ISS IEA ISO
GO_REF:0000024 GO_REF:0000107 (PMID:27677415)
UniProt Ensembl RGD
PMID:27677415
GO_REF:0000024 GO_REF:0000107
NCBI chr 7:62,828,997...62,864,784
Ensembl chr 7:62,845,488...62,864,769
G
Ears2
glutamyl-tRNA synthetase 2, mitochondrial
involved_in
ISO
(PMID:19805282)
RGD
PMID:19805282
NCBI chr 1:176,597,986...176,625,848
Ensembl chr 1:176,597,986...176,625,836
Term paths to the root one shortest all shortest one longest all longest one shortest and longest all